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Study of Biological Markers in Children With Sickle Cell Disease

Not Applicable
Conditions
Sickle Cell Disease
Interventions
Other: Blood sampling
Registration Number
NCT04839159
Lead Sponsor
Queen Fabiola Children's University Hospital
Brief Summary

Sickle cell disease is associated with significant morbi-mortality hence the interest in an early and targeted care. At present, there is no plasmatic marker able to identify infants at higher risk of developping severe complications later in life. However, recent studies have demonstrated a correlation between certain complications of the disease and biomarkers of the endothelial dysfunction characterizing it.

Investigators prospectively followed a cohort of children diagnosed with SCD through the universal neonatal screening using inflammatory and haemostatic plasmatic markers to study their annual evolution. Investigators then will evaluate potential associations between these biological markers and the occurrence of SCD related complications. A secondary objective of this study is to evaluate the repercussions of therapeutic intervention on these markers.

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Detailed Description

Not available

Recruitment & Eligibility

Status
UNKNOWN
Sex
All
Target Recruitment
41
Inclusion Criteria
  • Patient aged less than 6 months
  • Sickle cell syndrome SS, Sβthal or SC confirmed by hemoglobin electrophoresis
  • Subjects legal representatives must have signed an informed consent document indicating that they understand the purpose of and procedures required for the study and are willing to let participate their child in the study
Exclusion Criteria
  • Congenital abnormality other than sickle cell disease except for a glucose-6-phosphate-deshydrogenase
  • Prematurity
  • Initiation of the following therapies before enrollment: chronic transfusion regimen or bone marrow transplantation

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
SCD PatientBlood sampling-
Primary Outcome Measures
NameTimeMethod
Plasmatic levels of IL-6 at 12 months of age12 months of age

Measurement of plasmatic levels of IL-6 (fg/mL) by flow cytometric assay

Secondary Outcome Measures
NameTimeMethod
Plasmatic levels of IL-12 at 3 years of age3 years of age

Measurement of plasmatic levels of IL-12 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-1ß at 2 years of age2 years of age

Measurement of plasmatic levels of IL-1ß (fg/mL) by flow cytometric assay

Plasmatic levels of IL-6 at 6 months of age6 months of age

Measurement of plasmatic levels of IL-6 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-6 at 2 years of age2 years of age

Measurement of plasmatic levels of IL-6 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-8 at 12 months of age12 months of age

Measurement of plasmatic levels of IL-8 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-10 at 2 years of age2 years of age

Measurement of plasmatic levels of IL-10 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-12 at 12 months of age12 months of age

Measurement of plasmatic levels of IL-12 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-12 at 4 years of age4 years of age

Measurement of plasmatic levels of IL-12 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-12 before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of IL-12 (fg/mL) by flow cytometric assay

Plasmatic levels of TNF alpha at 3 years of age3 years of age

Measurement of plasmatic levels of TNF alpha (fg/mL) by flow cytometric assay

Plasmatic levels of TNF alpha at 4 years of age4 years of age

Measurement of plasmatic levels of TNF alpha (fg/mL) by flow cytometric assay

Plasmatic levels of ICAM-1 at 6 months of age6 months of age

Measurement of plasmatic levels of ICAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of ICAM-1 at 2 years of age2 years of age

Measurement of plasmatic levels of ICAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of ICAM-1 at 4 years of age4 years of age

Measurement of plasmatic levels of ICAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of VCAM-1 at 3 years of age3 years of age

Measurement of plasmatic levels of VCAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of IL-6 at 3 years of age3 years of age

Measurement of plasmatic levels of IL-6 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-6 at 4 years of age4 years of age

Measurement of plasmatic levels of IL-6 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-1ß at 6 months of age6 months of age

Measurement of plasmatic levels of IL-1ß (fg/mL) by flow cytometric assay

Plasmatic levels of IL-1ß at 4 years of age4 years of age

Measurement of plasmatic levels of IL-1ß (fg/mL) by flow cytometric assay

Plasmatic levels of IL-6 before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of IL-6 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-1ß at 12 months of age12 months of age

Measurement of plasmatic levels of IL-1ß (fg/mL) by flow cytometric assay

Plasmatic levels of IL-1ß at 3 years of age3 years of age

Measurement of plasmatic levels of IL-1ß (fg/mL) by flow cytometric assay

Plasmatic levels of IL-10 before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of IL-10 (fg/mL) by flow cytometric assay

Plasmatic levels of ICAM-1 at 12 months of age12 months of age

Measurement of plasmatic levels of ICAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of Vascular Endothelial Growth Factor (VEGF) at 12 months of age12 months of age

Measurement of plasmatic levels of VEGF (pg/mL) by flow cytometric assay

Plasmatic levels of IL-8 at 6 months of age6 months of age

Measurement of plasmatic levels of IL-8 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-8 at 2 years of age2 years of age

Measurement of plasmatic levels of IL-8 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-8 at 4 years of age4 years of age

Measurement of plasmatic levels of IL-8 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-10 at 6 months of age6 months of age

Measurement of plasmatic levels of IL-10 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-10 at 12 months of age12 months of age

Measurement of plasmatic levels of IL-10 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-12 at 6 months of age6 months of age

Measurement of plasmatic levels of IL-12 (fg/mL) by flow cytometric assay

Plasmatic levels of VCAM-1 at 2 years of age2 years of age

Measurement of plasmatic levels of VCAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of IL-1ß before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of IL-1ß (fg/mL) by flow cytometric assay

Plasmatic levels of IL-8 at 3 years of age3 years of age

Measurement of plasmatic levels of IL-8 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-10 at 4 years of age4 years of age

Measurement of plasmatic levels of IL-10 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-12 at 2 years of age2 years of age

Measurement of plasmatic levels of IL-12 (fg/mL) by flow cytometric assay

Plasmatic levels of TNF alpha at 2 years of age2 years of age

Measurement of plasmatic levels of TNF alpha (fg/mL) by flow cytometric assay

Plasmatic levels of ICAM-1 at 3 years of age3 years of age

Measurement of plasmatic levels of ICAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of VCAM-1 before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of VCAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of E-selectine at 6 months of age6 months of age

Measurement of plasmatic levels of E-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of IL-8 before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of IL-8 (fg/mL) by flow cytometric assay

Plasmatic levels of IL-10 at 3 years of age3 years of age

Measurement of plasmatic levels of IL-10 (fg/mL) by flow cytometric assay

Plasmatic levels of TNF alpha at 6 months of age6 months of age

Measurement of plasmatic levels of TNF alpha (fg/mL) by flow cytometric assay

Plasmatic levels of TNF alpha before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of TNF alpha (fg/mL) by flow cytometric assay

Plasmatic levels of VCAM-1 at 12 months of age12 months of age

Measurement of plasmatic levels of VCAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of TNF alpha at 12 months of age12 months of age

Measurement of plasmatic levels of TNF alpha (fg/mL) by flow cytometric assay

Plasmatic levels of ICAM-1 before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of ICAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of VCAM-1 at 6 months of age6 months of age

Measurement of plasmatic levels of VCAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of E-selectine at 12 months of age12 months of age

Measurement of plasmatic levels of E-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of E-selectine before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of E-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of P-selectine before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of P-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of Vascular Endothelial Growth Factor (VEGF) at 2 years of age2 years of age

Measurement of plasmatic levels of VEGF (pg/mL) by flow cytometric assay

Endogenous thrombin potential parameter in thrombin generation assay before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresbefore the introduction of any new sickle cell disease treatment

Measurement of endogenous thrombin potential (nM x minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Plasmatic levels of Factor VIII at 12 months of age12 months of age

Measurement of plasmatic levels of Factor VIII by flow cytometric assay

Plasmatic levels of VCAM-1 at 4 years of age4 years of age

Measurement of plasmatic levels of VCAM-1 (pg/mL) by flow cytometric assay

Plasmatic levels of E-selectine at 2 years of age2 years of age

Measurement of plasmatic levels of E-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of E-selectine at 3 years of age3 years of age

Measurement of plasmatic levels of E-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of E-selectine at 4 years of age4 years of age

Measurement of plasmatic levels of E-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of P-selectine at 6 months of age6 months of age

Measurement of plasmatic levels of P-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of P-selectine at 3 years of age3 years of age

Measurement of plasmatic levels of P-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of P-selectine at 4 years of age4 years of age

Measurement of plasmatic levels of P-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of Vascular Endothelial Growth Factor (VEGF) at 6 months of age6 months of age

Measurement of plasmatic levels of VEGF (pg/mL) by flow cytometric assay

Plasmatic levels of VEGF before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of VEGF (pg/mL) by flow cytometric assay

Peak height parameter in thrombin generation assay at 2 years of age2 years of age

Measurement of peak height (nM) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Time to peak parameter in thrombin generation assay at 12 months of age12 months of age

Measurement of time to peak (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method

Time to peak parameter in thrombin generation assay before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of time to peak (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method

Plasmatic levels of Factor VIII at 3 years of age3 years of age

Measurement of plasmatic levels of Factor VIII by flow cytometric assay

Plasmatic levels of P-selectine at 12 months of age12 months of age

Measurement of plasmatic levels of P-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of Vascular Endothelial Growth Factor (VEGF) at 3 years of age3 years of age

Measurement of plasmatic levels of VEGF (pg/mL) by flow cytometric assay

Lag time parameter in thrombin generation assay at 6 months of age6 months of age

Measurement of lag time (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Lag time parameter in thrombin generation assay at 12 months of age12 months of age

Measurement of lag time (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Lag time parameter in thrombin generation assay at 3 years of age3 years of age

Measurement of lag time (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Peak height parameter in thrombin generation assay at 12 months of age12 months of age

Measurement of peak height (nM) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Peak height parameter in thrombin generation assay at 3 years of age3 years of age

Measurement of peak height (nM) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Peak height parameter in thrombin generation assay at 4 years of age4 years of age

Measurement of peak height (nM) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Peak height parameter in thrombin generation assay before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of peak height (nM) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Time to peak parameter in thrombin generation assay at 6 months of age6 months of age

Measurement of time to peak (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method

Time to peak parameter in thrombin generation assay at 4 years of age4 years of age

Measurement of time to peak (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method

Endogenous thrombin potential parameter in thrombin generation assay at 2 years of age2 years of age

Measurement of endogenous thrombin potential (nM x minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Plasmatic VCAM-1 levels after in vitro stimulation with LPSPlasmatic level of VCAM-1 after in vitro stimulation with LPS

Measurement of plasmatic levels of VCAM-1 (pg/mL) by flow cytometric assay after in vitro stimulation with LPS

Plasmatic levels of P-selectine at 2 years of age2 years of age

Measurement of plasmatic levels of P-selectine (pg/mL) by flow cytometric assay

Plasmatic levels of Vascular Endothelial Growth Factor (VEGF) at 4 years of age4 years of age

Measurement of plasmatic levels of VEGF (pg/mL) by flow cytometric assay

Lag time parameter in thrombin generation assay before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of lag time (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Endogenous thrombin potential parameter in thrombin generation assay at 6 months of age6 months of age

Measurement of endogenous thrombin potential (nM x minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Lag time parameter in thrombin generation assay at 2 years of age2 years of age

Measurement of lag time (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Lag time parameter in thrombin generation assay at 4 years of age4 years of age

Measurement of lag time (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Peak height parameter in thrombin generation assay at 6 months of age6 months of age

Measurement of peak height (nM) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Time to peak parameter in thrombin generation assay at 2 years of age2 years of age

Measurement of time to peak (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method

Time to peak parameter in thrombin generation assay at 3 years of age3 years of age

Measurement of time to peak (minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method

Endogenous thrombin potential parameter in thrombin generation assay at 12 months of age12 months of age

Measurement of endogenous thrombin potential (nM x minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Endogenous thrombin potential parameter in thrombin generation assay at 3 years of age3 years of age

Measurement of endogenous thrombin potential (nM x minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Plasmatic levels of Factor VIII at 2 years of age2 years of age

Measurement of plasmatic levels of Factor VIII by flow cytometric assay

Plasmatic levels of Factor VIII at 4 years of age4 years of age

Measurement of plasmatic levels of Factor VIII by flow cytometric assay

Endogenous thrombin potential parameter in thrombin generation assay at 4 years of age4 years of age

Measurement of endogenous thrombin potential (nM x minutes) parameter of thrombin generation in platelet poor plasma using the Calibrated Automated Thrombogram (CAT®) method.

Plasmatic levels of Factor VIII at 6 months of age6 months of age

Measurement of plasmatic levels of Factor VIII by flow cytometric assay

Plasmatic levels of Factor VIII before the introduction of any new sickle cell disease treatment as determined by a physician according to the standard of care to which the hospital adheresBefore the introduction of any new sickle cell disease treatment

Measurement of plasmatic levels of Factor VIII by flow cytometric assay

Trial Locations

Locations (3)

CHU Saint Pierre

🇧🇪

Brussels, Belgium

Hôpital Universitaire Des Enfants Reine Fabiola

🇧🇪

Brussels, Belgium

HIS - Site Etterbeek-Ixelles

🇧🇪

Brussels, Belgium

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