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A Two-Period Open-label Trial Evaluating Efficacy and Safety of Dasiglucagon in Children With Congenital Hyperinsulinism

Phase 3
Completed
Conditions
Congenital Hyperinsulinism
Interventions
Other: Standard of Care
Registration Number
NCT03777176
Lead Sponsor
Zealand Pharma
Brief Summary

The objective of the trial is to evaluate the efficacy and safety of dasiglucagon administered as a subcutaneous (SC) infusion in reducing hypoglycemia in children with CHI.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
32
Inclusion Criteria
  • Established and documented diagnosis of CHI based on standard of care
  • Experiencing ≥3 events of hypoglycemia per week (plasma glucose [PG] <70 mg/dL [<3.9 mmol/L]) according to the investigator's evaluation
  • Previously undergone near-total pancreatectomy or being treated with a non-surgical approach, having been evaluated as not eligible for pancreatic surgery
  • If somatostatin analogues or sirolimus are used, the therapy should be well established as judged by the investigator, especially when considering their biological half-life
Exclusion Criteria
  • Previous administration of dasiglucagon
  • Known or suspected allergy to the trial drug or related products
  • Previous participation (randomization) in this trial
  • Circulatory instability requiring supportive medication or presence of pheochromocytoma
  • Requires exogenous insulin
  • Body weight of <4 kg (8.8 lbs.)
  • Documented HbA1c ≥7% subsequent to near-total pancreatectomy and within 6 months prior to screening
  • Known or suspected presence of significant central nervous system disease/injury such that in the investigator's opinion will affect trial participation
  • Use of systemic corticosteroids, e.g., hydrocortisone >20 mg/m2 body surface area or equivalent in the 5 days before screening
  • Use of anti-inflammatory biological agents, or other immune modulating agents in the 3 months prior to screening
  • Any clinically significant abnormality identified on echocardiogram that in the opinion of the investigator would affect the patient's ability to participate in the trial
  • Any recognized clotting or bleeding disorders
  • Has participated in an interventional clinical trial (investigational or marketed product) within 3 months of screening or 5 half-lives of the drug under investigation (whichever comes first), or plans to participate in another clinical trial.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Standard of Care OnlyStandard of Care4 weeks (Treatment Period 1) of standard of care only + 4 weeks (Treatment Period 2) of dasiglucagon treatment as an SC infusion starting at 10 µg/hr on top of standard of care
Standard of Care + dasiglucagonStandard of Care4 weeks (Treatment Period 1) + 4 weeks (Treatment Period 2) of dasiglucagon treatment as an SC infusion starting at 10 µg/hr on top of standard of care
Standard of Care + dasiglucagonDasiglucagon4 weeks (Treatment Period 1) + 4 weeks (Treatment Period 2) of dasiglucagon treatment as an SC infusion starting at 10 µg/hr on top of standard of care
Standard of Care OnlyDasiglucagon4 weeks (Treatment Period 1) of standard of care only + 4 weeks (Treatment Period 2) of dasiglucagon treatment as an SC infusion starting at 10 µg/hr on top of standard of care
Primary Outcome Measures
NameTimeMethod
Hypoglycemia Episode RateBaseline, Week 2-4 (Treatment Period 1)

Hypoglycemia episode rate, defined as average weekly number of hypoglycemic episodes (PG \<70 mg/dL \[3.9 mmol/L\]) during Weeks 2-4 as detected by self-monitored plasma glucose (SMPG). The Week 2-4 value is the average weekly number of hypoglycemic episodes across the last 3 weeks of the treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value is the average weekly number of hypoglycemic episodes during the 2-week baseline period.

Secondary Outcome Measures
NameTimeMethod
Rate of Gastric Carbohydrates Administrations to Treat HypoglycemiaBaseline, Week 2-4 (Treatment Period 1)

Rate of gastric carbohydrate administrations via nasogastric tube or gastrostomy per week to treat hypoglycemia, calculated as the number of times gastric carbohydrates were administered to treat hypoglycemia per week. The Week 2-4 value is the average weekly rate of gastric carbohydrate administrations across the last 3 weeks of the treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value is the value recorded during the 2-week Baseline period.

Total Amount of Gastric Carbohydrates AdministeredBaseline, Week 2-4 (Treatment Period 1)

Total amount of gastric carbohydrates administered (regardless of whether this was to treat hypoglycemia or not) via nasogastric tube or gastrostomy per week. The Week 2-4 value is the average amount of gastric carbohydrates administered via nasogastric tube or gastrostomy across the last 3 weeks of the treatment period. The change from baseline to Week 2-4 is also provided. The baseline value is the value recorded during the 2-week baseline period.

Percent Time in Hypoglycemia in Treatment Period 2Baseline, Week 6-8 (Treatment Period 2)

Percent time in hypoglycemia (PG \<70 mg/dL \[3.9 mmol/L\]) as measured by continuous glucose monitoring. The Week 6-8 value is the average weekly percent of time in hypoglycemia across the last 3 weeks of the treatment period. The change from Baseline to Week 6-8 is also provided. The Baseline value is the value assessed during the 14 days before randomization.

Rate of Gastric Carbohydrates Administrations to Treat Hypoglycemia in Treatment Period 2Baseline, Week 6-8 (Treatment Period 2)

Rate of gastric carbohydrate administrations via nasogastric tube or gastrostomy per week to treat hypoglycemia, calculated as the number of times gastric carbohydrates were administered to treat hypoglycemia per week. The Week 6-8 value is the average weekly rate of gastric carbohydrate administrations across the last 3 weeks of the treatment period. The change from Baseline to Week 6-8 is also provided. The Baseline value is the value recorded during the 2-week Baseline period.

Increase in Fasting ToleranceBaseline, Week 2-4 (Treatment Period 1)

Increase in fasting tolerance (time from beginning of meal to the beginning of the first continuous 15-minute continuous glucose monitoring reading \<70 mg/dL \[3.9 mmol/L\]), or the time the test ended if a continuous 15-minute CGM reading \<70 mg/dL was not reached. The change from Baseline to the End of Treatment Period 1 (Week 4) is also provided. The Baseline value is the value recorded at the Screening visit.

Percent Time in Range 70-180 mg/dLBaseline, Week 2-4 (Treatment Period 1)

Percent time in range 70-180 mg/dL (3.9-10.0 mmol/L) during Weeks 2-4 as measured by continuous glucose monitoring. The Week 2-4 value is the average weekly percent time in range 70-180 mg/dL across the last 3 weeks of the treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value was calculated as the average percent time in range during the 14 days before randomization.

Total Amount of Gastric Carbohydrates Administered to Treat HypoglycemiaBaseline, Week 2-4 (Treatment Period 1)

Total amount of gastric carbohydrates administered via nasogastric tube or gastrostomy per week to treat hypoglycemia. The Week 2-4 value is the average weekly total amount of gastric carbohydrates across the last 3 weeks of treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value is the value recorded during the 2-week Baseline period.

Rate of Clinically Significant Hypoglycemia Episodes in Treatment Period 2Baseline, Week 6-8 (Treatment Period 2)

Change from Baseline to Week 6-8 in the clinically significant (CS) hypoglycemia episode rate in treatment period 2, defined as the average weekly number of episodes \<54 mg/dL (3.0 mmol/L), for 15 minutes or more, as measured by continuous glucose monitoring (CGM). The Week 6-8 value is the average weekly CS hypoglycemia episode rate across the last 3 weeks of the treatment period. The Baseline value is the average weekly number of CS hypoglycemic episodes during the 14 days before randomization.

Clinically Significant Hypoglycemia Episode RatesBaseline, Week 2-4 (Treatment Period 1)

Clinically significant hypoglycemia episode rates during Weeks 2-4, defined as average weekly number of clinically significant hypoglycemic episodes (PG \<54 mg/dL \[3.0 mmol/L\]), as detected by SMPG. The Week 2-4 value is the average weekly clinically significant hypoglycemia episode rate across the last 3 weeks of the treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value is the average weekly number of clinically significant hypoglycemic episodes during the 2-week baseline period.

Extent of HypoglycemiaBaseline, Week 2-4 (Treatment Period 1)

Extent of hypoglycemia (area over the glucose curve \[AOCglucose\] below 70 mg/dL \[3.9 mmol/L\]) and below 54 mg/dL \[3.0 mmol/L\] as measured by continuous glucose monitoring. The extent of hypoglycemia was defined as the AOCglucose under the threshold divided by total duration in hours of CGM measurement. A reduction in this measure indicates a benefit. The Week 2-4 value is the average weekly extent of hypoglycemia below 70 mg/dL and below 54 mg/dL across the last 3 weeks of the treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value is the value assessed during the 14 days before randomization.

Amount of Nightly Gastric Carbohydrates AdministeredBaseline, Week 2-4 (Treatment Period 1)

Amount of nightly (midnight to 6 am) gastric carbohydrates administered via nasogastric tube or gastrostomy per week. The change from Baseline is also provided for each week. The Baseline value is the value recorded during the 2-week Baseline period.

Percent Time in HypoglycemiaBaseline, Week 2-4 (Treatment Period 1)

Percent time in hypoglycemia (PG \<70 mg/dL \[3.9 mmol/L\]) as measured by continuous glucose monitoring. The Week 2-4 value is the average weekly percent of time in hypoglycemia across the last 3 weeks of the treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value is the value assessed during the 14 days before randomization.

Rate of Hypoglycemic EpisodesBaseline, Week 2-4 (Treatment Period 1)

Rate of hypoglycemic episodes, defined as number of episodes with PG \<70 mg/dL (3.9 mmol/L) for 15 minutes or more per week, as measured by continuous glucose monitoring. The Week 2-4 value is the average weekly number of hypoglycemic episodes across the last 3 weeks of the treatment period. The change from Baseline to Week 2-4 is also provided. The Baseline value is the average weekly number of hypoglycemic episodes during the 14 days before randomization.

Rate of Hypoglycemic Episodes in Treatment Period 2Baseline, Week 6-8 (Treatment Period 2)

Hypoglycemia episode rate, defined as average weekly number of hypoglycemic episodes (PG \<70 mg/dL \[3.9 mmol/L\]) as detected by SMPG. The Week 6-8 value is the average weekly number of hypoglycemic episodes across the last 3 weeks of the treatment period. The change from Baseline to Week 6-8 is also provided. The Baseline value is the average weekly number of hypoglycemic episodes during the 2-week baseline period.

Trial Locations

Locations (10)

Hadassah Medical Center

🇮🇱

Jerusalem, Israel

Alder Hey Children'sHospital NHS Foundation Trust

🇬🇧

Liverpool, United Kingdom

Children's Hospital of Colorado

🇺🇸

Aurora, Colorado, United States

University Hospital Düsseldorf, Department of Pediatrics

🇩🇪

Düsseldorf, Germany

Otto von Guericke University Magdeburg, Department of Pediatrics

🇩🇪

Magdeburg, Germany

Cook Children's Medical Center

🇺🇸

Fort Worth, Texas, United States

Central Manchester University Hospital NHS Foundation Trust

🇬🇧

Manchester, United Kingdom

NHS Greater Glasgow and Clyde

🇬🇧

Glasgow, United Kingdom

Great Osmond Street Hospital for Children NHS Foundation Trust

🇬🇧

London, United Kingdom

Children's Hospital of Philadelphia

🇺🇸

Philadelphia, Pennsylvania, United States

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