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Assessment of Cystic Fibrosis Lung Involvement With UTE Pulse Sequences

Not Applicable
Completed
Conditions
Cystic Fibrosis
Interventions
Device: MR measurements of lung morphological changes in cystic fibrosis (Avanto dot, Siemens)
Device: CT measurements of lung morphological changes in cystic fibrosis
Registration Number
NCT02449785
Lead Sponsor
University Hospital, Bordeaux
Brief Summary

Non-invasive assessment of lung involvement is a crucial issue for the follow-up of cystic fibrosis patients. Currently, CT is the method of reference to evaluate and quantify the lung morphological changes in cystic fibrosis adults but it remains a radiation-based technique. MRI with ultrashort echo time (UTE) pulse sequences is a promising non-ionizing alternative for lung imaging. The investigators' objective is to evaluate cystic fibrosis lung involvement using CT and MRI-UTE, and to test the agreement between both techniques.

Detailed Description

Cystic fibrosis is a recessive autosomic fatal disease, affecting about 6000 people in France. Thanks to progress in symptomatic care, median survival is increasing. The lung involvement is the most common and responsible for most deaths. The evaluation of respiratory disease severity is based on pulmonary functional tests (PFT) and imaging. Multi-slice computed tomography (CT) is the method of reference to quantify lung involvement in cystic fibrosis. It detects respiratory lung involvement earlier than PFT, and it reveals lesions associated with the onset of respiratory exacerbations, the mortality increase and the reduction of quality of life. However CT provides ionizing radiation, thus limiting the possibility of long-term follow-up. MRI is a non-ionizing 3D imaging technique; nevertheless, lung MRI is technically challenging with the result that it is currently not used in routine practice. Indeed, both low proton density and susceptibility effects lead to very low signal intensity derived from lung parenchyma. Recently, pulse sequences with ultrashort echo time (UTE) have been implemented by the use of half radio-frequency excitations and radial projection reconstruction. These UTE sequences make it theoretically possible to retrieve more signal from the lung parenchyma. The investigators aim at using 3D T1-weighted UTE pulse sequences on a 1.5T magnet (Avanto dot, Siemens) in cystic fibrosis patients in order to assess lung involvement severity. Thirty three cystic fibrosis adults are expected to take part in the study. All will benefit from PFT, CT and MRI. The investigators' strategy is to establish a semi quantitative score of pulmonary severity (Helbich score) using MRI and CT in subjects, testing for correlations between MRI and CT measurements and assessing the reproducibility of lung lesions quantification using MRI. The investigators' objective is to demonstrate that MRI-UTE pulse sequence at 1.5T is accurate and reproducible in evaluating and quantifying pulmonary involvement in cystic fibrosis.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
30
Inclusion Criteria
  • cystic fibrosis adults
  • written informed consent
Exclusion Criteria
  • Subjects without any social security or health insurance
  • Pregnancy
  • MRI contraindications: Magnetically activated implanted devices (cardiac pacemakers, insulin pumps, neurostimulators, cochlear implants), metal inside the eye or the brain (aneurysm clip, ocular foreign body), cardiac valvular prosthesis (Starr-Edwards pre-6000), subject with claustrophobia.

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
Cystic fibrosis adultsMR measurements of lung morphological changes in cystic fibrosis (Avanto dot, Siemens)-
Cystic fibrosis adultsCT measurements of lung morphological changes in cystic fibrosis-
Primary Outcome Measures
NameTimeMethod
Agreement between MRI and CT for scoring lung involvement in cystic fibrosisDuring MRI and CT, Day one

MRI and CT evaluation of lung lesions quantification in cystic fibrosis will be assessed by 2 blind radiologists.

Agreement between both evaluation will be assessed during statistical analyses after study completion.

Secondary Outcome Measures
NameTimeMethod
Correlation between MRI cystic fibrosis scoring and PFT indexesDay one
Evolution of MRI cystic fibrosis scoring after one year12 month after Day one
Cystic fibrosis lesions scoring extracted from CT and MR imagesDuring MRI and CT, Day one

MRI and CT evaluation of lung lesions quantification in cystic fibrosis will be assessed by 2 blind radiologists.

Agreement between both evaluation will be assessed during statistical analyses after study completion.

MRI cystic fibrosis reproductibility scoring over the timeDuring MRI, Day one

MRI cystic fibrosis scoring will be assessed a second time the same blind radiologist

Correlation between MRI cystic fibrosis scoring and exacerbation number12 month after Day one
Correlation between MRI cystic fibrosis scoring and quality of lifeDay one and 12 month after Day one

Trial Locations

Locations (1)

University Hospital Bordeaux

🇫🇷

Pessac, France

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