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Hematopoietic Stem Cells Transplantation in Children With Combined Immunodeficiency (CID)

Phase 2
Terminated
Conditions
Combined Immunodeficiencies
Interventions
Biological: Depletion in CD45RA graft donor
Registration Number
NCT02737384
Lead Sponsor
Assistance Publique - Hôpitaux de Paris
Brief Summary

The purpose of this study is to evaluate selective depletion of naïve CD45RA+ T cells from allogenic peripheral blood stem cell graft in children transplanted for combined immune deficiency. The aims of this procedure are to prevent graft versus host disease (GVHD) while preserving anti-infectious response from donor memory T lymphocytes.

Detailed Description

Combined immunodeficiencies (CIDs) are an heterogeneous group of primitive immunodeficiency (PID), which affect T cells development, function or both. These inherited conditions can only be cured by allogeneic hematopoietic stem cell transplantation (HSCT). These procedures have a high risk of morbidity and mortality such a graft versus host disease (GVHD), rejection of the graft and serious infections, especially in this population of children with PID. GVHD is more frequent and severe if the donor is not an identical sibling and/or presents an HLA-mismatch. GVHD requires high immunosuppression as prevention and treatment, and therefore impedes immunity against infections.

In vitro and animal models suggest that GVHD is mediated by naïve T cells. The aim of this study is to decrease the rate and severity of GVHD after selective depletion of naïve CD45RA+ T cells from allogeneic hematopoietic stem cell grafts in patients with CIDs with high risk of severe GVHD, and to preserve immunity against pathogens in a population with high vulnerability to infections.

The project aims is, first, to show improvement of rejection-free and GVH-free survival 12 months post-transplant, and secondly, to show the decrease of viral infection, and assess immune reconstitution kinetic and quality and specific antiviral responses, after a engraftment with naïve cell depleted allograft.

Recruitment & Eligibility

Status
TERMINATED
Sex
All
Target Recruitment
4
Inclusion Criteria
  • Patient from 12 months to 18 years
  • Combined immunodeficiencies with known molecular diagnosis or if unknown, corresponding of p-CID study's definition
  • Hematopoietic stem cell Transplantation planned with one of the following donors :
  • sibling with 1 or 2 HLA antigens mismatch
  • parent 10/10 or 9/10 identical
  • unrelated donor: 10/10 or 9/10 identical
  • Consent form signed by the child's legal guardian
  • Patient using effectiveness contraception during this trial
  • Affiliated or beneficiary of a health insurance regimen
Exclusion Criteria
  • Wiskott-Aldrich syndrome
  • Ongoing pregnancy
  • Positive HIV PCR
  • Contraindication for hematopoetic stem cell transplantation
  • Geno-identical donor in the siblings
  • hematopoetic stem cell transplantation antecedent

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
TreatmentDepletion in CD45RA graft donor-
Primary Outcome Measures
NameTimeMethod
Number of graft rejection12 months after the transplantation
Number of graft versus host disease (GVHD) grade III or IV12 months after the transplantation
Number of death12 months after the transplantation
Secondary Outcome Measures
NameTimeMethod
T Lymphocyte proliferations to phytohemagglutinin (PHA)12 months after the transplantation

to assess immune reconstitution

Need of antiviral treatment12 months after the transplantation

to assess viral infection

Proportion of T CD4 and CD8 lymphocytes specific of cytomegalovirus, Epstein Barr virus and adenovirus12 months after the transplantation

to assess specific antiviral response

Trial Locations

Locations (1)

Hôpital Necker-Enfants Malades

🇫🇷

Paris, France

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