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AVAJAK: Apixaban/Rivaroxaban Versus Aspirin for Primary Prevention of Thrombo-embolic Complications in JAK2V617F-positive Myeloproliferative Neoplasms

Phase 3
Recruiting
Conditions
Prefibrotic/Early Primary Myelofibrosis
Polycythemia Vera
Essential Thrombocythemia
JAK2 V617F
High-risk Patients
Interventions
Drug: Direct Oral Anticoagulants
Registration Number
NCT05198960
Lead Sponsor
University Hospital, Brest
Brief Summary

Philadelphia-negative myeloproliferative neoplasms (MPN) are frequent and chronic myeloid malignancies including Polycythemia Vera (PV), essential thrombocythemia (ET), Primary Myelofibrosis (PMF) and Prefibrotic myelofibrosis (PreMF). These MPNs are caused by the acquisition of mutations affecting activation/proliferation pathways in hematopoietic stem cells. The principal mutations are JAK2V617F, calreticulin (CALR exon 9) and MPL W515. ET or MFP/PreMF patients who do not carry one of these three mutations are declared as triple-negative (3NEG) cases even if they are real MPN cases.

These diseases are at high risk of thrombo-embolic complications and with high morbidity/mortality. This risk varies from 4 to 30% depending on MPN subtype and mutational status.

In terms of therapy, all patients with MPNs should also take daily low-dose aspirin (LDA) as first antithrombotic drug, which is particularly efficient to reduce arterial but not venous events.

Despite the association of a cytoreductive drug and LDA, thromboses still occur in 5-8% patients/year.

All these situations have been explored in biological or clinical assays. All of them could increase the bleeding risk. We should look at different ways to reduce the thrombotic incidence: Direct Oral Anticoagulants (DOAC)? In the general population, in medical or surgical contexts, DOACs have demonstrated their efficiency to prevent or cure most of the venous or arterial thrombotic events.

At the present time, DOAC can be used in cancer populations according to International Society on Thrombosis and Haemostasis (ISTH) recommendations, except in patients with cancer at high bleeding risk (gastro-intestinal or genito-urinary cancers). Unfortunately, in trials evaluating DOAC in cancer patients, most patients have solid rather than hematologic cancers (generally less than 10% of the patients, mostly lymphoma or myeloma).

In cancer patients, DOAC are also highly efficient to reduce the incidence of thrombosis (-30 to 60%), but patients are exposed to a higher hemorrhagic risk, especially in digestive cancer patients.

In the cancer population, pathophysiology of both thrombotic and hemorrhagic events may be quite different between solid cancers and MPN. If MPN patients are also considered to be cancer patients in many countries, the pathophysiology of thrombosis is quite specific (hyperviscosity, platelet abnormalities, clonality, specific cytokines...) and they are exposed to a lower risk of digestive hemorrhages. It is thus difficult to extend findings from the "general cancer population" to MPN patients.

Unfortunately, only scarce, retrospective data regarding the use of DOAC in MPNs are available data.

We were the first to publish a "real-life" study about the use, the impact, and the risks in this population. In this local retrospective study, 25 patients with MPN were treated with DOAC for a median time of 2.1 years. We observed only one thrombosis (4%) and three major hemorrhages (12%, after trauma or unprepared surgery). Furthermore, we have compared the benefit/risk balance compared to patients treated with LDA without difference.

With the increasing evidences of efficacy and tolerance of DOAC in large cohorts of patients including cancer patients, with their proven efficacy on prevention of both arterial and venous thrombotic events and because of the absence of prospective trial using these drugs in MPN patients, we propose to study their potential benefit as primary thrombotic prevention in MPN.

Detailed Description

Not available

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
1308
Inclusion Criteria
  • Patients with diagnosis of PV or ET or PreMF according to WHO or BSCH criteria (bone marrow biopsy not compulsory).

  • Patients with JAK2V617F mutation (threshold allele burden > 1%).

  • Patients considered as "high-risk" patients:

    1. based on age (> 60-year-old)
    2. based on thrombotic history (compatible with antithrombotic randomization) but aged ≥ 18-year-old.
  • Length of time from MPN diagnostic to inclusion will not exceed 12 months.

Exclusion Criteria
  • Contra-indication to aspirin or DOAC due to allergic situation or recent history of major bleeding.
  • Formal indication of treatment with aspirin or DOAC (thus precluding randomization).
  • Inability to give informed consent.
  • Patients under curatorship/guardianship
  • Concomitant use of a strong inhibitor or inducer of CYP3A4 (like ruxolitinib).
  • Chronic liver disease or chronic hepatitis.
  • Renal insufficiency with creatinine <30 ml/mn on Cockcroft and Gault Formula
  • Patient considered at high-risk of bleeding: patients with current or recent major or clinical relevant non major bleeding gastrointestinal or cerebral bleedings
  • Planned pregnancy within 24 months
  • No appropriate contraception (estrogen contraception or no contraception) in women of childbearing age or breastfeeding woman
  • PS>2 or life expectancy <12 months.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Experimental groupDirect Oral AnticoagulantsPatients randomized to receive Direct Oral Anticoagulants, at the choice of the investigator Apixaban 2.5 mg both in day or Rivaroxaban 10 mg one per day, at the choice of the investigator
Control groupLow-dose aspirinPatients randomized to receive Low-Dose Aspirin Aspirin 100 mg one per day
Primary Outcome Measures
NameTimeMethod
Time to occurrence of arterial or venous thromboembolic events.Time to occurrence up to 24 months of patient follow-up

Nb and type of thrombotic events during the FU

Secondary Outcome Measures
NameTimeMethod
Time to occurrence of major and clinically relevant non-major bleedings as defined by International Society on Thrombosis and HaemostasisTime to occurrence up to 24 months of patient follow-up

Nb and type of new hemorrhagic events

Time to occurrence of arterial thromboembolic events.Time to occurrence up to 24 months of patient follow-up

Nb and type of new arterial events

Time to occurrence of venous thromboembolicTime to occurrence up to 24 months of patient follow-up

Nb and type of new venous events

Time to occurrence of thromboembolic and bleeding events according to the cytoreductive associated drugsTime to occurrence up to 24 months of patient follow-up

Nb and type of new thromboembolic and hemorrhage events

Time to occurrence of serious adverse events others than thromboses and hemorrhages hemorrhagesTime to occurrence up to 24 months of patient follow-up

Nb, type and grade of adverse events observed

Overall survival and event-free survival24 months

Time to last news and time to first event

Therapeutic adherence24 months

Therapeutic adherence by Girerd auto-questionnaire

Occurrence of atrial fibrillation episode (time to occurrence).24 months

Nb and timing of atrial fibrillation event

Evaluation of Quality of life under antithrombotic drugs24 months

Evaluation of QoL by the use of EQ-5D-5L Quality of life

Evaluation of costs and incremental cost utility ratio of low-dose DOAC compared to low-dose aspirin24 months

Evaluation of benefits/costs under antithrombotic drugs

Trial Locations

Locations (42)

CHU Brest

🇫🇷

Brest, France

CHU Bordeaux

🇫🇷

Bordeaux, France

Médipôle Hôpital Mutualiste Villeurbanne

🇫🇷

Villeurbanne, France

CHU d'Angers

🇫🇷

Angers, France

CH d'Annecy

🇫🇷

Annecy, France

Hôpital privé Cesson-Sévigné

🇫🇷

Cesson-Sévigné, France

CHU Grenoble Alpes

🇫🇷

Grenoble, France

CH Libourne

🇫🇷

Libourne, France

Centre Léon Bérard Lyon

🇫🇷

Lyon, France

CHU de Limoges - Hôpital Dupuytren

🇫🇷

Limoges, France

CHR d'Orléans

🇫🇷

Orléans, France

CHU de Rennes

🇫🇷

Rennes, France

Centre Henri Becquerel de Rouen

🇫🇷

Rouen, France

CHU La Réunion - Site Sud

🇫🇷

Saint-Pierre, France

CH d'Avignon

🇫🇷

Avignon, France

CH de Béziers

🇫🇷

Béziers, France

CHU de Clermont-Ferrand

🇫🇷

Clermont-Ferrand, France

CHD Vendée La Roche Sur Yon

🇫🇷

La Roche-sur-Yon, France

Hôpital Henri Mondor (APHP)

🇫🇷

Créteil, France

CHU Le Havre

🇫🇷

Le Havre, France

CH Le Mans

🇫🇷

Le Mans, France

CHU de Nancy

🇫🇷

Nancy, France

CHU de Nantes - Hôtel-Dieu

🇫🇷

Nantes, France

Hôpital Privé du Confluent Nantes

🇫🇷

Nantes, France

CH de Perpignan

🇫🇷

Perpignan, France

Hôpital St-Louis (APHP)

🇫🇷

Paris, France

CHIC de Quimper

🇫🇷

Quimper, France

CH de Périgueux

🇫🇷

Périgueux, France

CH de Rochefort

🇫🇷

Rochefort, France

Clinique Sainte Anne Strasbourg

🇫🇷

Strasbourg, France

CHU de Tours

🇫🇷

Tours, France

CH Bretagne Atlantique Vannes

🇫🇷

Vannes, France

CH de Versailles

🇫🇷

Versailles, France

CH Paul-Brousse (APHP)

🇫🇷

Villejuif, France

Hôpital Cochin (APHP)

🇫🇷

Paris, France

CH d'Argenteuil

🇫🇷

Argenteuil, France

CH de la Côte Basque Bayonne

🇫🇷

Bayonne, France

CHU de Montpellier

🇫🇷

Montpellier, France

CH de Morlaix

🇫🇷

Morlaix, France

CH de Roubaix

🇫🇷

Roubaix, France

Institut de Cancérologie Lucien Neuwirth St-Priest-en-Jarez

🇫🇷

Saint-Priest-en-Jarez, France

CHU La Réunion - Site Nord Félix GUYON

🇫🇷

Saint-Denis, France

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