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HELIOS-B: A Study to Evaluate Vutrisiran in Patients with Transthyretin Amyloidosis with Cardiomyopathy

Phase 3
Conditions
Patients with ATTR amyloidosis (hATTR or wtATTR) with cardiomyopathy
Registration Number
JPRN-jRCT2031210402
Lead Sponsor
Yamaji Hideomi
Brief Summary

Not available

Detailed Description

Not available

Recruitment & Eligibility

Status
ot Recruiting
Sex
All
Target Recruitment
24
Inclusion Criteria

Has a documented diagnosis of transthyretin (ATTR) amyloidosis with cardiomyopathy, classified as either hereditary ATTR (hATTR) amyloidosis with cardiomyopathy or wild-type ATTR (wtATTR) amyloidosis with cardiomyopathy meeting pre-specified diagnostic criteria
- Has medical history of heart failure (HF) with at least 1 prior hospitalization for HF OR clinical evidence of HF

Exclusion Criteria

- Has known primary amyloidosis (AL amyloidosis) or leptomeningeal amyloidosis.
- Has NYHA Class IV heart failureNYHA Class IV heart failure.
- Has NYHA Class III heart failure AND is at high risk based on pre-specified criteria.
- Has a polyneuropathy disability (PND) Score IIIa, IIIb, or IV at the Screening visit.
- Has eGFR <30 mL/min/1.73 m2.
- Has received prior TTR-lowering treatment.
- Has other non-TTR cardiomyopathy, hypertensive cardiomyopathy, cardiomyopathy due to valvular heart disease, or cardiomyopathy due to ischemic heart disease.

Study & Design

Study Type
Interventional
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Secondary Outcome Measures
NameTimeMethod
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