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Fontan Circulation and Cardiopulmonary Function: Prognostic Factors, Hemodynamics and Long-term Effects

Completed
Conditions
Congenital Heart Disease
Registration Number
NCT02378857
Lead Sponsor
Oslo University Hospital
Brief Summary

Cross-sectional study of a national cohort of adolescents with univentricular congenital heart defects and Fontan type palliation.

Detailed Description

A study group of 40-50 individuals will be investigated by non-invasive and invasive methods, including echocardiography at rest and during exercise, heart catheterization with advanced hemodynamic studies, cardiac and abdominal MRI, abdominal ultrasound and transient elastography, quality of life assessment and cardiopulmonary exercise testing. A selection of tests will be performed in a healthy control group as well.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
76
Inclusion Criteria
  • age, heart defect, heart surgery and type of palliation/correction, informed consent
Exclusion Criteria
  • non-consenting, contraindications or increased risk to perform study tests (i.e. metal parts prohibiting MRI, motoric impairment prohibiting CPET)

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Quality of life and psycho-social outcomeCurrent at time of inclusion

Status as found by questionnaire

Hemodynamic statusCurrent at time of inclusion

Status as found by invasive and non-invasive assessment

Structural and functional hepatic changesCurrent at time of inclusion

Status as found by non-invasive assessment

Cardio-pulmonary function and functional reserveCurrent at time of inclusion

Status as found by non-invasive assessment

Secondary Outcome Measures
NameTimeMethod

Trial Locations

Locations (1)

Oslo University Hospital, Rikshospitalet, Department of Paediatric Cardiology

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Oslo, Norway

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