MedPath

Fitness, Body Composition, Physical Activity and Sleep Patterns in People With Cystic Fibrosis on Modulator Therapy.

Recruiting
Conditions
Cystic Fibrosis
Registration Number
NCT05857709
Lead Sponsor
University of Portsmouth
Brief Summary

Cystic fibrosis (CF) is the most common inherited condition in the United Kingdom, affecting approximately 10,837 people. It is well recognised that regular exercise is clinically important for people with CF. Exercise function measured by the maximal oxygen consumption during a cardiopulmonary exercise test is often reduced in people with CF and this has been attributed to multiple factors including, altered heart and blood vessel function, muscle function, reduced physical activity levels and poorer sleep quality.

New medicine (modulators) have become available for many people with CF. Modulators appear able to reduce sweat chloride concentrations, improve lung function and reduce the frequency of pulmonary exacerbations in people with CF. Little evidence exists to show how they may have changed the fitness and underlying mechanisms responsible for this in people with CF.

This study aims to:

1. determine the exercise function

2. determine the blood vessel function

3. determine body composition

4. determine physical activity and sleep levels in people with CF on modulator therapy compared to a healthy controls group.

Detailed Description

CF is the most common inherited condition in the United Kingdom, affecting approximately 10,837 people. CF affects the movement of salt and water across the body which leads to a thick sticky build up of mucus causing problems in the lungs and digestive system. CF also causes problems in other parts of the body for example, the heart, the blood vessels and muscles. This can impact a person with CFs' ability to exercise which can have impact prognosis, quality of life and increase the amount of times someone with CF is admitted to hospital due to a chest infection.

For many people with CF, new medicine (modulators) have lately become accessible bringing big changes to their health. Elexacaftor-tezacaftor-ivacaftor (ETI) is the most recently approved modulator for use in people with specific CF transmembrane conductance regulator gene mutations and is now the most widely used modulator therapy. So far clinical trials have largely looked at lung function, sweat chloride levels and body mass index. The wider reaching effects of modulator therapy on exercise function has not been studied. This study will see if people with CF have blood vessel and exercise dysfunction, abnormal body composition and reduced physical activity and sleep quality when they are taking modulator therapy compared to a healthy group.

The aims of this study are:

1. Determine the aerobic exercise function and mechanisms underlying this in people with CF stable on ETI and whether this is different to healthy age- and sex-matched controls;

2. Determine the peripheral muscle function in people with CF stable on ETI and whether this is different to healthy age- and sex-matched controls;

3. Determine the functional exercise capacity in people with CF stable on ETI and whether this is different to healthy age- and sex-matched controls;

4. Determine the micro- and macrovascular endothelial function in people with CF stable on ETI and whether this is different to healthy age- and sex-matched controls;

5. Determine body composition in people with CF stable on ETI and whether this is different to healthy age- and sex-matched controls;

6. Determine the physical activity levels and sleep duration and quality in people with CF stable on ETI and whether this is different to healthy age- and sex-matched controls

This study will recruit 50 people with CF and 50 healthy age- and sex-matched control participants who are older than 10 years of age. It will ask them to attend the University of Portsmouth for 2 visits. The first visit will last \~3 hours. During this time they will undergo measures on blood vessel function and aerobic exercise function. The second visit will last \~2 hours. During this time they will undergo a body composition scan and a series of muscle function test. At home, participants will wear an accelerometer for 7 days and complete a series of questionnaires.

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
100
Inclusion Criteria

Not provided

Exclusion Criteria

Not provided

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Maximal oxygen uptakeDay 1 - baseline

Between group differences in maximal oxygen uptake derived from a maximal cardiopulmonary exercise testing on a cycle ergometer

Secondary Outcome Measures
NameTimeMethod
Total minutes of physical activity (light, moderate, moderate to vigorous physical activity)Physical activity will be measured continuously for 7 days

Between group differences in physical activity assessed via wrist-worn accelerometery

Peak minute ventilationDay 1 - baseline

Between group differences in peak minute ventilation derived from a maximal cardiopulmonary exercise test on a cycle ergometer

Cardiac outputDay 1 - baseline

Between group differences in dynamics of non-invasive thoracic impedance cardiography

Quadricep fatigability indexDay 2 - baseline

Derived from change in maximal voluntary contraction

Handgrip strengthDay 2 - baseline

Between group difference in handgrip strength

Body composition (total fat-free mass and total fat mass)Day 2 - baseline

Derived from dual-energy X-ray absorptiometry

Forced Vital Capacity (%predicted)Day 1 - baseline

Between group differences in Forced Vital Capacity measured using flow-volume loop spirometry

Heart rateDay 1 - baseline

Between group differences in heart rate derived from a maximal cardiopulmonary exercise test on a cycle ergometer

Sleep efficiency (time in bed + time asleep)Sleep efficiency will be measured continuously for 7 days

Between group differences in sleep efficiency assessed via wrist-worn accelerometery

Maximum quadricep strengthDay 2 - baseline

Derived from a maximal voluntary contraction

Cystic fibrosis questionnaire revisedDay 2 - baseline

Between group difference in health related quality of life on a 0 - 100 scale with higher scores indicating better health related quality of life

Oxygen uptake at the gas exchange thresholdDay 1 - baseline

Between group differences in oxygen uptake at the gas exchange threshold derived from a maximal cardiopulmonary exercise test on a cycle ergometer

Peak power outputDay 1 - baseline

Between group differences in peak power output derived from a maximal cardiopulmonary exercise test on a cycle ergometer

Stroke volume indexDay 1 - baseline

Between group differences in dynamics of non-invasive thoracic impedance cardiography

Insulin iontophoresisDay 1 - baseline

Between group differences in insulin iontophoresis measure of microvascular function

Percentage change in brachial artery diameter taken from the Flow Mediated Dilation assessmentDay 1 - baseline

Between group differences in Flow Mediated Dilation assessment derived from baseline brachial artery diameter and peak brachial artery diameter from flow mediated dilation measure of macrovascular function

Time to exhaustionDay 1 - baseline

Between group differences in time to exhaustion derived from a maximal cardiopulmonary exercise test on a cycle ergometer

Near-infrared spectroscopy derived deoxygenated [haemoglobin + myoglobin]Day 1 - baseline

Between group differences in dynamics of near-infrared spectroscopy derived deoxygenated \[haemoglobin + myoglobin\]

Forced Expiratory Volume in the 1st second (% predicted)Day 1 - baseline

Between group differences in Forced Expiratory Volume in the 1st second measured using flow-volume loop spirometry

Acetylcholine iontophoresisDay 1 - baseline

Between group differences in acetylcholine iontophoresis measure of microvascular function

Sit to stand repetitions per minuteDay 2 - baseline

Between group difference in sit to stand repetitions per minute

The Pittsburgh Sleep Quality IndexDay 2 - baseline

Between group differences in the Pittsburgh Sleep Quality Index on a 0 - 21 scale with higher scores indicating worse sleep quality

Habitual activity estimation scaleDay 2 - baseline

Between group difference in habitual activity estimation scale - answers are varied and require numerical values, percentages and/or multiple choice questions

Perceived exertion (breathing effort, chest tightness, throat narrowing, perceived exertion)Day 1 - baseline

Between group differences in perceived exertion using the Dalhousie Dyspnoea and Perceived Exertion Scales during a maximal cardiopulmonary exercise testing on a cycle ergometer on a 1 - 7 scale with a higher value indicating a worse perceived exertion

Trial Locations

Locations (1)

University of Portsmouth

🇬🇧

Portsmouth, United Kingdom

© Copyright 2025. All Rights Reserved by MedPath