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MAGNITUDE: A Phase 3 Study of NTLA-2001 in Participants With Transthyretin Amyloidosis With Cardiomyopathy (ATTR-CM)

Phase 3
Recruiting
Conditions
Transthyretin Amyloidosis (ATTR) With Cardiomyopathy
Interventions
Registration Number
NCT06128629
Lead Sponsor
Intellia Therapeutics
Brief Summary

To evaluate the efficacy and safety of a single dose of NTLA-2001 compared to placebo in participants with ATTR-CM.

Detailed Description

This is a multinational, multicenter, double-blind, placebo-controlled study in approximately 765 participants, who will be randomized to receive a single infusion of either NTLA-2001 or placebo.

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
765
Inclusion Criteria
  • Documented diagnosis of ATTR amyloidosis with cardiomyopathy
  • Medical history of heart failure (HF)
  • Symptoms of HF are optimally managed and clinically stable within 28 days prior to administration of study intervention
  • Screening NT-proBNP, a blood marker of HF severity, greater than or equal to 600 pg/mL and less than 10,000 pg/mL
Exclusion Criteria
  • New York Heart Association (NYHA) Class IV HF
  • Polyneuropathy Disability score of IV (confined to wheelchair or bed)
  • Has hepatitis B, hepatitis C or human immunodeficiency virus (HIV) infection
  • History of active malignancy within 3 years prior to screening
  • RNA silencer therapy (patisiran, inotersen and/or eplontersen) within 12 months prior to dosing. Any prior vutrisiran use is not allowed
  • Initiation of tafamidis or acoramidis within 56 days prior to study dosing
  • Estimated glomerular filtration rate (eGFR) <30 mL/min/1.73m^2
  • Liver failure
  • Uncontrolled blood pressure
  • Unable or unwilling to take vitamin A supplementation for the duration of the study

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
NTLA-2001NTLA-2001Single intravenous (IV) infusion of NTLA-2001
PlaceboPlaceboSingle IV infusion of normal saline
Primary Outcome Measures
NameTimeMethod
Composite outcome of cardiovascular (CV) mortality and CV eventsMaximum study duration is dependent on event rates and is estimated to be at least 18 months and up to 48 months
Secondary Outcome Measures
NameTimeMethod
Change in baseline to month 18 in serum TTRBaseline, Month 18
Change from baseline to month 18 in KCCQ-OS scoreBaseline, Month 18

Trial Locations

Locations (102)

AP-HP Hopital Henri Mondor

🇫🇷

Créteil, France

AP-HM - Hopital de la Timone

🇫🇷

Marseille, France

Houston Methodist Hospital

🇺🇸

Houston, Texas, United States

AP-HP Hopital Bichat - Claude Bernard

🇫🇷

Paris, France

Charite Universitaetsmedizin Berlin

🇩🇪

Berlin, Germany

Rigshospitalet

🇩🇰

Copenhagen, Denmark

CHU Rennes - Hopital Pontchaillou

🇫🇷

Rennes, France

Aarhus University Hospital

🇩🇰

Aarhus, Denmark

CHU de Toulouse - Hopital Rangueil

🇫🇷

Toulouse, France

University of Arizona

🇺🇸

Tucson, Arizona, United States

Cedars-Sinai Medical Center

🇺🇸

Los Angeles, California, United States

Western Greater Los Angeles VA Medical Center

🇺🇸

Los Angeles, California, United States

Stanford University

🇺🇸

Palo Alto, California, United States

University of Colorado Denver

🇺🇸

Denver, Colorado, United States

Yale University School of Medicine

🇺🇸

New Haven, Connecticut, United States

MedStar Washington Hospital Center - MedStar Heart and Vascular Institute

🇺🇸

Washington, District of Columbia, United States

Emory University School of Medicine

🇺🇸

Atlanta, Georgia, United States

Northwestern University

🇺🇸

Chicago, Illinois, United States

Indiana University Health

🇺🇸

Indianapolis, Indiana, United States

University of Kentucky Gill Heart Institute

🇺🇸

Lexington, Kentucky, United States

Johns Hopkins University

🇺🇸

Baltimore, Maryland, United States

Brigham and Women's Hospital

🇺🇸

Boston, Massachusetts, United States

Boston University School of Medicine

🇺🇸

Boston, Massachusetts, United States

University of Michigan

🇺🇸

Ann Arbor, Michigan, United States

Barbara Ann Karmanos Cancer Institute

🇺🇸

Detroit, Michigan, United States

Mayo Clinic

🇺🇸

Rochester, Minnesota, United States

St. Luke's Hospital

🇺🇸

Kansas City, Missouri, United States

New York University (NYU) School of Medicine - Langone Medical Center

🇺🇸

New York, New York, United States

Columbia University Medical Center

🇺🇸

New York, New York, United States

Duke University Medical Center

🇺🇸

Durham, North Carolina, United States

Cleveland Clinic

🇺🇸

Cleveland, Ohio, United States

Oregon Health and Science University (OHSU)

🇺🇸

Portland, Oregon, United States

Penn Presbyterian Medical Center

🇺🇸

Philadelphia, Pennsylvania, United States

Allegheny General Hospital

🇺🇸

Pittsburgh, Pennsylvania, United States

University of Pittsburgh Medical Center

🇺🇸

Pittsburgh, Pennsylvania, United States

Medical University of South Carolina

🇺🇸

Charleston, South Carolina, United States

University of Texas Southwestern Medical Center

🇺🇸

Dallas, Texas, United States

Baylor College of Medicine

🇺🇸

Houston, Texas, United States

Virginia Commonwealth University - Department of Internal Medicine

🇺🇸

Richmond, Virginia, United States

Fundacion Favalro

🇦🇷

Buenos Aires, Argentina

Hospital Italiano de Buenos Aires

🇦🇷

Ciudad Autonoma de Buenos Aire, Argentina

Fundacion Favaloro

🇦🇷

Ciudad Autonoma de Buenos Aire, Argentina

Hospital Privado de Rosario

🇦🇷

Rosario, Argentina

The Canberra Hospital

🇦🇺

Garran, Australian Capital Territory, Australia

Westmead Hospital

🇦🇺

Westmead, New South Wales, Australia

Cairns Hospital

🇦🇺

Cairns, Queensland, Australia

Eastern Health - Box Hill Hospital

🇦🇺

Box Hill, Victoria, Australia

Fiona Stanley Hospital

🇦🇺

Perth, Western Australia, Australia

Royal Adelaide Hospital

🇦🇺

Adelaide, Australia

The Alfred Hospital

🇦🇺

Melbourne, Australia

Princess Alexandra Hospital

🇦🇺

Woolloongabba, Australia

Medizinische Universitaet Innsbruck

🇦🇹

Innsbruck, Austria

Universitaesklinikum St. Poelten

🇦🇹

St. Polten, Austria

Antwerp University Hospital

🇧🇪

Edegem, Belgium

UZ Leuven

🇧🇪

Leuven, Belgium

HCFMRP - Hospital das Clinicas da Faculdade de Medicina de Ribeirao Preto

🇧🇷

Ribeirão Preto, Brazil

Instituto Dante Pazzanese de Cardiologia

🇧🇷

São Paulo, Brazil

PSEG Centro de Pesquisa Clinica S.A.

🇧🇷

São Paulo, Brazil

Alberta Health Services - University of Calgary

🇨🇦

Calgary, Alberta, Canada

Vancouver Coastal Health Research Institute

🇨🇦

Vancouver, British Columbia, Canada

University Health Network - Toronto General Hospital

🇨🇦

Toronto, Ontario, Canada

McGill University Health Centre

🇨🇦

Montréal, Quebec, Canada

Fakultni nemocnice u sv. Anny v Brne

🇨🇿

Brno, Czechia

Universitaetsklinikum Heidelberg

🇩🇪

Heidelberg, Germany

Universitaetsklinikum Wuerzburg

🇩🇪

Würzburg, Germany

Semmelweis Egyetem Belgyogyaszati es Hematologiai Klinika

🇭🇺

Budapest, Hungary

Rambam Health Care Campus

🇮🇱

Haifa, Israel

Hadassah University Hospital, Ein Karem

🇮🇱

Jerusalem, Israel

Sheba Medical Center

🇮🇱

Tel HaShomer, Israel

Azienda Ospedaliero-Universitaria Careggi

🇮🇹

Firenze, Italy

Ospedale Policlinico San Martino IRCCS

🇮🇹

Genova, Italy

Fondazione IRCCS Policlinico San Matteo

🇮🇹

Pavia, Italy

Azienda sanitaria universitaria Giuliano Isontina (ASU GI) - Ospedale di Cattinara

🇮🇹

Trieste, Italy

Chonnam National University Hospital

🇰🇷

Gwangju, Korea, Republic of

Seoul National University Hospital

🇰🇷

Seoul, Korea, Republic of

Severance Hospital, Yonsei University Health System

🇰🇷

Seoul, Korea, Republic of

Instituto Nacional de Ciencias Medicas y Nutricion Salvador Zubiran

🇲🇽

Ciudad de mexico, Mexico

University Medical Center

🇳🇱

Groningen, Netherlands

Universitair Medisch Centrum Utrecht

🇳🇱

Utrecht, Netherlands

New Zealand Clinical Research

🇳🇿

Christchurch, New Zealand

Oslo University Hospital - Rikshospitalet

🇳🇴

Oslo, Norway

Centro Hospitalar Universitario de Lisboa Norte

🇵🇹

Lisbon, Portugal

Centro Hospitalar Universitario do Porto

🇵🇹

Porto, Portugal

National Heart Centre

🇸🇬

Singapore, Singapore

National University Hospital

🇸🇬

Singapore, Singapore

Hospital Universitari de Bellvitge

🇪🇸

Barcelona, Spain

Hospital Universitario Vall d'Hebron

🇪🇸

Barcelona, Spain

Hospital Universitario Puerta de Hierro

🇪🇸

Majadahonda, Spain

Hospital Universitario Virgen de la Victoria

🇪🇸

Málaga, Spain

Hospital Universitario Son Llatzer

🇪🇸

Palma De Mallorca, Spain

Karolinska University Hospital

🇸🇪

Stockholm, Sweden

University Hospital of Umea

🇸🇪

Umea, Sweden

Far Eastern Memorial Hospital

🇨🇳

New Taipei City, Taiwan

National Taiwan University Hospital

🇨🇳

Taipei, Taiwan

Taipai Veterans General Hospital

🇨🇳

Taipei, Taiwan

Synexus Midlands Clinical Research Centre

🇬🇧

Birmingham, United Kingdom

Synexus Wales Clinical Research Centre

🇬🇧

Cardiff, United Kingdom

Synexus Scotland Clinical Research Centre

🇬🇧

Glasgow, United Kingdom

Synexus Hexham Clinical Research Centre

🇬🇧

Hexham, United Kingdom

Synexus Merseyside Clinical Research Centre

🇬🇧

Liverpool, United Kingdom

Richmond Pharmacology

🇬🇧

London, United Kingdom

Synexus Manchester Clinical Research Centre

🇬🇧

Manchester, United Kingdom

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