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Denali Therapeutics Plans Accelerated Approval for MPS II Treatment

Denali Therapeutics has announced its intention to seek accelerated approval for DNL310, a treatment for MPS II (Hunter Syndrome), following positive discussions with the FDA. The company plans to submit a biologics license application in early 2025.

After recent successful meetings with the FDA, Denali Therapeutics announced its plan to file for accelerated approval of DNL310 for the treatment of MPSII, also known as Hunter Syndrome.

Carole Ho, MD, Chief Medical Officer of Denali, expressed gratitude towards the FDA's Center for Drug Evaluation and Research (CDER) for their positive and collaborative discussion. She highlighted the significance of their guidance on CSF HS as a surrogate biomarker, which is seen as a crucial step towards accelerating the development of medicines for individuals and families affected by MPS II.

This milestone is a testament to the collective effort across the patient community, academia, and industry to communicate the science and advocate for faster paths to effective treatments for these devastating rare diseases. Denali Therapeutics is excited about the potential to deliver a new MPS treatment sooner using the accelerated approval pathway. The company also looks forward to plans for conversion to full approval following the completion of the global Phase 2/3 COMPASS study.

Denali Therapeutics plans to submit a biologics license application (BLA) early in 2025 under the accelerated approval pathway, marking a significant step forward in the treatment of MPS II.


Reference News

Denali Therapeutics Announces Plans to File for ...

Denali Therapeutics plans to file for accelerated approval of DNL310 for MPSII (Hunter Syndrome) treatment, following positive FDA discussions. The company aims for a biologics license application (BLA) submission in early 2025, leveraging CSF HS as a surrogate biomarker, and anticipates full approval post-global Phase 2/3 COMPASS study completion.

Denali Therapeutics Announces Successful Meeting with the

Denali Therapeutics plans to submit a biologics license application (BLA) for tividenofusp alfa (DNL310) under the accelerated approval pathway in early 2025, following a successful FDA meeting. Phase 1/2 data presented at SSIEM 2024 shows robust biomarker responses and clinical improvements in MPS II (Hunter syndrome) treatment, supporting the drug's potential for accelerated and full approval.

Denali's DNL310 Eyes Accelerated FDA Approval With ...

FDA and Denali Therapeutics agreed on cerebrospinal fluid heparan sulfate as a surrogate endpoint for DNL310's accelerated approval in treating Hunter syndrome. DNL310 showed a 90% reduction in CSF HS, with sustained effects and safety. Phase 1/2 data revealed improvements in clinical outcomes, supporting its development. A BLA submission is planned for early 2025.

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