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Investigating Loss of Neuromuscular Junction Transmission Fidelity in Older Adults

Completed
Conditions
Sarcopenia
Registration Number
NCT04904926
Lead Sponsor
NMD Pharma A/S
Brief Summary

Sarcopenia is a condition characterised by age-related loss of muscle mass and function. Factors affecting the strength of muscle contraction independent of mass, such as neuromuscular junction (NMJ) transmission, are increasingly suspected as important contributors to the development of age-related physical disability. The group of investigators leading the current study, have recently demonstrated NMJ transmission deficits in aged mice, but whether this translates in older human individuals is not known

The primary aim is to assess whether clinically meaningfull muscle weakness is associated with NMJ transmission deficits in older human individuals with clinically meaningfull muscle weakness.

The secondary aim is to assess whether NMJ transmission deficits correlate with different measures of functional capacity to inform future trials of the most appropriate choice of tests.

Detailed Description

The study is a cross-sectional pilot study and will be led by investigators:

1. Professor Brian Clark, PhD, Ohio University

2. Professor William David Arnold, MD, Ohio State University

Up to 16 older (\>70 yrs.) individuals and 8 healthy younger (18-50 yrs.) individuals will be included in this cross-sectional pilot study. To assess whether clinically meaningfull muscle weakness is associated with NMJ transmission failure, results from single fiber EMG analyses and repetitive nerve stimulation in older individuals with clinically meaningfull muscle weakness will be compared to those obtained in older adults without muscle weakness and with healthy young individuals. To assess whether NMJ transmission deficits correlates with different measures of functional capacity, a series of different functional tests will be performed.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
19
Inclusion Criteria

Not provided

Exclusion Criteria
  • Neuromuscular Disease (ie. movement disorder, or overt neurological disease, such as Sensory Neuropathy with Sensory Ataxia, Apraxia, Post-Polio Syndrome, Mitochondrial Myopathy, Myelopathy, myasthenia gravis)
  • Neurological Disease (ie. Dementia (Alzheimers, multi-infarct, fronto-temporal); multiple sclerosis, amyotrophic lateral sclerosis, Parkinsons Disease, cerebellar ataxia, or significant cognitive impairment (a score of 22 or less on the Montreal Cognitive Assessment (MOCA))
  • Musculoskeletal disorders (ie. rheumatoid arthritis, ankylosing spondylitis, psoriatic arthritis, acute gout or osteoarthritis limiting mobility)
  • Terminal illness(i.e., Cancer, myeloma, acute leukaemia)
  • Uncontrolled Psychiatric disorder (ie. bipolar, schizophrenia, major depression)
  • Cardiovascular Diseases (ie. NYHA Class III or IV congestive heart failure, clinically significant aortic stenosis, recent history of cardiac arrest, uncontrolled atrial fibrillation, use of a cardiac defibrillator, or uncontrolled angina or hypertension)
  • Other significant conditions (ie, that would impact safety and/or compliance to the protocol (e.g. chronic renal failure requiring peritoneal or hemodialysis, chronic liver disease, blood dyscrasia, carcinoma within last 3 years, severe inflammatory bowel disease, severe respiratory disease (uncontrolled asthma, COPD), etc)
  • Drug or alcohol abuse
  • Not meeting MRI eligibility (e.g. metal implants, reported pregnancy or positive pregnancy test at the time of imaging for women aged 55 years or younger);
  • Not meeting the DEXA eligibility (e.g. reported pregnancy or positive pregnancy test at the time of imaging for women aged 55 years or younger);
  • Failure to provide informed consent;
  • Subjects who do not answer "male" or female" to the question of biological sex
  • Currently or recently (within the last 1 year) taking gender affirming hormones.

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Single Fiber Electromyography (sfEMG)Baseline

sfEMG of the vastus lateralis will be performed to ascertain NMJ transmission at a minimum of 30 synapses per participant.

Secondary Outcome Measures
NameTimeMethod
60-Sec MVC Fatigue TestBaseline

Assessment of lower extremity fatigue

Dual Energy X-ray Absorption (DEXA) ScanningBaseline

Assessment of percent body fat

Four Square TestBaseline

Assessment of coordination

Repetitive Nerve StimulationBaseline

As additional measures of NMJ transmission, Repetitive Nerve Stimulation (3Hz) of the spinal accessory nerve (recorded from the trapezius) and fibular nerve (recorded from tibialis anterior) will be performed

Stair Climb Power TestBaseline

Assessment of lower leg power

Magnetic Resonance ImagingBaseline

Assessment of thigh muscle cross-sectional area

Short Physical Performance Battery (SPPB) - 4 Meter Walk TestBaseline

4 Meter Walk Test score ranging from 0 (worst performance) to 4 (best performance)

Isometric and Isokinetic Leg Extension StrengthBaseline

Assessment of isometric and isokinetic leg extonsor strength. Isokinetic leg extensor strength is also used for weakness classification in older adults

Short Physical Performance Battery (SPPB)Baseline

Total Short Physical Performance Battery test score ranging from 0 (worst performance) to 12 (best performance)

Short Physical Performance Battery (SPPB) - Standing Balance TestBaseline

Standing Balance Test score ranging from 0 (worst performance) to 4 (best performance)

Short Physical Performance Battery (SPPB) - Chair Stand TestBaseline

Chair Stand Test score ranging from 0 (worst performance) to 4 (best performance)

Hand Grip DynamometryBaseline

Assessment of Hand Grip Strength

Trial Locations

Locations (1)

Ohio University

🇺🇸

Athens, Ohio, United States

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