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Clinical Trials/DRKS00011383
DRKS00011383
Recruiting
Not Applicable

Autoimmune-Lymphproliferative Primary Immunodeficiencies: A clinical, immunological and genetic cohort study (AL-PID study, formerly: ALPS study) - AL-PID (formerly: ALPS)

niversitätsklinikum FreiburgCentrum für Chronische Immundefizienz (CCI)0 sites600 target enrollmentDecember 21, 2016

Overview

Phase
Not Applicable
Intervention
Not specified
Conditions
Autoimmune Lymphoproliferative Syndrome other genetically defined or up to now not yet defined primary immunodeficiencies
Sponsor
niversitätsklinikum FreiburgCentrum für Chronische Immundefizienz (CCI)
Enrollment
600
Status
Recruiting
Last Updated
last year

Overview

Brief Summary

No summary available.

Registry
who.int
Start Date
December 21, 2016
End Date
TBD
Last Updated
last year
Study Type
Observational
Sex
All

Investigators

Sponsor
niversitätsklinikum FreiburgCentrum für Chronische Immundefizienz (CCI)

Eligibility Criteria

Inclusion Criteria

  • 1\.Chronic benign lymphoproliferation (i.e. splenomegaly \+/\- lymphadenopathy at 2 sites without infectious or malignant cause)
  • 2\.Autoimmune disease (i.e. AI cytopenia OR inflammatory bowel disease OR CNS inflammatory disease OR interstitial lung disease)
  • one of the two above manifestions
  • 3\.At least one factor indicating a primary immunodeficiency (i.e. infection susceptibility OR additional autoimmune or inflammatory manifestations OR hypogammaglobulinemia OR aberrant immunophenotype OR positive family history OR consanguinity)

Exclusion Criteria

  • No written informed consent of patient or parents (in case of minors) has been obtained

Outcomes

Primary Outcomes

Not specified

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