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Exploratory Study of Danicamtiv in Patients With Primary Dilated Cardiomyopathy (DCM) Due to Genetic Variants or Other Causalities

Phase 2
Terminated
Conditions
Primary Familial Dilated Cardiomyopathy
Interventions
Registration Number
NCT04572893
Lead Sponsor
Bristol-Myers Squibb
Brief Summary

The purpose of this Phase 2a study is to establish safety and preliminary efficacy of treatment with danicamtiv in patients with primary dilated cardiomyopathy (DCM) due to MYH7 or TTN variants or other causalities.

Detailed Description

Not available

Recruitment & Eligibility

Status
TERMINATED
Sex
All
Target Recruitment
41
Inclusion Criteria
  • For MYH7 and TTN cohorts, must have diagnosis of primary DCM (dilated cardiomyopathy), clinically stable and due to probably disease-causing variant of MYH7 or TTN
  • Has adequate acoustic windows for echocardiography
  • Maximum of 3 family members with same variant can be enrolled
  • For the cohort of primary DCM due to causalities other than MYH7 and TTN, participant must have diagnosis of primary DCM with a cause not related to MYH7 or TTN variants
Exclusion Criteria
  • Significant structural cardiac abnormalities including valvar dysfunction on Screening transthoracic echo(s)
  • Routinely scheduled outpatient intravenous (IV) infusions for heart failure (e.g., inotropes, afterload reduction, or diuretics)
  • Presence of protocol specified laboratory abnormalities at Screening
  • Recent acute coronary syndrome or angina pectoris (<90 days)
  • Recent hospitalization for heart failure (<90 days)

Study & Design

Study Type
INTERVENTIONAL
Study Design
SEQUENTIAL
Arm && Interventions
GroupInterventionDescription
MYK-491danicamtivPrimary DCM due to MYH7 or TTN Variant or due to other causalities not related to MYH7 or TTN variants
Primary Outcome Measures
NameTimeMethod
Number of Participants With Clinically Significant Changes in 12-Lead ECG Recordings in Part AFrom first dose to 30 days post last dose (Up to approximately 15 weeks)

Number of participants with clinically significant changes in 12-lead ECG recordings.

Number of Participants With Adverse Events (AEs) in Part AFrom first dose to 30 days post last dose (Up to approximately 15 weeks)

An AE is defined as any new untoward medical occurrence or worsening of a preexisting medical condition in a clinical investigation participant administered study drug and that does not necessarily have a causal relationship with this treatment.

Number of Participants With Serious Adverse Events (SAEs) in Part AFrom first dose to 30 days post last dose (Up to approximately 15 weeks)

An SAE is defined as any untoward medical occurrence that, at any dose: results in death, is life-threatening, requires inpatient hospitalization or causes prolongation of existing hospitalization, results in persistent or significant disability or permanent damage, is a congenital anomaly/birth defect, is an important medical event.

Number of Participants With Safety Laboratory Assessments by Intensity in Part AFrom first dose to 14 days post last dose (Up to approximately 13 weeks)

Number of participants with safety laboratory assessments by intensity. Mild=An event that is easily tolerated by the participant, causing minimal discomfort and not interfering with everyday activities; Moderate= An event causing sufficient discomfort and interferes with normal everyday activities.

Number of Participants With Clinically Significant Changes in Physical Examinations in Part AFrom first dose to 30 days post last dose (Up to approximately 15 weeks)

Number of participants with clinically significant changes in physical examinations.

Number of Participants With Clinically Significant Changes in Vital Signs in Part AFrom first dose to 30 days post last dose (Up to approximately 15 weeks)

Number of participants with clinically significant changes in vital signs.

Number of Participants With Treatment Emergent Adverse Events (TEAEs) by Intensity in Part AFrom first dose to 14 days post last dose (Up to approximately 13 weeks)

An AE is defined as any new untoward medical occurrence or worsening of a preexisting medical condition in a clinical investigation participant administered study drug and that does not necessarily have a causal relationship with this treatment.

Mild=An event that is easily tolerated by the participant, causing minimal discomfort and not interfering with everyday activities; Moderate= An event causing sufficient discomfort and interferes with normal everyday activities.

Severe= An event preventing normal everyday activities. (An AE that is assessed as severe should not be confused with a SAE. Severe is a category utilized for rating the intensity of an event; and both AEs and SAEs can be assessed as severe.)

Secondary Outcome Measures
NameTimeMethod
Transthoracic Echo (TTE) Left Ventricular Ejection Time (LVET) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Ventricular Stroke Volume (LVSV) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Ventricular Ejection Fraction (LVEF) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 42, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Ventricular Global Longitudinal Strain (LVGLS) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 42, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Ventricular Global Circumferential Strain (LVGCS) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 42, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) S Prime Lateral Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) S Prime Septal Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) Left Ventricular End-Systolic Diameter (LVESD) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) Left Ventricular End-Systolic Volumen Index (LVESVi) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 42, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) Left Ventricular End-Diastolic Diameter (LVEDD) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) Left Ventricular End-Diastolic Volumen Index (LVEDVi) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 42, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) E Prime Lateral Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Tissue Doppler Imaging (TDI) E Prime Septal Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) E/E Prime Average Ratio Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) E/E Prime Lateral Ratio Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) E/E Prime Septal Ratio Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Ratio of Peak Inflow Velocities in Early and Late Diastole - E/A Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Atrial Minimum Volume (LAminV) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Atrial Maximum Volume Index (LAmaxVi) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Atrial Emptying Fraction (LAEF) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days.

Transthoracic Echo (TTE) Left Atrial Function Index (LAFI) Change From BaselinePart A: Baseline, end of treatment period 1. end of treatment period 2, early termination; Part B: Baseline, weeks 2, 6, 12, 24, 36, 48, and early termination

Baseline is defined as the last non-missing result prior to the first dose of study medication. for part B, baseline is defined as visit 1B regardless of rescreening. Treatment periods 1 and 2 are 5 to 8 days. Higher LAFI values are considered better left atrial function while lower LFAI values may indicate left atrial dysfunction.

Trial Locations

Locations (19)

Local Institution - 0007

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La Jolla, California, United States

Local Institution - 0010

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Washington, District of Columbia, United States

Local Institution - 0009

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Tampa, Florida, United States

Local Institution - 0002

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Chicago, Illinois, United States

Local Institution - 0003

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Boston, Massachusetts, United States

Local Institution - 0005

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Rochester, Minnesota, United States

Local Institution - 0006

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Cleveland, Ohio, United States

Local Institution - 0019

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Columbus, Ohio, United States

Local Institution - 0001

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Philadelphia, Pennsylvania, United States

Local Institution - 0004

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Charleston, South Carolina, United States

Local Institution - 0008

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Germantown, Tennessee, United States

Local Institution - 0018

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Austin, Texas, United States

Local Institution - 0014

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Heidelberg, Baden-Württemberg, Germany

Local Institution - 0015

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Wuerzburg, Germany

Local Institution - 0012

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A Coruña, Spain

Local Institution - 0011

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El Palmar, Spain

Local Institution - 0013

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Majadahonda, Spain

Local Institution - 0016

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London, United Kingdom

Local Institution - 0017

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Middlesex, United Kingdom

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