MedPath

Neuroblastoma Maintenance Therapy Trial

Phase 2
Recruiting
Conditions
Neuroblastoma
Interventions
Drug: Difluoromethylornithine (DFMO)
Registration Number
NCT02679144
Lead Sponsor
Giselle Sholler
Brief Summary

Difluoromethylornithine (DFMO) will be used in an open label, single agent, multicenter, study for patients with neuroblastoma in remission. In this study subjects will receive 730 Days of oral difluoromethylornithine (DFMO) at a dose of 750 mg/m2 ± 250 mg/m2 BID (strata 1, 2, 3, and 4) OR 2500 mg/m2 BID (stratum 1B) on each day of study. This study will focus on the use of DFMO in high risk neuroblastoma patients that are in remission as a strategy to prevent recurrence.

Detailed Description

Not available

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
258
Inclusion Criteria
  • All patients must have a pathologically confirmed diagnosis of neuroblastoma, < 30.99 years of age and classified as high risk at the time of diagnosis. Exception: patients who are initially diagnosed as non-high-risk neuroblastoma, but later converted (and/or relapsed) to high risk neuroblastoma are also eligible.

  • All patients must be in complete remission (CR):

    1. No evidence of residual disease on scan
    2. No evidence of disease metastatic to bone marrow.
  • Specific Criteria by Stratum:

Stratum 1/1B: All patients must have completed standard upfront therapy that replicates treatment which patients who were enrolled on ANBL0032 received, including:

intensive induction chemotherapy and (if feasible) resection of primary tumor, followed by: consolidation with high-dose chemotherapy with stem cell transplant and radiotherapy, followed by: immunotherapy with Ch14.18/IL-2/GM-CSF (dinutuximab) and retinoic acid;.

All subjects on Stratum 1/B must have also met the following criteria:

• A pre-transplant disease status evaluation that met International Neuroblastoma Response Criteria (INRC) for CR (complete response), VGPR (very good partial response), or PR (partial response) for primary site, soft tissue metastases and bone metastases. Patients who meet those criteria must also meet the protocol-specified criteria for bone marrow response prior to transplant as outlined below: No more than 10% tumor involvement (based on total nucleated cellular content) seen on any specimen from a bilateral bone marrow aspirate/biopsy.

Stratum 2: Neuroblastoma that is in first complete remission following standard upfront therapy different from that described for Stratum 1.

Stratum 3: Neuroblastoma that failed to have a response of at least PR following induction chemotherapy and surgical resection of the primary tumor, but that has achieved CR following additional therapy.

Stratum 4: Patients who have achieved a second or subsequent CR following relapse(s).

  • Pre-enrollment tumor survey: Prior to enrollment on this study, a determination of mandatory disease staging must be performed:

    • Tumor imaging studies including
    • Bilateral bone marrow aspirates and biopsy
    • This disease assessment is required for eligibility and preferably should be done within 2 weeks prior to enrollment, but must be done within a maximum of 4 weeks before enrollment.
  • Timing from prior therapy:

Stratum 1/1B: Enrollment no later than 60 days after completion of upfront therapy, (last dose of cis-retinoic acid) with a maximum of 6 cycles of cis-retinoic acid maintenance therapy.

Stratum 2, 3 and 4: Enrollment no later than 60 days from last dose of the most recent therapy.

  • Patients must have a Lansky or Karnofsky Performance Scale score of > 50% and patients must have a life expectancy of ≥ 2 months.

  • All clinical and laboratory studies for organ functions to determine eligibility must be performed within 7 days prior to enrollment unless otherwise indicated below.

  • Patients must have adequate organ functions at the time of registration:

    • Hematological: Total absolute phagocyte count ≥1000/μL
    • Liver: Subjects must have adequate liver function
    • Renal: Adequate renal function
  • Females of childbearing potential must have a negative pregnancy test. Patients of childbearing potential must agree to use an effective birth control method. Female patients who are lactating must agree to stop breast-feeding.

  • Written informed consent in accordance with institutional and FDA (food and drug administration) guidelines must be obtained from all subjects (or patients' legal representative).

Exclusion Criteria
  • BSA (Body Surface Area) of <0.25 m2.
  • Investigational Drugs: Subjects who are currently receiving another investigational drug are excluded from participation.
  • Anti-cancer Agents: Subjects who are currently receiving other anticancer agents are not eligible. Subjects must have fully recovered from hematological and bone marrow suppression effects of prior chemotherapy.
  • Infection: Subjects who have an uncontrolled infection are not eligible until the infection is judged to be well controlled in the opinion of the investigator.
  • Subjects who, in the opinion of the investigator, may not be able to comply with the safety monitoring requirements of the study, or in whom compliance is likely to be suboptimal, should be excluded.

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
Difluoromethylornithine (DFMO)Difluoromethylornithine (DFMO)Subjects will receive 730 Days of oral difluoromethylornithine (DFMO) at a dose of 750 mg/m2 ± 250 mg/m2 BID (strata 1, 2, 3, and 4) OR 2500 mg/m2 BID (stratum 1B) on each day of study.
Primary Outcome Measures
NameTimeMethod
Number of participants with event free survival (EFS) during study.2 years
Secondary Outcome Measures
NameTimeMethod
Peak Plasma Concentration (Cmax)1 year

Pharmacokinetic assay

Length of time that participants experience Overall Survival (OS)7 years
Number of Participants with Adverse Events as a Measure of Safety and Tolerability2 years
Area under the plasma concentration versus time curve (AUC)1 year

Pharmacokinetic assay

Number of participants with ODC (Ornithine decarboxylase) single nucleotide polymorphisms.1 year
Time to reach Peak Plasma Concentration (Tmax)1 year

Pharmacokinetic assay

Trial Locations

Locations (47)

St. Lukes

🇺🇸

Boise, Idaho, United States

Children's Medical Center

🇺🇸

Dallas, Texas, United States

UCSF Benioff Children's Hospital Oakland-

🇺🇸

Oakland, California, United States

Arkansas Children's Hospital

🇺🇸

Little Rock, Arkansas, United States

Hackensack University Medical Center

🇺🇸

Hackensack, New Jersey, United States

Nationwide Children's Hospital

🇺🇸

Columbus, Ohio, United States

Tufts Medical Center

🇺🇸

Boston, Massachusetts, United States

New York University

🇺🇸

New York, New York, United States

Helen DeVos Children's Hospital

🇺🇸

Grand Rapids, Michigan, United States

University of Massachusetts Medical School Worcester

🇺🇸

Worcester, Massachusetts, United States

Cleveland Clinic Children's

🇺🇸

Cleveland, Ohio, United States

Rady Children's Hospital

🇺🇸

San Diego, California, United States

Montreal Children's Hospital

🇨🇦

Montreal, Quebec, Canada

Janesway Children's Health and Rehabilitation Centre

🇨🇦

Saint John's, Newfoundland and Labrador, Canada

Penn State Milton S. Hershey Medical Center and Children's Hospital

🇺🇸

Hershey, Pennsylvania, United States

All Children's Hospital Johns Hopkins Medicine

🇺🇸

Saint Petersburg, Florida, United States

Gina Martin

🇺🇸

Saint Louis, Missouri, United States

Augusta University Health

🇺🇸

Augusta, Georgia, United States

Levine Children's Hospital

🇺🇸

Charlotte, North Carolina, United States

CIUSSS de l'Estrie-CHUS

🇨🇦

Sherbrooke, Quebec, Canada

Texas Children's Cancer and Hematology Centers

🇺🇸

Houston, Texas, United States

UHC Sainte-Justine

🇨🇦

Montréal, Quebec, Canada

Children's Hospital of The King's Daughters

🇺🇸

Norfolk, Virginia, United States

CancerCare Manitoba

🇨🇦

Winnipeg, Manitoba, Canada

University of Alabama, Children's of Alabama

🇺🇸

Birmingham, Alabama, United States

Rocky Mountain Pediatric Hematology

🇺🇸

Denver, Colorado, United States

Children's Hospital and Clinics of Minnesota

🇺🇸

Minneapolis, Minnesota, United States

Primary Children's Hospital

🇺🇸

Salt Lake City, Utah, United States

Duke University

🇺🇸

Durham, North Carolina, United States

Randall Children's Hospital

🇺🇸

Portland, Oregon, United States

Monroe Carrell Jr. Children's Hospital at Vanderbilt

🇺🇸

Nashville, Tennessee, United States

CHUQ

🇨🇦

Quebec City, Quebec, Canada

Medical College of Wisconsin

🇺🇸

Milwaukee, Wisconsin, United States

Connecticut Children's Hospital

🇺🇸

Hartford, Connecticut, United States

Rebecca McFall

🇺🇸

Chicago, Illinois, United States

Alberta Children's Hospital

🇨🇦

Calgary, Alberta, Canada

St. Joseph's Children's Hospital

🇺🇸

Tampa, Florida, United States

Children's Mercy Hospitals and Clinics

🇺🇸

Kansas City, Missouri, United States

Medical University of South Carolina

🇺🇸

Charleston, South Carolina, United States

Arnold Palmer Hospital for Children

🇺🇸

Orlando, Florida, United States

University of Louisville

🇺🇸

Louisville, Kentucky, United States

Virginia Commonwealth University

🇺🇸

Richmond, Virginia, United States

University of Florida

🇺🇸

Gainesville, Florida, United States

Kapiolani Medical Center for Women and Children

🇺🇸

Honolulu, Hawaii, United States

Dell Children's Blood and Cancer Center

🇺🇸

Austin, Texas, United States

Kentucky Children's Hospital

🇺🇸

Lexington, Kentucky, United States

Hasbro Children's Hospital

🇺🇸

Providence, Rhode Island, United States

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