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RCT of Steroids Following Kasai Portoenterostomy for Biliary Atresia.

Phase 3
Conditions
Biliary Atresia
Interventions
Drug: placebo
Registration Number
NCT00539565
Lead Sponsor
King's College Hospital NHS Trust
Brief Summary

Biliary atresia is a congenital disorder of bile duct development or destruction of established but immature bile ducts. The study tests the hypothesis that post-operative steroids improve outcome following the Kasai procedure - the commonest surgical treatment.

Detailed Description

Biliary atresia is a potentially fatal condition of infants presenting as persisting jaundice in the first few weeks of life. The disease is characterised by obstruction and damage to the intra and extrahepatic parts of the biliary tree. Within the liver there is also a pronounced inflammatory response. The initial treatment is an attempt, by surgery, to restore bile flow by excising the obliterated extrahepatic bile ducts and joining part of the intestine to the bile "root" of the liver (the porta hepatis). This is known as the Kasai procedure. This is successful in \~50% of cases in reducing the level of jaundice to near-normal values. The use of steroids post-operatively has been suggested as improving outcome by diminishing the inflammatory response.

Recruitment & Eligibility

Status
UNKNOWN
Sex
All
Target Recruitment
100
Inclusion Criteria
  • biliary atresia
Exclusion Criteria
  • <100 days at portoenterostomy
  • no other anomalies (e.g. Biliary Atresia Splenic Malformation syndrome)
  • anu contra-indications to corticosteroids

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Aprednisoloneoral corticosteroids
Bplaceboas for active regimen
Primary Outcome Measures
NameTimeMethod
clearance of jaundice (<20 umol/L)1 year
Proportion transplanted or died1 year
Secondary Outcome Measures
NameTimeMethod
biochemical indices of liver function1 year

Trial Locations

Locations (1)

Kings College Hospital

🇬🇧

London, United Kingdom

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