跳至主要内容
临床试验/DRKS00011383
DRKS00011383招募中不适用

Autoimmune-Lymphproliferative Primary Immunodeficiencies: A clinical, immunological and genetic cohort study (AL-PID study, formerly: ALPS study) - AL-PID (formerly: ALPS)

niversitätsklinikum FreiburgCentrum für Chronische Immundefizienz (CCI)0 个研究点目标入组 600 人开始时间: 2016年12月21日最近更新:
适应症

试验速览

阶段
不适用
状态
招募中
发起方
入组人数
600

研究概览

简要总结

暂无简介。

研究设计

研究类型
Observational

入排标准

年龄范围
1 Years 至 18 Years(—)
性别
All

入选标准

  • 1.Chronic benign lymphoproliferation (i.e. splenomegaly +/- lymphadenopathy at 2 sites without infectious or malignant cause)
  • 2.Autoimmune disease (i.e. AI cytopenia OR inflammatory bowel disease OR CNS inflammatory disease OR interstitial lung disease)
  • one of the two above manifestions
  • 3.At least one factor indicating a primary immunodeficiency (i.e. infection susceptibility OR additional autoimmune or inflammatory manifestations OR hypogammaglobulinemia OR aberrant immunophenotype OR positive family history OR consanguinity)

排除标准

  • No written informed consent of patient or parents (in case of minors) has been obtained

研究者

发起方
niversitätsklinikum FreiburgCentrum für Chronische Immundefizienz (CCI)

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