MedPath

Cixutumumab in Treating Patients With Relapsed or Refractory Solid Tumors

Phase 2
Completed
Conditions
Adult Rhabdomyosarcoma
Adult Synovial Sarcoma
Recurrent Adrenocortical Carcinoma
Recurrent Childhood Rhabdomyosarcoma
Recurrent Adult Soft Tissue Sarcoma
Recurrent Retinoblastoma
Recurrent Childhood Liver Cancer
Recurrent Osteosarcoma
Childhood Hepatoblastoma
Childhood Synovial Sarcoma
Interventions
Biological: cixutumumab
Other: laboratory biomarker analysis
Registration Number
NCT00831844
Lead Sponsor
National Cancer Institute (NCI)
Brief Summary

This phase II trial is studying the side effects and how well cixutumumab works in treating patients with relapsed or refractory solid tumors. Monoclonal antibodies, such as cixutumumab, can block tumor growth in different ways. Some block the ability of tumor cells to grow and spread. Others find tumor cells and help kill them or carry tumor-killing substances to them.

Detailed Description

PRIMARY OBJECTIVES:

I. To determine the response rate to IMC-A12 (cixutumumab) administered in various strata of recurrent/refractory malignant solid tumors in childhood and young adulthood.

II. To further define and describe the toxicities of IMC-A12. III. To further characterize the pharmacokinetics of IMC-A12.

SECONDARY OBJECTIVES:

I. To examine the relationship between tumor expression of insulin-like growth factor (IGF)-I, IGF-II, and IGF-I receptor (IR) and response to IMC-A12.

II. To determine the human anti-human antibody (HAHA) response after treatment with IMC-A12.

III. To further evaluate the effect of IMC-A12 on circulating levels of proteins involved in linear growth and glucose homeostasis, including IGF-I, IGF-II, IGF-BP3, growth hormone, insulin, and C-peptide.

OUTLINE: This is a multicenter study. Patients are stratified according to disease type.

Patients receive cixutumumab intravenously (IV) over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.

Patients undergo blood sample collection periodically for correlative laboratory studies. Samples are analyzed for IGF-I, IGF-II, IGF-BP3, growth hormone, insulin, and C-peptide levels and for immunogenicity.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
116
Inclusion Criteria
  • Histologically confirmed malignant solid tumor, including the following:

    • Osteosarcoma
    • Ewing sarcoma/peripheral primitive neuroectodermal tumor
    • Rhabdomyosarcoma
    • Neuroblastoma
    • Wilms tumor
    • Synovial sarcoma
    • Hepatoblastoma
    • Adrenocortical carcinoma
    • Retinoblastoma
  • No known curative therapy or therapy proven to prolong survival with an acceptable quality of life exists

  • Radiographically measurable disease*, defined as ≥ 1 unidimensionally measurable lesion ≥ 20 mm by MRI or CT scan or ≥ 10 mm by spiral CT scan

    • The following are not considered measurable disease:

      • Ascites, pleural effusions, or other malignant fluid collections
      • Bone marrow infiltration by tumor
      • Lesions detected only by non-MIBG nuclear medicine studies (e.g., bone scan)
      • Previously irradiated lesions that have not demonstrated clear progression post-radiotherapy
  • No known Central Nervous System (CNS) metastases unless they were treated by surgery or radiotherapy AND are stable with no recurrent lesions for ≥ 3 months

  • Lansky or Karnofsky performance status (PS) 50-100% OR Eastern Cooperative Oncology Group (ECOG) PS 0-2

  • Absolute neutrophil count (ANC) ≥ 1,000/mm³ (> 250/mm³ for patients with neuroblastoma)

  • Platelet count ≥ 75,000/mm³ (> 25,000/mm³ for patients with neuroblastoma) (transfusion independent)

  • Hemoglobin ≥ 8.0 g/dL (≥ 7.5 g/dL for patients with neuroblastoma) (RBC transfusion allowed)

  • Creatinine clearance or radioisotope glomerular filtration rate ≥ 70 mL/min OR serum creatinine normal based on age/gender as follows:

    • ≤ 0.4 mg/dL (for patients 1 to 5 months of age)
    • ≤ 0.5 mg/dL (for patients 6 to 11 months of age)
    • ≤ 0.6 mg/dL (for patients 1 year of age)
    • ≤ 0.8 mg/dL (for patients 2 to 5 years of age)
    • ≤ 1 mg/dL (for patients 6 to 9 years of age)
    • ≤ 1.2 mg/dL (for patients 10 to 12 years of age)
    • ≤ 1.5 mg/dL (males) or 1.4 mg/dL (females) (for patients 13 to 15 years of age)
    • ≤ 1.7 mg/dL (males) or 1.4 mg/dL (females) (for patients ≥ 16 years of age)
  • Total bilirubin ≤ 1.5 times upper limit of normal for age

  • Alanine transaminase (ALT) ≤ 110 U/L

  • Serum albumin ≥ 2 g/dL

  • Blood glucose normal

  • Not pregnant or nursing

  • Negative pregnancy test

  • Fertile patients must use effective contraception during and for 3 months after completion of study treatment

  • Able to comply with safety monitoring requirements of study

  • No history of allergic reactions attributed to compounds of similar chemical or biologic composition to study drug

  • No uncontrolled infection

  • No known type I or II diabetes mellitus

  • Recovered from prior chemotherapy, immunotherapy, or radiotherapy

  • More than 3 weeks since prior myelosuppressive chemotherapy (6 weeks for nitrosoureas)

  • At least 7 days since prior hematopoietic growth factors (14 days for pegfilgrastim)

  • At least 6 weeks since prior monoclonal antibody therapy

  • At least 7 days since other prior antineoplastic biologic agents

  • No prior monoclonal antibody targeting the IGF-IR

  • No prior small molecule kinase inhibitors of IGF-IR

  • At least 2 weeks since prior local palliative (small port) radiotherapy

  • At least 3 months since prior total-body irradiation, craniospinal radiotherapy, or radiotherapy to ≥ 50% of the pelvis

  • At least 6 weeks since other prior substantial bone marrow radiotherapy

  • At least 2 months since prior stem cell transplantation

    • No evidence of graft-versus-host disease
  • Concurrent corticosteroids allowed provided dose is stable or decreasing over the past 7 days

    • Intermittent use of corticosteroids to manage infusional reactions allowed
  • No other concurrent anticancer therapy, including chemotherapy, radiotherapy, immunotherapy, or biologic therapy

  • No other concurrent investigational agents

  • No concurrent insulin or growth hormone therapy

Exclusion Criteria

Not provided

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
Group 3 - Recurrent or Refractory Rhabdomyosarcomalaboratory biomarker analysisGroup 3 - Recurrent or Refractory Rhabdomyosarcoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 4-Recurrent or Refractory Adrenocortical CarcinomacixutumumabGroup 4 - Recurrent or Refractory Adrenocortical Carcinoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 4-Recurrent or Refractory Adrenocortical Carcinomalaboratory biomarker analysisGroup 4 - Recurrent or Refractory Adrenocortical Carcinoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 6 - Neuroblastoma-MIBG Positive Without Measurable DiseasecixutumumabGroup 6 - Recurrent or Refractory Neuroblastoma -meta-iodobenzylguanidine (MIBG) Positive Without Measurable Disease. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 2 - Recurrent or Refractory Synovial Sarcomalaboratory biomarker analysisGroup 2 - Recurrent or Refractory Synovial Sarcoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 1 - Recurrent or Refractory HepatoblastomacixutumumabGroup 1 - Recurrent or Refractory Hepatoblastoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 5-Ewing Sarcoma/Peripheral Primitive Neuroectodermal TumorcixutumumabGroup 5 - Recurrent or Refractory Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 1 - Recurrent or Refractory Hepatoblastomalaboratory biomarker analysisGroup 1 - Recurrent or Refractory Hepatoblastoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 3 - Recurrent or Refractory RhabdomyosarcomacixutumumabGroup 3 - Recurrent or Refractory Rhabdomyosarcoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 2 - Recurrent or Refractory Synovial SarcomacixutumumabGroup 2 - Recurrent or Refractory Synovial Sarcoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 5-Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumorlaboratory biomarker analysisGroup 5 - Recurrent or Refractory Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 6 - Neuroblastoma-MIBG Positive Without Measurable Diseaselaboratory biomarker analysisGroup 6 - Recurrent or Refractory Neuroblastoma -meta-iodobenzylguanidine (MIBG) Positive Without Measurable Disease. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 7-Neuroblastoma with measurable diseaselaboratory biomarker analysisGroup 7 - Recurrent or Refractory Neuroblastoma -With Measurable Disease. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Grp 7-Neuroblastoma with measurable diseasecixutumumabGroup 7 - Recurrent or Refractory Neuroblastoma -With Measurable Disease. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 10 - Recurrent or Refractory RetinoblastomacixutumumabGroup 10 - Recurrent or Refractory Retinoblastoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 8 - Recurrent OsteosarcomacixutumumabGroup 8 - Recurrent Osteosarcoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 9 - Recurrent or Refractory Wilms TumorcixutumumabGroup 9 - Recurrent or Refractory Wilms Tumor. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 9 - Recurrent or Refractory Wilms Tumorlaboratory biomarker analysisGroup 9 - Recurrent or Refractory Wilms Tumor. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 10 - Recurrent or Refractory Retinoblastomalaboratory biomarker analysisGroup 10 - Recurrent or Refractory Retinoblastoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Group 8 - Recurrent Osteosarcomalaboratory biomarker analysisGroup 8 - Recurrent Osteosarcoma. Patients receive cixutumumab IV over 1 hour on days 1, 8, 15, and 22. Treatment repeats every 28 days for up to 24 courses in the absence of disease progression or unacceptable toxicity.
Primary Outcome Measures
NameTimeMethod
Disease ResponseFirst six treatment cycles - 24 weeks

Response rates will be calculated as the percent of patients whose best response is a Complete Response (CR) or Partial Response (PR).

Secondary Outcome Measures
NameTimeMethod

Trial Locations

Locations (105)

University of Texas Southwestern Medical Center

🇺🇸

Dallas, Texas, United States

University of Illinois

🇺🇸

Chicago, Illinois, United States

Miami Children's Hospital

🇺🇸

Miami, Florida, United States

Cincinnati Children's Hospital Medical Center

🇺🇸

Cincinnati, Ohio, United States

University of California San Francisco Medical Center-Parnassus

🇺🇸

San Francisco, California, United States

University of Alabama at Birmingham

🇺🇸

Birmingham, Alabama, United States

University of Kentucky

🇺🇸

Lexington, Kentucky, United States

Sinai Hospital of Baltimore

🇺🇸

Baltimore, Maryland, United States

Janeway Child Health Centre

🇨🇦

Saint John's, Newfoundland and Labrador, Canada

University of Arkansas for Medical Sciences

🇺🇸

Little Rock, Arkansas, United States

Southern California Permanente Medical Group

🇺🇸

Downey, California, United States

Miller Children's Hospital

🇺🇸

Long Beach, California, United States

Children's Hospital Central California

🇺🇸

Madera, California, United States

Children's Hospital Los Angeles

🇺🇸

Los Angeles, California, United States

Kaiser Permanente-Oakland

🇺🇸

Oakland, California, United States

Childrens Hospital of Orange County

🇺🇸

Orange, California, United States

Lucile Packard Children's Hospital Stanford University

🇺🇸

Palo Alto, California, United States

Connecticut Children's Medical Center

🇺🇸

Hartford, Connecticut, United States

Alfred I duPont Hospital for Children

🇺🇸

Wilmington, Delaware, United States

Lee Memorial Health System

🇺🇸

Fort Myers, Florida, United States

Lombardi Comprehensive Cancer Center at Georgetown University

🇺🇸

Washington, District of Columbia, United States

Nemours Children's Clinic - Jacksonville

🇺🇸

Jacksonville, Florida, United States

UF Cancer Center at Orlando Health

🇺🇸

Orlando, Florida, United States

University of Miami Miller School of Medicine-Sylvester Cancer Center

🇺🇸

Miami, Florida, United States

Nemours Childrens Clinic - Orlando

🇺🇸

Orlando, Florida, United States

Nemours Children's Clinic - Pensacola

🇺🇸

Pensacola, Florida, United States

Children's Healthcare of Atlanta - Egleston

🇺🇸

Atlanta, Georgia, United States

University of Hawaii

🇺🇸

Honolulu, Hawaii, United States

Saint Luke's Mountain States Tumor Institute

🇺🇸

Boise, Idaho, United States

Lurie Children's Hospital-Chicago

🇺🇸

Chicago, Illinois, United States

Loyola University Medical Center

🇺🇸

Maywood, Illinois, United States

Southern Illinois University

🇺🇸

Springfield, Illinois, United States

Saint Jude Midwest Affiliate

🇺🇸

Peoria, Illinois, United States

Indiana University Medical Center

🇺🇸

Indianapolis, Indiana, United States

Dana-Farber Cancer Institute

🇺🇸

Boston, Massachusetts, United States

Wayne State University/Karmanos Cancer Institute

🇺🇸

Detroit, Michigan, United States

University of Minnesota Medical Center-Fairview

🇺🇸

Minneapolis, Minnesota, United States

Nevada Cancer Research Foundation CCOP

🇺🇸

Las Vegas, Nevada, United States

Hackensack University Medical Center

🇺🇸

Hackensack, New Jersey, United States

UMDNJ - Robert Wood Johnson University Hospital

🇺🇸

New Brunswick, New Jersey, United States

University of New Mexico Cancer Center

🇺🇸

Albuquerque, New Mexico, United States

Albany Medical Center

🇺🇸

Albany, New York, United States

Columbia University Medical Center

🇺🇸

New York, New York, United States

Memorial Sloan-Kettering Cancer Center

🇺🇸

New York, New York, United States

New York Medical College

🇺🇸

Valhalla, New York, United States

State University of New York Upstate Medical University

🇺🇸

Syracuse, New York, United States

Carolinas Medical Center

🇺🇸

Charlotte, North Carolina, United States

Children's Hospital Medical Center of Akron

🇺🇸

Akron, Ohio, United States

Nationwide Children's Hospital

🇺🇸

Columbus, Ohio, United States

Rainbow Babies and Childrens Hospital

🇺🇸

Cleveland, Ohio, United States

Penn State Hershey Children's Hospital

🇺🇸

Hershey, Pennsylvania, United States

University of Missouri - Ellis Fischel

🇺🇸

Columbia, Missouri, United States

Children's Hospital of Pittsburgh of UPMC

🇺🇸

Pittsburgh, Pennsylvania, United States

Palmetto Health Richland

🇺🇸

Columbia, South Carolina, United States

Greenville Cancer Treatment Center

🇺🇸

Greenville, South Carolina, United States

East Tennessee Childrens Hospital

🇺🇸

Knoxville, Tennessee, United States

Texas Tech University Health Science Center-Amarillo

🇺🇸

Amarillo, Texas, United States

Vanderbilt-Ingram Cancer Center

🇺🇸

Nashville, Tennessee, United States

Medical City Dallas Hospital

🇺🇸

Dallas, Texas, United States

Cook Children's Medical Center

🇺🇸

Fort Worth, Texas, United States

Baylor College of Medicine

🇺🇸

Houston, Texas, United States

Scott and White Memorial Hospital

🇺🇸

Temple, Texas, United States

University of Texas Health Science Center at San Antonio

🇺🇸

San Antonio, Texas, United States

Primary Children's Hospital

🇺🇸

Salt Lake City, Utah, United States

Childrens Hospital-King's Daughters

🇺🇸

Norfolk, Virginia, United States

Virginia Commonwealth University

🇺🇸

Richmond, Virginia, United States

Seattle Children's Hospital

🇺🇸

Seattle, Washington, United States

Providence Sacred Heart Medical Center and Children's Hospital

🇺🇸

Spokane, Washington, United States

The Children's Hospital at Westmead

🇦🇺

Westmead, New South Wales, Australia

Royal Brisbane and Women's Hospital

🇦🇺

Herston, Queensland, Australia

Royal Children's Hospital

🇦🇺

Parkville, Victoria, Australia

Princess Margaret Hospital for Children

🇦🇺

Perth, Western Australia, Australia

British Columbia Children's Hospital

🇨🇦

Vancouver, British Columbia, Canada

CancerCare Manitoba

🇨🇦

Winnipeg, Manitoba, Canada

IWK Health Centre

🇨🇦

Halifax, Nova Scotia, Canada

Centre Hospitalier Universitaire Sainte-Justine

🇨🇦

Montreal, Quebec, Canada

Hospital for Sick Children

🇨🇦

Toronto, Ontario, Canada

Allan Blair Cancer Centre

🇨🇦

Regina, Saskatchewan, Canada

Saskatoon Cancer Centre

🇨🇦

Saskatoon, Saskatchewan, Canada

Saint Joseph Children's Hospital of Tampa

🇺🇸

Tampa, Florida, United States

University of Nebraska Medical Center

🇺🇸

Omaha, Nebraska, United States

Mayo Clinic

🇺🇸

Rochester, Minnesota, United States

Midwest Children's Cancer Center

🇺🇸

Milwaukee, Wisconsin, United States

Children's Hospital and Medical Center of Omaha

🇺🇸

Omaha, Nebraska, United States

Oregon Health and Science University

🇺🇸

Portland, Oregon, United States

University of Oklahoma Health Sciences Center

🇺🇸

Oklahoma City, Oklahoma, United States

T C Thompson Children's Hospital

🇺🇸

Chattanooga, Tennessee, United States

New York University Langone Medical Center

🇺🇸

New York, New York, United States

Children's Hospitals and Clinics of Minnesota - Minneapolis

🇺🇸

Minneapolis, Minnesota, United States

Saint John Hospital and Medical Center

🇺🇸

Detroit, Michigan, United States

All Children's Hospital

🇺🇸

Saint Petersburg, Florida, United States

Children's Hospital of Philadelphia

🇺🇸

Philadelphia, Pennsylvania, United States

University of Mississippi Medical Center

🇺🇸

Jackson, Mississippi, United States

Mary Bridge Children's Hospital and Health Center

🇺🇸

Tacoma, Washington, United States

The Childrens Mercy Hospital

🇺🇸

Kansas City, Missouri, United States

University of Rochester

🇺🇸

Rochester, New York, United States

Saint Mary's Hospital

🇺🇸

West Palm Beach, Florida, United States

University of Chicago

🇺🇸

Chicago, Illinois, United States

Newark Beth Israel Medical Center

🇺🇸

Newark, New Jersey, United States

Helen DeVos Children's Hospital at Spectrum Health

🇺🇸

Grand Rapids, Michigan, United States

Washington University School of Medicine

🇺🇸

Saint Louis, Missouri, United States

Cleveland Clinic Foundation

🇺🇸

Cleveland, Ohio, United States

Lehigh Valley Hospital - Muhlenberg

🇺🇸

Bethlehem, Pennsylvania, United States

Florida Hospital

🇺🇸

Orlando, Florida, United States

C S Mott Children's Hospital

🇺🇸

Ann Arbor, Michigan, United States

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