MedPath

PKUDOS: Phenylketonuria (PKU) Demographic, Outcomes, and Safety Registry

Completed
Conditions
Phenylketonuria
Hyperphenylalaninaemia
Interventions
Registration Number
NCT00778206
Lead Sponsor
BioMarin Pharmaceutical
Brief Summary

The objective of this study is to evaluate the safety of long-term treatment with Kuvan.

Detailed Description

The PKUDOS program is a voluntary, multicenter, strictly observational program for patients with PKU who have either received Kuvan therapy, or currently receive Kuvan, or intend to begin receiving Kuvan therapy within 90 days of entering the registry.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
1887
Inclusion Criteria
  • Patient has confirmed diagnosis of PKU with hyperphenylalaninemia documented by a Phenylalanine level of greater than or equal to 360 umol/L (6 mg/dL)
  • Patient has previously received Kuvan
  • Patient is currently receiving Kuvan
  • Patient intends to receive Kuvan therapy within 90 days of enrollment into the registry
  • The Patient is being followed at a PKUDOS participating center
  • Willing and able to provide written authorization or, if under the age of 18 years, provide written assent (if required) and written patient authorization by a parent or legal guardian
  • Willing to provide personal health information
Exclusion Criteria
  • Patients are not eligible to participate in PKUDOS if they are participating in a BioMarin-sponsored clinical study of Kuvan
  • Patients not previously treated with Kuvan and patients that are unwilling to begin Kuvan therapy within 90 days of entry into the registry

PKU MOMS Subregistry

Inclusion Criteria:

  • Willing to enroll in (or are already enrolled in) PKUDOS
  • Agree to follow the standard of care for pregnant women with PKU in the United States (NIH, 200, NIH Consensus Statement)
  • Agree to be followed by a hospital or PKU clinic offering the standard of care for maternal PKU
  • Are within 10 weeks of their last menstrual period

Exclusion Criteria:

  • Patients who have not adhered to the standard of care for pregnant women with PKU in the United States are not eligible to participate in PKU MOMS

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Arm && Interventions
GroupInterventionDescription
2. PKU MOMS SubregistryKuvanPatients with PKU who are pregnant at enrollment in the registry or who become pregnant while participating in the registry.
Primary Outcome Measures
NameTimeMethod
Observational Data Only15 years

Registry data including demographic and baseline characteristics

Secondary Outcome Measures
NameTimeMethod

Trial Locations

Locations (45)

LAC and USC Medical Center

🇺🇸

Los Angeles, California, United States

UCLA

🇺🇸

Los Angeles, California, United States

Ann and Robert H. Lurie Children's Hospital of Chicago

🇺🇸

Chicago, Illinois, United States

Nationwide Children's Hospital

🇺🇸

Columbus, Ohio, United States

Children's Hospital of Philadelphia

🇺🇸

Philadelphia, Pennsylvania, United States

Children's Hospital of Pittsburgh

🇺🇸

Pittsburgh, Pennsylvania, United States

University of Iowa

🇺🇸

Iowa City, Iowa, United States

University of Kentucky

🇺🇸

Lexington, Kentucky, United States

University of Missouri Health Care

🇺🇸

Columbia, Missouri, United States

West Virginia Genetics Center, Department of Pediatrics

🇺🇸

Morgantown, West Virginia, United States

University of California, San Diego

🇺🇸

San Diego, California, United States

University of Miami, Miller School of Medicine, Department of Human Genetics

🇺🇸

Miami, Florida, United States

University of Minnesota

🇺🇸

Minneapolis, Minnesota, United States

Children's Hospital of Orange County

🇺🇸

Orange, California, United States

University of Rochester Medical Center

🇺🇸

Rochester, New York, United States

Indiana University School of Medicine

🇺🇸

Indianapolis, Indiana, United States

University of Nebraska

🇺🇸

Omaha, Nebraska, United States

Oregon Health and Science University

🇺🇸

Portland, Oregon, United States

University of Utah

🇺🇸

Salt Lake City, Utah, United States

Children's Hospital of Wisconsin

🇺🇸

Milwaukee, Wisconsin, United States

Children's Hospital, University of Colorado School of Medicine

🇺🇸

Aurora, Colorado, United States

Tampa Children's Hospital, St. Joseph's Pediatric Endocrine Associates

🇺🇸

Tampa, Florida, United States

Childrens Hospital of Los Angeles

🇺🇸

Los Angeles, California, United States

Stanford University, Pediatrics

🇺🇸

Stanford, California, United States

Children's National Medical Center

🇺🇸

Washington, District of Columbia, United States

Emory University

🇺🇸

Decatur, Georgia, United States

Wesley Pediatric Faculty Clinic

🇺🇸

Wichita, Kansas, United States

Children's Hosptial of Boston

🇺🇸

Boston, Massachusetts, United States

AHS Hospital Corp

🇺🇸

Morristown, New Jersey, United States

Albany Medical Center

🇺🇸

Albany, New York, United States

St. Louis Children's Hospital

🇺🇸

Saint Louis, Missouri, United States

Akron Children's Hospital

🇺🇸

Akron, Ohio, United States

Westchester Medical Center

🇺🇸

Valhalla, New York, United States

St. Christophers Hospital for Children

🇺🇸

Philadelphia, Pennsylvania, United States

Penn State, Milton S. Hershey Medical Center

🇺🇸

Hershey, Pennsylvania, United States

Sanford Children's Specialty Clinic

🇺🇸

Sioux Falls, South Dakota, United States

Greenwood Genetic Center

🇺🇸

Greenwood, South Carolina, United States

Children's Hospital of the King's Daughters

🇺🇸

Norfolk, Virginia, United States

Johns Hopkins University School of Medicine

🇺🇸

Baltimore, Maryland, United States

University of Oklahoma

🇺🇸

Oklahoma City, Oklahoma, United States

University of South Florida

🇺🇸

Tampa, Florida, United States

Kosair Charities Pediatric Clinical Research Unit

🇺🇸

Louisville, Kentucky, United States

University of North Carolina

🇺🇸

Chapel Hill, North Carolina, United States

University of Florida

🇺🇸

Gainesville, Florida, United States

Tulane University Medical School

🇺🇸

New Orleans, Louisiana, United States

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