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Study of TL-895 in Subjects With Myelofibrosis or Indolent Systemic Mastocytosis

Phase 2
Recruiting
Conditions
Myelofibrosis
Indolent Systemic Mastocytosis
Interventions
Drug: Placebo
Registration Number
NCT04655118
Lead Sponsor
Telios Pharma, Inc.
Brief Summary

This study evaluates TL-895, a potent, orally-available and highly selective irreversible tyrosine kinase inhibitor for the treatment of Myelofibrosis (Cohorts 1-3) or Indolent Systemic Mastocytosis (Cohort 5). Participants must be diagnosed with Myelofibrosis and be relapsed/refractory (e.g., having failed prior therapy), intolerant, or ineligible to receive JAKi treatment, or be diagnosed with Indolent Systemic Mastocytosis.

Detailed Description

Not available

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
121
Inclusion Criteria
  • Adults ≥18 years of age
  • Confirmed diagnosis of PMF, post-PV MF, or post-ET MF, as assessed by treating physician according to the World Health Organization (WHO) criteria
  • Eastern Cooperative Oncology Group (ECOG) performance status of ≤2
  • Adequate hematologic, hepatic, and renal functions
  • MF symptoms as defined by having at least 2 symptoms with an average baseline (Day -7 to Day -1) score of at least 1 for each of the 2 symptoms per MFSAF v4.0
  • Cohort 3 only: Ineligibility for JAKi treatment with a platelet count of ≥ 25 and < 50 x 10^9/L

Key

Exclusion Criteria
  • Prior treatment with any BTK or BMX inhibitors
  • Prior treatment with JAKi within 28 days prior to study treatment
  • Prior splenectomy or splenic irradiation within 24 weeks prior to first dose of study treatment

Cohort 5

Key Inclusion Criteria:

  • Adults ≥18 years of age
  • Confirmed diagnosis of ISM as defined by WHO diagnostic criteria based on review of bone marrow biopsy pathology report results
  • Subject must have moderate-to-severe symptoms

Key Exclusion Criteria:

  • Prior treatment with any BTK or BMX inhibitors
  • Prior treatment with Avapritinib, bezuclastinib, or BLU-263/elenestinib
  • Diagnosis with another myeloproliferative disorder

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Cohort 1a, Relapsed/Refractory MyelofibrosisTL-895150 mg of TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle.
Cohort 2a, JAKi Intolerant MyelofibrosisTL-895150 mg of TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle.
Cohort 5e, Indolent Systemic MastocytosisPlaceboPlacebo to match TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle in combination with BSC.
Cohort 1b, Relapsed/Refractory MyelofibrosisTL-895300 mg of TL-895 will be administered orally, once daily (QD) continuously starting on Day 1 in a 28-day cycle.
Cohort 1c, Relapsed/Refractory MyelofibrosisTL-895300 mg of TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle.
Cohort 1d, Relapsed/Refractory MyelofibrosisTL-895450 mg of TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle.
Cohort 2b, JAKi Intolerant MyelofibrosisTL-895300 mg of TL-895 will be administered orally, once daily (QD) continuously starting on Day 1 in a 28-day cycle.
Cohort 3a, JAKi Ineligible Myelofibrosis with platelet count of ≥ 25 and < 50 × 109/LTL-895150 mg of TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle.
Cohort 5a, Indolent Systemic MastocytosisTL-895TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle in combination with best supportive care (BSC).
Cohort 5c, Indolent Systemic MastocytosisTL-895TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle in combination with BSC.
Cohort 3b, JAKi Ineligible Myelofibrosis with platelet count of ≥ 25 and < 50 × 109/LTL-895300 mg of TL-895 will be administered orally, once daily (QD) continuously starting on Day 1 in a 28-day cycle.
Cohort 5b, Indolent Systemic MastocytosisTL-895TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle in combination with BSC.
Cohort 5d, Indolent Systemic MastocytosisTL-895TL-895 will be administered orally, twice daily (BID) continuously starting on Day 1 in a 28-day cycle in combination with BSC.
Primary Outcome Measures
NameTimeMethod
Cohorts 1-3: Determine the RP2D of TL-8959 months

The RP2D for Cohorts 1, 2 and 3 will be reported

Cohort 5: Determine the RP2D of TL-895Week 24

The RP2D for Cohort 5 will be reported

Secondary Outcome Measures
NameTimeMethod
Cohort 5: Changes in patient reported symptomsWeek 12

Mean change in patient reported symptom assessment

Cohorts 1-3: Spleen volume reduction (SVR) rateWeek 24

The proportion of subjects achieving ≥35% SVR at Week 24 by MRI or CT scan (central review).

Trial Locations

Locations (52)

University of Colorado - Aurora Cancer Center

🇺🇸

Aurora, Colorado, United States

Mayo Clinic - Rochester

🇺🇸

Rochester, Minnesota, United States

Gabrail Cancer Center

🇺🇸

Canton, Ohio, United States

University of Cincinnati (UC) Physicians Company, LLC

🇺🇸

Cincinnati, Ohio, United States

Ohio State University

🇺🇸

Columbus, Ohio, United States

University of Texas, MD Anderson Cancer Center

🇺🇸

Houston, Texas, United States

Border Medical Oncology

🇦🇺

East Albury, Australia

Southern Oncology Specialists

🇦🇺

Kogarah, Australia

Royal Perth Hospital

🇦🇺

Perth, Australia

St Vincent's Hospital Sydney

🇦🇺

Sydney, Australia

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University of Colorado - Aurora Cancer Center
🇺🇸Aurora, Colorado, United States

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