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A Study of DS-1211b in Individuals With PseudoXanthoma Elasticum

Phase 2
Completed
Conditions
Pseudoxanthoma Elasticum
Interventions
Other: Placebo
Registration Number
NCT05569252
Lead Sponsor
Daiichi Sankyo
Brief Summary

This study was designed to evaluate the safety, tolerability, pharmacodynamics (PD) of DS-1211b, and pharmacokinetics (PK) in individuals with Pseudoxanthoma elasticum (PXE). PXE is a rare disease that is associated with significant risks of visual impairments and comorbidity from peripheral and cardiovascular diseases, and adversely impacts the quality of life in afflicted individuals.

Detailed Description

DS-1211b, a potent small-molecule inhibitor of tissue-nonspecific alkaline phosphatase, is being developed for the treatment ectopic calcification diseases such as PXE. This study will assess DS-1211b (low-, middle-, and high-dose tablets) administered once daily for 12 weeks in individuals with PXE.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
65
Inclusion Criteria
  • Signed and dated informed consent
  • Male or female participants aged 18 to 75 years at screening
  • Have an established diagnosis of PXE
  • Fully vaccinated for coronavirus disease 2019 (COVID-19) per current Center for Disease Control and Prevention guidelines

Key

Exclusion Criteria
  • Have a history of bone fracture in the past 6 months
  • Have a history of active metabolic bone disease, excluding osteopenia or osteoporosis without fragility fracture
  • Have a history of calcium pyrophosphate deposit disease
  • Have a history of hypophosphatasia
  • Have a history of untreated hyperparathyroidism
  • Participated in another interventional research study in the past 60 days.
  • Used bisphosphonate in the preceding 12 months or had plans to use bisphosphonate during the study.
  • Received Vitamin B6 supplementation >5 mg/day in the month prior to screening and during the study
  • Initiated or changed dose of Vitamin D in the preceding month prior to screening
  • Have an alkaline phosphatase <lower limit of normal (LLN) range
  • Have a QTcF interval duration >450 ms at screening
  • Have moderate to severe renal insufficiency
  • Are pregnant or breast-feeding women
  • Are female participants unwilling to use contraceptive methods
  • Have any elective surgery planned during the study period
  • Have any other significant condition (medical, psychiatric, social, or medication) that, in the judgment of the Investigator, would prevent full participation or would be inappropriate for the study

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
DS-1211b low doseDS-1211bParticipants who will be randomized to receive a DS-1211 tablet once daily for 12 weeks.
DS-1211b middle doseDS-1211bParticipants who will be randomized to receive a DS-1211b tablet once daily for 12 weeks.
PlaceboPlaceboParticipants who will be randomized to receive a placebo tablet once daily for 12 weeks.
DS-1211b high doseDS-1211bParticipants who will be randomized to receive a DS-1211b tablet once daily for 12 weeks.
Primary Outcome Measures
NameTimeMethod
Number of Participants With Treatment-emergent Adverse Events (TEAEs) in Participants Receiving DS-1211bFrom the date of signing informed consent form up to Day 98 (14 days after last dose of study drug) post-dose of 12-week treatment period

TEAEs are defined as events that start on or after the first dose of study drug or start prior to but then worsen after the first dose of study drug. Adverse events are coded using MedDRA version 26.1.

Percent Change From Baseline in Pharmacodynamic Parameter Alkaline Phosphatase (ALP) LevelsPre-dose on Days 15, 43, 84; Day 86-88 and Day 98 of 12-week treatment period

ALP levels were assessed using the IFCC serum assay.

Percent Change From Baseline in Pharmacodynamic Parameter Inorganic Pyrophosphate (PPi) LevelsPre-dose on Days 15, 43, and 84 of 12-week treatment period

PPi levels were assessed from collected plasma.

Percent Change From Baseline in Pharmacodynamic Parameter Pyridoxal 5'-Phosphate (PLP) LevelsPre-dose on Days 15, 43, 84; Day 86-88 and Day 98 of 12-week treatment period

PLP levels were assessed from collected plasma.

Secondary Outcome Measures
NameTimeMethod
Pharmacokinetic Parameter Maximum Concentration (Cmax)Day1 and Day 84 post-dose of 12-week treatment period

Pharmacokinetic parameter Cmax was estimated using population PK modeling.

Pharmacokinetic Parameter Time to Maximum Concentration (Tmax)Day 1 and Day 84 post-dose of 12-week treatment period

Pharmacokinetic parameter Tmax was assessed using population PK modeling.

Pharmacokinetic Parameter Trough Plasma Concentration (Ctrough)Day 1 and Day 84 post-dose of 12-week treatment period

Pharmacokinetic parameter Ctrough was assessed using observed concentrations at 10 hours post-dose.

Pharmacokinetic Parameter Area Under the Plasma Concentration-time Curve (AUC)Day 1 and Day 84 post-dose of 12-week treatment period

Pharmacokinetic parameter AUCtau was assessed using population PK modeling.

Trial Locations

Locations (7)

UMC Utrecht

🇳🇱

Utrecht, Netherlands

Clinical Research of Philadelphia, LLC

🇺🇸

Philadelphia, Pennsylvania, United States

Boston Neuro Research Center

🇺🇸

North Dartmouth, Massachusetts, United States

Clinilabs

🇺🇸

New York, New York, United States

Mid-Atlantic Epilepsy and Sleep Center

🇺🇸

Bethesda, Maryland, United States

Infinity Medical Research Inc

🇺🇸

North Dartmouth, Massachusetts, United States

Frontage Clinical Services, Inc.

🇺🇸

Secaucus, New Jersey, United States

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