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Treatment of Deficient Subclass or Anti-polysaccharide Antibody Response

Phase 4
Completed
Conditions
IgG Deficiency
Infections
Interventions
Drug: intravenous immunoglobulins
Drug: antibiotics
Registration Number
NCT00522821
Lead Sponsor
Prothya Biosolutions
Brief Summary

There is no consensus on the treatment of patients with recurrent infections and isolated immunoglobulin G (IgG)-subclass deficiency and/or selective antipolysaccharide antibody deficiency. Therefore, the Dutch Inter University Working Party will start a study in which the treatment with antibiotics is compared with intravenous immunoglobulin therapy with respect to clinical outcome measures in both children and adults with this disorder.

Detailed Description

There is no consensus on the treatment of patients with recurrent infections and isolated IgG-subclass deficiency and/or selective antipolysaccharide antibody deficiency. At present, there are no robust criteria to predict which patient will or will not respond adequately to antibiotic treatment or to IVIG. Furthermore, it is unknown whether IVIG treatment improves the quality of life in these patients. Therefore, the Dutch InterUniversity Working Party intends to start a study in this patient group. In this study, treatment for a year with antibiotics will be compared with a year intravenous immunoglobulin therapy with respect to clinical outcome measures in both children and adults with this disorder.

The patient will visit the clinic every 3 months during which laboratory tests and physiological measurements will be performed. Moreover the occurrence of infections and fever, the use of antibiotics, hospital admissions, and quality of life will be documented.

The study should result in a national harmonization in the treatment of this patient group. To this end, the results of the study will be used to compile a treatment protocol for this group of patients in the Netherlands and if applicable also in other countries worldwide.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
55
Inclusion Criteria
  • IgG subclass deficiency and/or (selective) antipolysaccharide antibody deficiency
  • At least 2 physician documented infections before the start of the current treatment or in the last 6 months for newly diagnosed patients.
  • Total serum IgG > 4 g/l
  • ≥ 5 years of age
  • Informed consent
Exclusion Criteria
  • Treatment with any other investigational drug within 7 days prior to study entry, or previous enrolment in this study
  • Allergic reactions against human plasma/plasma products, or co-trimoxazole
  • An ongoing progressive terminal disease
  • Pregnancy or lactation
  • History of (transient) cerebrovascular accident or coronary insufficiency
  • Renal insufficiency (plasma creatinin > 115 µmol/L; or creatinin clearance <20 ml/min)
  • An ongoing active disease causing general symptoms e.g. chronic active hepatitis or persistent enterovirus infection with ongoing systemic complaints
  • Detectable anti-IgA antibodies
  • Active systemic lupus erythematosus (SLE)
  • Glucose-6-phosphate hydrogenase deficiency

Study & Design

Study Type
INTERVENTIONAL
Study Design
CROSSOVER
Arm && Interventions
GroupInterventionDescription
AntibioticsantibioticsA: co-trimoxazole prophylactically for 12 months followed by intravenous immunoglobulin treatment for 12 months. Treatments will be separated by a washout period of 3 months during which co-trimoxazole will be given.
Antibioticsintravenous immunoglobulinsA: co-trimoxazole prophylactically for 12 months followed by intravenous immunoglobulin treatment for 12 months. Treatments will be separated by a washout period of 3 months during which co-trimoxazole will be given.
intravenous immunoglobulinsintravenous immunoglobulinsB: intravenous immunoglobulin treatment for 12 months followed by co-trimoxazole prophylactically for 12 months. Treatments will be separated by a washout period of 3 months during which co-trimoxazole will be given.
intravenous immunoglobulinsantibioticsB: intravenous immunoglobulin treatment for 12 months followed by co-trimoxazole prophylactically for 12 months. Treatments will be separated by a washout period of 3 months during which co-trimoxazole will be given.
Primary Outcome Measures
NameTimeMethod
the number, duration and type of infection (including use of antibiotics to treat infections), days of fever, hospital admissions and, if applicable, days absent from school or work due to infections.27 months
Secondary Outcome Measures
NameTimeMethod
Safety will be monitored by occurrence of adverse events, vital signs, and laboratory measurements.27 months

Trial Locations

Locations (9)

UMCG

🇳🇱

Groningen, Netherlands

UMC St Radboud

🇳🇱

Nijmegen, Netherlands

AMC

🇳🇱

Amsterdam, Netherlands

LUMC

🇳🇱

Leiden, Netherlands

AZM

🇳🇱

Maastricht, Netherlands

Erasmus MC

🇳🇱

Rotterdam, Netherlands

Jeroen Bosch Ziekenhuis

🇳🇱

Den Bosch, Netherlands

VU

🇳🇱

Amsterdam, Netherlands

UMCU

🇳🇱

Utrecht, Netherlands

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