MedPath

A Study to Test Whether BI 655130 (Spesolimab) Prevents Flare-ups in Patients With Generalized Pustular Psoriasis

Phase 2
Completed
Conditions
Generalized Pustular Psoriasis
Interventions
Drug: Placebo
Registration Number
NCT04399837
Lead Sponsor
Boehringer Ingelheim
Brief Summary

This is a study in adolescents and adults with Generalized Pustular Psoriasis (GPP). People between 12 and 75 years old can take part in the study. The study is open to people who had GPP flare-ups in the past but whose skin is clear or almost clear when they join the study. The purpose of the study is to test 3 different doses of a medicine called spesolimab and to see whether it helps to prevent GPP flare-ups.

Participants are put into 4 groups by chance. Three groups get different doses of spesolimab. The fourth group gets a placebo. Placebo looks like spesolimab but does not contain any medicine.

Spesolimab and placebo are given as an injection under the skin. Participants are in the study for about 1 year and 4 months. During this time, they visit the study site about 15 times. For the first 11 months, participants get spesolimab or placebo injections every month. At the study visits, the doctors check participants' skin for signs of a new GPP flare-up. The doctors also check the general health of the participants.

If a participant has a GPP flare-up during the study, more visits may be necessary. In case of a flare-up, participants get a dose of spesolimab as an infusion into a vein.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
123
Inclusion Criteria
  • Patients with a known and documented history of GPP per ERASPEN criteria (see Section 3.3.1) regardless of IL36RN mutation status, with at least 2 presentations of moderate to severe GPP flares with fresh pustulation (new appearance or worsening) in the past.
  • Patients with a GPPGA score of 0 or 1 at screening and randomization.
  • Patients who are not on concomitant GPP treatment at time of randomization (V2) must have had at least two presentations of moderate to severe GPP flare in the past year, at least one of which had evidence of either fever and/or elevated CRP and/or elevated WBC, and/or asthenia and/or myalgia.
  • Patients who are not on concomitant GPP treatment at time of randomization (V2) but who were on concomitant GPP treatment until shortly before randomization (V2) (≤ 12 weeks before randomization), these patients must have a history of flaring while on concomitant treatment for GPP or in case of dose reduction or discontinuation of their concomitant medication.
  • Patients who are on concomitant treatment regimen with retinoids and/or methotrexate and/or cyclosporine must stop at the day of randomization (V2). These patients must have a history of flaring while on concomitant treatment for GPP or in case of dose reduction or discontinuation of these concomitant medications.
  • Male or female patients, aged 12 to 75 years at screening. For all patients, a minimum weight of 40 kg is required.
  • Signed and dated written informed consent and assent in accordance with ICH-GCP and local legislation prior to admission in the trial.
  • Women of childbearing potential (WOCBP)1 must be ready and able to use highly effective methods of birth control per ICH M3 (R2) that result in a low failure rate of less than 1% per year when used consistently and correctly. A list of contraception methods meeting these criteria is provided in the CTP as well as in the patient, parent(s) (or patient's legal guardian) information.
Exclusion Criteria
  1. Patients with SAPHO (Synovitis-acne-pustulosis-hyperostosis-osteitis) syndrome.

  2. Patients with primary erythrodermic psoriasis vulgaris.

  3. Severe, progressive, or uncontrolled hepatic disease, defined as >3-fold Upper Limit of Normal (ULN) elevation in Aspartate Aminotransferase (AST) or Alanine Aminotransferase (ALT) or alkaline phosphatase, or >2-fold ULN elevation in total bilirubin.

  4. Treatment with:

    1. Any restricted medication as specified in the CTP, or any drug considered likely to interfere with the safe conduct of the study, as assessed by the investigator.
    2. Any prior exposure to BI 655130 or another IL36R inhibitor biologic.
  5. Increased risk of infectious complications (e.g. recent pyogenic infection, any congenital or acquired immunodeficiency (e.g. HIV), past organ or stem cell transplantation), as assessed by the investigator.

  6. Relevant chronic or acute infections including active tuberculosis, human immunodeficiency virus (HIV) infection or viral hepatitis at the time of randomization. A patient can be re-screened if the patient was treated and is cured from the acute infection.

  7. Active or Latent Tuberculosis (TB):

    • Patients with active tuberculosis should be excluded
    • Patients with a positive QuantiFERON® (or if applicable, T-Spot®) TB test during screening are excluded, unless the patient had previous diagnosis of active or latent TB and has completed appropriate treatment per the discretion of the local investigator within the last 3 years and at the latest at the time of screening (i.e. 2 to 4 weeks before study drug administration); patients may be re-screened once to meet this criterion)
    • Patients with suspected false positive or indeterminate QuantiFERON® (or if applicable, T-Spot®) TB result may be re-tested once
    • If QuantiFERON® (or if applicable, T-Spot®) TB testing is not available or provides indeterminate results after repeat testing, a tuberculin skin test (TST) can be performed: A TST reaction of ≥10mm (≥5mm if receiving ≥15mg/d prednisone or its equivalent) is considered positive.
  8. History of allergy/hypersensitivity to the systemically administered trial medication agent or its excipients.

Further exclusion criteria apply.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
PlaceboPlacebo-
Spesolimab SC low doseSpesolimab-
Spesolimab SC medium doseSpesolimab-
Spesolimab SC high doseSpesolimab-
Primary Outcome Measures
NameTimeMethod
Time to First Generalized Pustular Psoriasis (GPP) FlareGPPGA was regularly assessed at baseline (Week 1) and up to Week 48 (at Week 4, 8, 12, 16, 20, 24, 28, 32, 36, 40, 44, 48). Patients could come to site for flare confirmation anytime as unscheduled visit. Visit window was ±7 days.

A GPP flare was defined as increase in Generalized Pustular Psoriasis Physician Global Assessment (GPPGA) score by ≥ 2 from baseline and the pustular component of GPPGA ≥ 2) up to week 48. Use of rescue medication, or investigator-prescribed Standard of Care (SoC) for GPP worsening, was considered to represent a GPP flare onset.

GPPGA relied on clinical assessment of the Generalized Pustular Psoriasis (GPP) patient's skin presentation. The GPPGA total score was calculated by taking the mean of the erythema subscore, pustules subscore and scaling/crusting subscore. The severity of each subscore was assessed using a 5 point scale score ranging from 0 to 4 (0=clear, 1=almost clear, 2=mild, 3=moderate, 4=severe). The final GPPGA score is assigned as follows:

* 0 , if scores for all three subscores are 0,

* 1, if 0 \< mean \< 1.5,

* 2, if 1.5 ≤ mean \< 2.5,

* 3, if 2.5 ≤ mean \< 3.5,

* 4, if mean ≥ 3.5.

Secondary Outcome Measures
NameTimeMethod
Sustained RemissionGPPGA was regularly assessed at baseline (Week 1) and up to Week 48 (at Week 4, 8, 12, 16, 20, 24, 28, 32, 36, 40, 44, 48). Patients could come to site for flare confirmation anytime as unscheduled visit. Visit window was ±7 days.

Proportion of patients with sustained remission at all visits up to Week 48. Proportions were rounded up to three decimal places.

Remission was defined as a patient with a GPPGA score of 0 or 1 (clear or almost clear) at all visits up to week 48, without intake of rescue medication, or investigator-prescribed SoC for GPP worsening.

GPPGA relied on clinical assessment of the Generalized Pustular Psoriasis (GPP) patient's skin presentation. The GPPGA total score was calculated by taking the mean of the erythema subscore, pustules subscore and scaling/crusting subscore. The severity of each subscore was assessed using a 5 point scale score ranging from 0 to 4 (0=clear, 1=almost clear, 2=mild, 3=moderate, 4=severe). The final GPPGA score is assigned as follows:

* 0 , if scores for all three subscores are 0,

* 1, if 0 \< mean \< 1.5,

* 2, if 1.5 ≤ mean \< 2.5,

* 3, if 2.5 ≤ mean \< 3.5,

* 4, if mean ≥ 3.5.

Time to First Worsening of Psoriasis Symptom Scale (PSS) up to Week 48PSS assessments were performed at: Baseline (Week 1) and up to Week 48 (at Week 4, 8, 12, 16, 20, 24, 28, 32, 36, 40, 44, 48). Visit window was ±7 days.

Worsening of Psoriasis Symptom Scale (PSS) was defined as a 4-point increase in total score from baseline. Intake of rescue medication, or investigator-prescribed SoC for GPP worsening, was considered as onset of a worsening.

The PSS is a 4-item patient-reported outcome (PRO) instrument that was developed to assess the severity of 4 psoriasis symptoms in patients with moderate to severe psoriasis.

The symptoms included are: pain, redness, itching, and burning. Current symptom severity is assessed using a 5-point scale ranging from 0 (none) to 4 (very severe). The symptom scores are added to an unweighted total score (range: 0 (no symptoms) to 16 (severe symptoms)).

Time to First Worsening of Dermatology Quality of Life Index (DLQI) up to Week 48DLQI assessments were performed at: Baseline (Week 1) and up to Week 48 (at Week 4, 8, 12, 24, 36 and 48). Visit window was ±7 days. Time window for Week 48 was from Week 46 to Week 50.

Worsening of DLQI up to week 48 was defined as a 4-point increase in total score from baseline. Intake of rescue medication, or investigator-prescribed SoC for GPP worsening, was considered as onset of a worsening.

The DLQI is a patient-administered, ten-question, quality of life questionnaire that covers six domains including symptoms and feelings, daily activities, leisure, work and school, personal relationships and treatment. Response categories include "not relevant" (score of 0), "not at all" (score of 0), "a little" (score of 1), "a lot" (score of 2) and "very much" (score of 3). Question 7 is a "yes"/ "no" question where "yes" is scored as 3. DLQI total score is calculated by summing the scores of each question resulting in a range of 0 (no effect on patient's life) to 30 (extremely large effect on patient's life).

Key Secondary Endpoint: The Occurrence of at Least One Generalized Pustular Psoriasis (GPP) Flare up to Week 48GPPGA was regularly assessed at baseline (Week 1) and up to Week 48 (at Week 4, 8, 12, 16, 20, 24, 28, 32, 36, 40, 44, 48). Patients could come to site for flare confirmation anytime as unscheduled visit. Visit window was ±7 days.

Proportion of patients with at least one GPP flare up to Week 48 is reported. Proportions were rounded up to three decimal places.

A GPP flare was defined as increase in Generalized Pustular Psoriasis Physician Global Assessment (GPPGA) score by ≥ 2 from baseline and the pustular component of GPPGA ≥ 2. Any use of rescue medication, or investigator-prescribed SoC for GPP worsening, prior to week 48 was considered to represent the onset of a GPP flare.

Generalized Pustular Psoriasis Physician Global Assessment (GPPGA) relied on the clinical assessment of GPP patient's skin presentation. The total score is calculated by taking the mean of the three subscores: 1) erythema; 2) pustules and 3) scaling/crusting which were assessed using a scale score 0 to 4 (0=clear, 1=almost clear, 2=mild, 3=moderate, 4=severe). The final GPPGA score:

0 , if scores for all three subscores are 0,

1. if 0 \< mean \< 1.5;

2. if 1.5 ≤ mean \< 2.5;

3. if 2.5 ≤ mean \< 3.5;

4. if mean ≥ 3.5.

The Occurrence of Treatment Emergent Adverse Events (TEAEs)Up to 62 weeks (for detailed timeframe see description).

Percentage of patients with treatment emergent adverse events (TEAEs) is reported. Percentages were rounded up to one decimal places.

Time Frame: Placebo, Spesolimab (Speso) SC low, medium, high: From randomized study treatment start until the first use of rescue medication with IV spesolimab or until last dose + 16 weeks, up to 62 weeks.

Speso IV SD and Speso IV DD: From first use of rescue medication with IV spesolimab until OL maintenance spesolimab SC or until last dose of spesolimab IV + 16 weeks, up to 17 weeks.

Speso OL SC: From the first dose of OL spesolimab SC treatment until last dose + 16 weeks, up to 62 weeks.

Trial Locations

Locations (72)

Universitätsklinikum Bonn AöR

🇩🇪

Bonn, Germany

Washington University School of Medicine

🇺🇸

Saint Louis, Missouri, United States

Klinikum Oldenburg AöR

🇩🇪

Oldenburg, Germany

Istituto Clinico Humanitas

🇮🇹

Rozzano (MI), Italy

Universitätsklinikum Münster

🇩🇪

Münster, Germany

Universitätsklinikum Würzburg AÖR

🇩🇪

Würzburg, Germany

HOP l'Archet

🇫🇷

Nice, France

Universitätsklinikum Frankfurt

🇩🇪

Frankfurt am Main, Germany

Pusan National Univ. Hosp

🇰🇷

Busan, Korea, Republic of

Hospital Kuala Lumpur

🇲🇾

Kuala Lumpur, Malaysia

Hospital Universitario 12 de Octubre

🇪🇸

Madrid, Spain

Centro de Investigación de Enfermedades Autoinmunes S.C.

🇲🇽

Guadalajara, Mexico

Severance Hospital

🇰🇷

Seoul, Korea, Republic of

HOP Saint-Louis

🇫🇷

Paris, France

Fachklinik Bad Bentheim

🇩🇪

Bad Bentheim, Germany

Hospital Italiano de Buenos Aires

🇦🇷

Caba, Argentina

Klinikum der Universität München - Campus Innenstadt

🇩🇪

München, Germany

Hospital Sultanah Aminah

🇲🇾

Johor Bahru, Malaysia

Marmara Universitesi Tip Fakultesi

🇹🇷

Istanbul, Turkey

Hospital Pulau Pinang

🇲🇾

Pulau Pinang, Malaysia

Uludag University Medicine Faculty Departmant of Dermatology

🇹🇷

Bursa, Turkey

Hospital Universitario Dr Jose Eleuterio Gonzalez

🇲🇽

Monterrey, Mexico

Bezmi Alem Valide Sultan Vakif Gureba Egitim ve Arastirma Hastanesi

🇹🇷

Istanbul, Turkey

Hospital Sant Joan de Déu

🇪🇸

Esplugues Del Llobregat, Spain

Arthritis Clinical Research Trials

🇿🇦

Cape Town, South Africa

Charles Nicolle Hospital

🇹🇳

Tunis, Tunisia

Habib Thameur Hospital

🇹🇳

Tunis, Tunisia

National Hospital of Dermatology and Venereology

🇻🇳

Ha Noi, Vietnam

Shanghai Skin Disease Hospital

🇨🇳

Shanghai, China

Sun yet-sen Memorial Hospital, Sun yet-sen Univesity

🇨🇳

Guangzhou, China

The Second Affiliated Hospital Zhejiang University School of Medicine

🇨🇳

Hangzhou, China

Tianjin Academy of Traditional Chinese Medicine Affiliated Hospital

🇨🇳

Tianjin, China

Second Affiliated Hospital of Xi'an JiaoTong University

🇨🇳

Xi'an, China

Oakland Hills Dermatology

🇺🇸

Auburn Hills, Michigan, United States

Buenos Aires Skin S.A.

🇦🇷

Caba, Argentina

Huashan Hospital, Fudan University

🇨🇳

Shanghai, China

The First Hospital of China Medical University

🇨🇳

Shenyang, China

Saratov State Med.Univ.n.a.Razumovskogo

🇷🇺

Saratov, Russian Federation

Chang Gung Medical Foundation (CGMF) - Linkou Bran

🇨🇳

Linkou, Taiwan

La Rabta Hospital

🇹🇳

Tunis, Tunisia

Istanbul Universitesi Cerrahpasa Tip Fakultesi

🇹🇷

Istanbul, Turkey

Farhat Hached Hospital

🇹🇳

Sousse, Tunisia

HCMC Hospital of Dermato-Venereology

🇻🇳

Ho Chi Minh, Vietnam

Hospital Sultan Ismail

🇲🇾

Johor Bahru, Malaysia

General Hospital of Thessaloniki "Ippokrateio"

🇬🇷

Thessaloniki, Greece

Hospital Raja Permaisuri Bainun

🇲🇾

Ipoh, Malaysia

FSBEI HE "Kirov State Medical University"

🇷🇺

Kirov, Russian Federation

National Taiwan University Hospital

🇨🇳

Taipei, Taiwan

Hospital Pakar Sultanah Fatimah

🇲🇾

Muar, Malaysia

Hedi Chaker Hospital, Department of Dermatology

🇹🇳

Sfax, Tunisia

Clínica Dermacross S.A.

🇨🇱

Vitacura, Chile

Nagoya City University Hospital

🇯🇵

Aichi, Nagoya, Japan

Kyushu Rosai Hospital

🇯🇵

Fukuoka, Kitakyushu, Japan

Saitama Medical University Hospital

🇯🇵

Saitama, Iruma-gun, Japan

Erasmus Medisch Centrum

🇳🇱

Rotterdam, Netherlands

Southern Philippines Medical Center

🇵🇭

Davao City, Philippines

Center for Skin Research, Testing and Product Development

🇵🇭

Makati City, Philippines

SBHI Chelyabinsk Reg.Clin.Derma.Dispen.

🇷🇺

Chelyabinsk, Russian Federation

LLC "Medical Center Azbuka Zdorovia"

🇷🇺

Kazan, Russian Federation

King Chulalongkorn Memorial Hospital

🇹🇭

Bangkok, Thailand

Tokyo Medical University Ibaraki Medical Center

🇯🇵

Ibaraki, Inashiki-gun, Japan

Brussels - UNIV Saint-Luc

🇧🇪

Bruxelles, Belgium

Tokyo Medical University Hachioji Medical Center

🇯🇵

Tokyo, Hachioji, Japan

Tokyo Medical University Hospital

🇯🇵

Tokyo, Shinjuku-ku, Japan

Sarawak General Hospital

🇲🇾

Kuching, Sarawak, Malaysia

Iloilo Doctors Hospital

🇵🇭

Iloilo City, Iloilo, Philippines

1stPavlov St.Med.Univ.St.-Petersburg Res.Inst.

🇷🇺

Saint-Petersburg, Russian Federation

Queen Elizabeth Hospital

🇲🇾

Kota Kinabalu, Malaysia

LLC Skin Disease Clinic of Pier Volkenstein, St. Petersburg

🇷🇺

St. Petersburg, Russian Federation

LLC "Avrora Medfort"

🇷🇺

St. Petersburg, Russian Federation

Institute of Dermatology

🇹🇭

Bangkok, Thailand

Ramathibodi Hospital

🇹🇭

Ratchatewi, Bangkok, Thailand

© Copyright 2025. All Rights Reserved by MedPath