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A Study to Evaluate Safety, PK and PD of FDL169 in Cystic Fibrosis Subjects

Phase 1
Completed
Conditions
Cystic Fibrosis
Interventions
Drug: Placebo
Registration Number
NCT03093714
Lead Sponsor
Flatley Discovery Lab LLC
Brief Summary

This is a multicenter, randomized, placebo-controlled, dose-escalation study. Enrollment is planned to occur at approximately 14 global sites. Approximately 24 subjects with CF.

Detailed Description

This is a multicenter, randomized double-blind, placebo-controlled dose-escalation and parallel-arm, dose-ranging study. Enrollment is planned to occur at approximately 14 global sites. Approximately 24 subjects with CF who are homozygous for the F508del-CFTR mutation will be enrolled in two cohorts.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
27
Inclusion Criteria
  • Male or female subjects with a confirmed diagnosis of CF defined as a sweat chloride value ≥60 mmol/L by quantitative pilocarpine iontophoresis or two CF-causing mutations,documented in the subject's medical record or confirmed at screening.
  • Age 18 and above on the date of informed consent.
  • Weight ≥40 kg.
  • Homozygous for the F508del-CFTR mutation. Genotyping to be confirmed at screening.
  • Ability to perform a valid, reproducible spirometry test with demonstration of a forced expiratory volume in 1 sec (FEV1) >40% of predicted normal for age, sex and height.
  • Screening laboratory tests with no clinically significant abnormalities that would interfere with the study assessments (as judged by the Investigator).
  • Subjects who are sexually active must agree to follow the study's contraception requirements.
Exclusion Criteria
  • An acute upper or lower respiratory tract infection, pulmonary exacerbation, or changes in therapy for pulmonary disease within 4 weeks prior to Day 1.
  • Major complications of lung disease (including massive hemoptysis, pneumothorax, or pleural effusion) within 8 weeks prior to screening.
  • Impaired renal function or known portal hypertension.
  • History of prolonged QT and/or QTcF (Fridericia's correction) interval (>450 msec) or QTcF >450 msec at Screening.
  • History of solid organ or hematological transplantation.
  • History of alcohol abuse or drug addiction (including cannabis, cocaine and opiates) during the past year, (as judged by the Investigator).
  • Use of ivacaftor or lumacaftor, within 4 weeks of Day 1
  • Any change (initiation, change in type of drug, dose modification, schedule modification, interruption, discontinuation, or re-initiation) in a chronic treatment/prophylaxis regimen for CF or for CF-related conditions within 4 weeks prior to Day 1.
  • Ongoing immunosuppressive therapy (including systemic corticosteroids).
  • Hemoglobin <10 g/dL.
  • Abnormal liver function, at screening.
  • Abnormal renal function at screening.
  • Ongoing participation in another clinical study or prior participation without appropriate washout (minimum of 10 half- lives or 30 days, whichever is longer) prior to Screening visit.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
PlaceboPlaceboMultiple dose placebo as repeat doses in CF subjects
FDL 169 test formulation (Dose Level 1)FDL169Multiple dose (Dose Level 1) FDL 169 test formulation administered as repeat doses in CF subjects
FDL 169 test formulation ( Dose Level 3)FDL169Multiple dose (Dose Level 3) FDL 169 test formulation administered as repeat doses in CF subjects
FDL 169 test formulation (Dose Level 2)FDL169Multiple dose (Dose Level 2) FDL 169 test formulation administered as repeat doses in CF subjects
Primary Outcome Measures
NameTimeMethod
Incidence of Treatment-Emergent Adverse Events28 days

Safety and tolerability of FDL169 as determined by the incidence of adverse events (AEs) and serious adverse events (SAEs).

Secondary Outcome Measures
NameTimeMethod
Pharmacokinetic parameters, Cmax28 days

The pharmacokinetic parameters of FDL169: maximal plasma concentration (Cmax).

Pharmacokinetic parameters, AUC28 days

The pharmacokinetic parameters of FDL169: area under the plasma concentration curve (AUC).

Pharmacokinetic parameters, CL/F28 days

The pharmacokinetic parameters of FDL169: clearance (CL/F).

Pharmacokinetic parameters, Tmax28 days

The pharmacokinetic parameters of FDL169: maximal concentration (Tmax).

Pharmacokinetic parameters, V/F28 days

The pharmacokinetic parameters of FDL169: apparent volume of distribution (V/F).

Trial Locations

Locations (13)

Mater Misericordiae Ltd

🇦🇺

South Brisbane, Queenland, Australia

The Alfred Hospital

🇦🇺

Melbourne, Australia

Charité - Universitätsmedizin Berlin CVK

🇩🇪

Berlin, Germany

FN v Motole, Pediatrická klinika, Centrum cystické fibrózy

🇨🇿

Praha, Czechia

Klinik Donaustauf, Zentrum für Pneumologie

🇩🇪

Donaustauf, Germany

Ruhrlandklinik

🇩🇪

Essen, Germany

Universitätsklinikum Frankfurt

🇩🇪

Frankfurt, Germany

NICRN Respiratory Research Office, Belfast City Hospital

🇬🇧

Belfast, United Kingdom

Research Dept., Liverpool Heart and Chest Hospital

🇬🇧

Liverpool, United Kingdom

The Medicines Evaluation Unit (MEU)

🇬🇧

Manchester, United Kingdom

NIHR Wellcome Trust Clinical Research Facility

🇬🇧

Southampton, United Kingdom

The Prince Charles Hospital

🇦🇺

Chermside, Queensland, Australia

Royal Brompton Hospital

🇬🇧

London, United Kingdom

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