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An Extension Study to Assess Long-Term Safety of Eplontersen in Adults With Transthyretin-Mediated Amyloid Cardiomyopathy (ATTR-CM)

Phase 3
Conditions
Transthyretin-Mediated Amyloid Cardiomyopathy (ATTR CM)
Interventions
Registration Number
NCT05667493
Lead Sponsor
Ionis Pharmaceuticals, Inc.
Brief Summary

The purpose of this study is to evaluate the safety and tolerability of extended dosing with eplontersen in participants with ATTR-CM.

Detailed Description

This is a multicenter, open-label extension, Phase 3 study in up to approximately 1400 participants from the 682884-CS2 study. Eligible participants will receive eplontersen once every 4 weeks for up to 36 months or until after eplontersen is approved and available in the site's country, whichever occurs first. Participants will also receive daily supplemental doses of the recommended daily allowance (RDA) of vitamin A.

Recruitment & Eligibility

Status
ENROLLING_BY_INVITATION
Sex
All
Target Recruitment
1400
Inclusion Criteria
  1. Satisfactory completion of Treatment Period and the End of Treatment Visit of the Index Study (ION-682884-CS2) OR diagnosis of ATTR-CM and satisfactory participation on ISIS 420915- CS101 study as judged by the Investigator and Sponsor.
  2. Investigator is willing to treat the participant with open-label eplontersen.
  3. Willingness to adhere to vitamin A supplementation per protocol.
Exclusion Criteria
  1. Permanently discontinued study drug administration while participating in the Index Study (ION 682884-CS2) or IST (ISIS 420915-CS101 Study).
  2. Have any new condition or worsening of an existing condition that in the opinion of the Investigator or Sponsor would make the participant unsuitable for enrolment, or which could interfere with the participant participating in or completing the study, including the need for treatment with medications disallowed in the Index Study.

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
EplontersenEplontersenEplontersen will be administered once every month by sub-cutaneous (SC) injection for up to 36 months or 6 months after eplontersen is approved and available in the site's country, whichever occurs first.
Primary Outcome Measures
NameTimeMethod
Number of Participants With Adverse Events (AE) and Serious Adverse Events (SAE)Baseline up to 36 months
Change From Baseline in Platelet CountBaseline up to 36 months
Change From Baseline in Estimated Glomerular Filtration Rate (eGFR)Baseline up to 36 months
Change From Baseline in Urine Protein Creatinine Ratio (UPCR)Baseline up to 36 months
Secondary Outcome Measures
NameTimeMethod
Change From Baseline in 6-minute Walk Test (6MWT)Baseline up to 36 months
Change From Baseline in Transthyretin (TTR) Serum LevelsBaseline up to 36 months
Change From Baseline in Kansas City Cardiomyopathy Questionnaire (KCCQ)Baseline up to 36 months

Trial Locations

Locations (96)

Mayo Clinic

🇺🇸

Rochester, Minnesota, United States

Cedars-Sinai Medical Center

🇺🇸

Beverly Hills, California, United States

Altman Clinical and Translational Research Institute - Center for Clinical Research

🇺🇸

La Jolla, California, United States

Stanford University (Leland Stanford Junior University)

🇺🇸

Stanford, California, United States

University of Colorado Hospital - Anschutz Medical Campus

🇺🇸

Aurora, Colorado, United States

MedStar Washington Hospital Center

🇺🇸

Washington, District of Columbia, United States

The George Washington Medical Faculty Associates - Foggy Bottom North Pavilion

🇺🇸

Washington, District of Columbia, United States

Cleveland Clinic Florida

🇺🇸

Weston, Florida, United States

Piedmont Heart of Fayetteville

🇺🇸

Atlanta, Georgia, United States

Emory Heart and Vascular Center - Emory Clifton Campus

🇺🇸

Atlanta, Georgia, United States

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Mayo Clinic
🇺🇸Rochester, Minnesota, United States
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