MedPath

Study of Subretinally Injected AAVB-081 in Patients with Usher Syndrome Type IB (USH1B) Retinitis Pigmentosa

Phase 1/2
Recruiting
Conditions
Usher Syndrome Type 1B (USH1B) Retinitis Pigmenotsa
Registration Number
2024-518489-29-00
Lead Sponsor
Aavantgarde Bio S.r.l.
Brief Summary

- To assess the safety and tolerability of subretinal administration of AAVB-081 in participants with USH1B retinitis pigmentosa

- To determine a well-tolerated dose with optimal risk-benefit profile (RBP)

Detailed Description

Not available

Recruitment & Eligibility

Status
Ongoing, recruiting
Sex
Not specified
Target Recruitment
9
Inclusion Criteria

All participants: Informed consent signed by the participant or participant’s legally authorized representative (if applicable).

All participants: Male and female adults diagnosed with USH1B; ≥ 18 to 50 ≤ 60 years of age

All participants: Molecular diagnosis of USH1B due to MYO7A mutations (homozygotes or compound heterozygotes) by a Sponsor approved CLIA laboratory.

All participants: Residual central visual function evidenced by LLVA of ≥10 letters in the MVA subjects.

All participants: Female participants of childbearing potential must use a highly effective method of contraception (see Appendix 3 for examples) for 1 year after treatment (from Day 0). Male participants who have a partner of childbearing potential must use condoms (barrier contraception) for 1 year after treatment. For the purpose of this protocol, a female participant is considered of childbearing potential (FPOCBP), i.e., fertile, following menarche and until becoming post-menopausal unless permanently sterile. Permanent sterilization methods include hysterectomy, bilateral salpingectomy and bilateral oophorectomy. A postmenopausal state is defined as no menses for 12 months without an alternative medical cause.

Exclusion Criteria

Unable or unwilling to meet the requirements of the study.

Previous participation in any other gene therapy trial.

Pre-existing eye conditions that would preclude the planned surgery or interfere with the interpretation of study endpoints (including but not limited to glaucoma, steroid response, corneal or significant lenticular or media opacities, cystoid macular oedema, macular hole, uveitis, epiretinal membrane).

Any systemic condition that would preclude subretinal surgery.

Profound vision loss in one eye with visual acuity of counting fingers (CF) or worse on semiquantitative scale.

Complicating ocular and systemic diseases, medications, or clinically significant abnormal baseline laboratory values.

Prior ocular non-macular laser within 3 months, prior cataract surgery within 3 months, use of post-operative anti-inflammatory drops in the past month, presence of inflammatory complications of cataract surgery in the past month, any other non-retinal intra-ocular surgery in the past 6 months prior to Day 0; and prior macular laser or retinal surgery at any time.

Use of high dose vitamin A (>7500 retinol equivalent units or >3300 IU per day), tretinoin-containing skin crème (e.g., Retin-A), or isotretinoin within 3 months prior to Day 0, or intended use during the study.

Chronic use of Viagra (sildenafil) or any other phosphodiesterase type 5 inhibitors used to treat erectile dysfunction, defined as at least once per month over the 12 months prior to Screening and until completion of study participation.

Participants who are positive for hepatitis B, hepatitis C, HIV, tuberculosis (TB), or syphilis infection.

Suspected or laboratory confirmed SARS-CoV-2 infection within 14 days prior to Day 0.

History of retinal detachment.

Has received a live, attenuated vaccine within 30 days prior to Day 0. Examples of live vaccines include, but are not limited, to the following: measles, mumps, rubella, varicella/zoster (chicken pox), yellow fever, rabies, Bacillus Calmette-Guerin (BCG), typhoid vaccine, and covid vaccine.

Poorly controlled diabetes mellitus (of any type), defined as HbA1c ≥7, in the 6 months prior to subretinal injection.

Presence of moderate or severe non-proliferative diabetic retinopathy or worse, diabetic macular edema (DME), retinal tumors, high axial myopia (>-6 Diopters), and micro/nanophthalmos.

Known sensitivity to medications planned for use in the peri- operative period.

Participants who are pregnant and/or breastfeeding at Screening.

Any other condition that would not allow the potential participant to complete follow-up examinations during the course of the study and in the opinion of the investigator, makes the potential participant unsuitable for the study.

Unable to communicate with suitable verbal/auditory and/or tactile sign language (in the opinion of the investigator).

Participation in a clinical study with an investigational drug in the past six months, or 5 half-lives, whichever is longer.

Study & Design

Study Type
Interventional clinical trial of medicinal product
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
The incidence and severity of adverse events (AEs) including serious adverse events (SAEs), treatment emergent adverse events (TEAEs) and dose limiting toxicities (DLTs) at 24 months.

The incidence and severity of adverse events (AEs) including serious adverse events (SAEs), treatment emergent adverse events (TEAEs) and dose limiting toxicities (DLTs) at 24 months.

The incidence and nature of DLTs at each dose level at 24 months

The incidence and nature of DLTs at each dose level at 24 months

Secondary Outcome Measures
NameTimeMethod

Trial Locations

Locations (1)

Azienda Ospedaliera Universitaria Universita' Degli Studi Della Campania Luigi Vanvitelli

🇮🇹

Naples, Italy

Azienda Ospedaliera Universitaria Universita' Degli Studi Della Campania Luigi Vanvitelli
🇮🇹Naples, Italy
Francesca Simonelli
Site contact
00390815666762
francesca.simonelli@unicampania.it

MedPath

Empowering clinical research with data-driven insights and AI-powered tools.

© 2025 MedPath, Inc. All rights reserved.