A Study Of Association of Pulmonary Hypertension in Connective Tissue Disorders

This is a prospective observational study at a tertiary care center recruiting the outpatients and inpatients with one of the connective tissue disorders for a study duration of 1 year . After obtaining due permission and clearance from the departments involved, the patients meeting the inclusion criteria, after ruling out the exclusion criteria will be recruited in the study after obtaining their informed consent. The clinical and laboratory data including presenting complaints, relevant examination findings, blood investigation reports along with 2D transthoracic echocardiography findings and additional imaging findings as applicable will be tabulated in a predesigned proforma. The findings of echocardiography, if done as a standard of care routinely, are noted to look for pulmonary hypertension and its severity. In case a recruited participant has multiple visits during the study period, relevant additional details like disease progression and new findings in repeat echocardiography will be noted. Since this is an observational study, there will be no interventions involved.