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A comparative trial studying the molecular action of vitamin D and retinoids (acitretin) in children with autosomal recessive congenital ichthyosis

Phase 2
Conditions
Health Condition 1: null- autosomal recessive congenital ichthyosis with vitamin D Deficiency
Registration Number
CTRI/2017/08/009565
Lead Sponsor
Department of Science Technology
Brief Summary

Not available

Detailed Description

Not available

Recruitment & Eligibility

Status
ot Yet Recruiting
Sex
Not specified
Target Recruitment
20
Inclusion Criteria

1.All patients of autosomal recessive congenital ichthyosis belonging to either lamellar or congenital ichthyosiform erythroderma phenotypes.

Lamellar Ichthyosis:

a. Children with large parchment like scales all over the body

b. Scales are larger, severely thicker and brownish that might fracture resulting in tessellated or tile like pattern.

c. Hyperkeratotic and more verrucous scaling around the joints

d. Erythroderma

e. Severe ectropion

Congenital Ichthyosiform erythroderma

f. Prominent erythroderma

g. Scaling is present all over the body, less severe than seen in lamellar phenotype.

h. Scales are lighter and thinner

2.Serum 25 (OH) D levels < 20 ng/mL with or without rickets

3.Age > 6 months

Exclusion Criteria

1.Other variants of congenital Ichthyosis (Ichthyosis vulgaris, X linked recessive ichthyosis, epidermolytic ichthyosis)

2.Children with liver and kidney impairment or any other systemic illness.

Study & Design

Study Type
Interventional
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Secondary Outcome Measures
NameTimeMethod
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