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Ex Vivo Laboratory Assays Application for Therapy Tailoring in Patients With Severe Bleeding Disorders

Conditions
Severe Hemophilia
Registration Number
NCT02324517
Lead Sponsor
Sheba Medical Center
Brief Summary

Therapy of patients with severe hemophilia (including hemophilia with inhibitors) and other severe bleeding disorders could be monitored and guided based upon special clotting assays , eg thrombin generation and thromboelastography. In this study blood sampled from patients with bleeding disorders will be evaluated applying ex- vivo spiking assays with various coagulation concentrates to potentially address the feasibility of replacement /bypass agents/ combined therapy for future bleeding episodes. Patients that will be further treated by any regimen potentially suggested (as standard care- not within trial) will be thereafter followed , including repeated lab studies to assess the impact of therapy upon hemostasis.

Detailed Description

Not available

Recruitment & Eligibility

Status
UNKNOWN
Sex
All
Target Recruitment
300
Inclusion Criteria
  • Informed consent
  • Validated coagulation disorder
Exclusion Criteria
  • Not consenting to participate
  • Multiple coagulopathies and comorbidities

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Thrombin Generation Parameters pre and post therapy / spiking assays1 year from enrollment

Thrombin Generation Parameters (Peak height, ETP) before and after spiking assays with procoagulant drugs will be compared for each patient separately and within each group of patients diagnosed with similar coagulation disorder.

Secondary Outcome Measures
NameTimeMethod

Trial Locations

Locations (1)

Sheba Mediacl Center

🇮🇱

Ramat Gan, Israel

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