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Assessing Neurodevelopment in Congenital Heart Disease.

Not Applicable
Conditions
Congenital Heart Disease
Interventions
Procedure: Sonography
Device: Magnetic Resonance Imaging
Other: Bailey Test
Procedure: Surgical intervention
Procedure: cord blood sample
Procedure: Brain monitoring
Registration Number
NCT02996630
Lead Sponsor
Hospital Universitari Vall d'Hebron Research Institute
Brief Summary

Congenital heart disease (CHD) is the most prevalent congenital malformation affecting 1 in 100 newborns per year. Children with CHD are a known risk population for brain injury, with neurodevelopmental alterations shown over time in up to 50% of cases. No adequate description exists of the type of neurocognitive anomalies or risk factors associated with CHD, and consequently no prognostic markers that may allow identification of high-risk cases are available.

Detailed Description

The main objectives of this study are: 1. to describe the neurodevelopmental outcome of patients with CHD at 24 months of age; 2. identify the subgroup with poorer outcome; and 3. evaluate the utility of fetal and postnatal diagnostic techniques for early detection of patients at risk for altered neurological outcomes.

Seven Spanish referral centers for CHD included in the research network on maternal and child health currently participating in this prospective multicentric case-control coordinated study. Fetuses with CHD (transposition of great arteries, tetralogy of Fallot, hypoplastic left heart syndrome and septal defects) will be studied from 24 weeks of gestation to 2 years of age. Diagnostic tests will be repeated throughout the study in all patients, from the fetal period to 24 months of age, and will include: fetal cerebral hemodynamic Doppler assessment, functional echocardiography, brain MRI, regional cerebral oxymetry, electroencephalography and serum neurological and cardiac biomarkers analysis. Neurodevelopmental assessment will be made at 12 months of age using the ages and stages questionnaire (ASQ) and at 24 months of age with the Bayley-III test. From this data, statistical analysis will select the most useful as predictors of damage; to be then combined and create algorithms for predicting brain damage and poor neurodevelopment. Once description has been made, we will proceed to identify amongst our results, children with the poorest neurological outcome and remark possible common prenatal and early life markers in them as well as the CHD severity they present.

While advances in early diagnosis and postnatal management have increased survival in CHD children, worrying long-term outcomes, particularly neurodevelopmental disability, have emerged as a key prognostic factor in the counseling of these pregnancies. Evidence available does not allow clinicians to assess on neurological prognosis although has opened up the possibility of finding prenatal markers of brain damage. Even though, no prospective studies have been performed until now. We present a multicentric prospective study able to recruit enough fetal CHD affected pregnancies to obtain neurological prognostic tools.

Recruitment & Eligibility

Status
UNKNOWN
Sex
Female
Target Recruitment
250
Inclusion Criteria
  • Single pregnancies
  • Major Congenital Heart Disease
  • Informed Consent Signed
Exclusion Criteria
  • Major extra-cardiac malformations
  • Parental Refusal to participate
  • Maternal Chronic Disease
  • Multiple Pregnancies

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Healthy fetusesSonographyPregnant patients carrying a healthy fetus. Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging and bailey test.
Healthy fetusesMagnetic Resonance ImagingPregnant patients carrying a healthy fetus. Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging and bailey test.
Congenital Hearth DiseaseSonographyPregnant patients carrying a fetus with a moderate-severe congenital heart disease Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging, Surgical intervention, brain monitoring and bailey test.
Congenital Hearth DiseaseSurgical interventionPregnant patients carrying a fetus with a moderate-severe congenital heart disease Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging, Surgical intervention, brain monitoring and bailey test.
Healthy fetusescord blood samplePregnant patients carrying a healthy fetus. Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging and bailey test.
Healthy fetusesBailey TestPregnant patients carrying a healthy fetus. Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging and bailey test.
Congenital Hearth DiseaseBailey TestPregnant patients carrying a fetus with a moderate-severe congenital heart disease Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging, Surgical intervention, brain monitoring and bailey test.
Congenital Hearth DiseaseBrain monitoringPregnant patients carrying a fetus with a moderate-severe congenital heart disease Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging, Surgical intervention, brain monitoring and bailey test.
Congenital Hearth DiseaseMagnetic Resonance ImagingPregnant patients carrying a fetus with a moderate-severe congenital heart disease Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging, Surgical intervention, brain monitoring and bailey test.
Congenital Hearth Diseasecord blood samplePregnant patients carrying a fetus with a moderate-severe congenital heart disease Interventions in this group will be: cord blood sample, sonography, Magnetic Resonance Imaging, Surgical intervention, brain monitoring and bailey test.
Primary Outcome Measures
NameTimeMethod
Bailey-III test punctuation45 minutes

Results in pediatric Bailey-III test scale

Secondary Outcome Measures
NameTimeMethod
Brain biometriesone day

Calcarine sulcus depth (mm)

Cerebral insulaone day

Insula (mm) measured with MRI

Cerebellumone day

Cerebellum vermis (mm) measured with MRI

Umbilical dopplerone day

Umbilical artery pulsatility index

Biparietal diameter (mm)one day

Biparietal diameter (mm) measured with MRI

Middle cerebral artery dopplerone day

Middle cerebral artery pulsatility index

Lateral sulcus depthone day

Lateral sulcus depth (mm) measured with MRI

Corpus callosumone day

Corpus callosum (mm) measured with MRI

Angiogenic PLGF (placental growth factor)Two days

Placental growth factor in maternal serum

Cerebral cingulata sulcusone day

Cingulata sulcus depth (mm) measured with MRI

Angiogenic s-FLt (soluble fms-like tyrosine kinase)Two days

Soluble fms-like tyrosine kinase factor in maternal serum

Trial Locations

Locations (1)

Hospital Universitari Vall d'Hebrón

🇪🇸

Barcelona, Spain

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