MedPath

TrEatment Approach in the Multimodal Era Registry

Active, not recruiting
Conditions
Chronic Thromboembolic Pulmonary Hypertension
CTEPH
Registration Number
NCT05629052
Lead Sponsor
International CTEPH Association
Brief Summary

The goal of this observational patient registry is to learn how expert centers treat patients with chronic thromboembolic pulmonary hypertension (CTEPH). CTEPH is a condition in which blood clots block the blood vessels in the lungs. There are currently three treatment options for patients with CTEPH:

* surgery to remove blood clots from large vessels in the lungs (pulmonary endarterectomy (PEA))

* the use of a small balloon to unblock smaller blood vessels (balloon pulmonary angioplasty (BPA))

* drugs

Patients can also receive a combination of these treatments.

The main question this registry aims to answer are:

* How many patients receive a given kind of treatment?

* How do expert centers combine the different treatments?

* Are patients doing better after they receive a given kind of treatment?

* How many patients are alive 1, 3 and 5 years after they receive a given kind of treatment?

Participants will receive the same treatments that they would receive if they did not participate in the study. During the study, patients will visit their doctors as they would do normally. The doctors will collect information on the patients' health and enter it into the study database. The follow-up time will be at least 3 years for all patients.

Detailed Description

Not available

Recruitment & Eligibility

Status
ACTIVE_NOT_RECRUITING
Sex
All
Target Recruitment
1000
Inclusion Criteria
  1. Newly referred patient with CTEPH or chronic thromboembolic pulmonary disease (CTEPD) without PH according to the following criteria:

    1. Mean pulmonary arterial pressure (mPAP) > 20 mmHg at rest with pulmonary vascular resistance (PVR) > 2 Wood units (WU); or if mPAP ≤ 20 mmHg or PVR ≤ 2 WU at rest, have exercise limitations from CTEPD without PH
    2. Abnormal ventilation perfusion scan, pulmonary angiogram, computer tomographic pulmonary angiogram, or magnetic resonance pulmonary angiogram confirming CTEPD as recommended by standard guidelines
  2. Treatment with anticoagulation for ≥ 3 months before diagnosis of CTEPH or CTEPD without PH

  3. Naïve to interventional treatment (both PEA and BPA)

  4. Pre-treatment with PH-specific medication for ≤ 12 months, or no medical pre-treatment, at enrollment

  5. Willing and able to provide informed consent in order to participate in the study (informed consent signed)

  6. Age ≥ 18 years

  7. CTEPH-specific treatment must be modified or initiated at the participating site

Exclusion Criteria
  1. Main cause of PH other than CTEPH
  2. Participating in an interventional clinical trial at enrollment

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
3-year survival3 years after last intervention

Proportion of patients alive 3 years after the last intervention recorded in the registry, or after start of medical treatment for patients not undergoing any interventional treatment

Utilization and combination of treatment modalitiesMin. 3 years

Proportion of patients undergoing a certain type of treatment modality, or a certain combination of modalities

Secondary Outcome Measures
NameTimeMethod
Reason why PEA was not performedMin. 3 years

The main reason why PEA was not performed as chosen by the investigator from a list of pre-defined reasons

1-year survival1 year after last intervention

Proportion of patients alive 1 year after the last intervention recorded in the registry, or after start of medical treatment for patients not undergoing any interventional treatment

Changes in PH-specific medicationMin. 3 years

Proportion of patients experiencing a change in PH-specific medication during the study

Reason why BPA was not performedMin. 3 years

The main reason why BPA was not performed as chosen by the investigator from a list of pre-defined reasons

Complications of treatment interventions (per patient)Min. 3 years

Proportion of patients experiencing complications from BPA or PEA

Complications of treatment interventions (per BPA session)Min. 3 years

Proportion of BPA sessions associated with complications

5-year survival5 year after last intervention

Proportion of patients alive 5 years after the last intervention recorded in the registry, or after start of medical treatment for patients not undergoing any interventional treatment

Trial Locations

Locations (25)

Pulmonary Hypertension Unit, Hospital 12 de Octubre

🇪🇸

Madrid, Spain

Marmara University School of Medicine

🇹🇷

Istanbul, Turkey

Narayana Institute of Cardiac Science

🇮🇳

Bangalore, India

University of Bologna

🇮🇹

Bologna, Italy

Okayama Medical Center

🇯🇵

Okayama, Japan

National Heart Institute

🇲🇽

Mexico City, Mexico

China-Japan Friendship Hospital

🇨🇳

Beijing, China

Shaio Clinic Foundation

🇨🇴

Bogotá, Colombia

General University Hospital

🇨🇿

Prague, Czech Republic

Aarhus University Hospital

🇩🇰

Aarhus, Denmark

University of California San Diego

🇺🇸

San Diego, California, United States

Northwestern University

🇺🇸

Evanston, Illinois, United States

Duke University

🇺🇸

Durham, North Carolina, United States

UT Southwestern

🇺🇸

Dallas, Texas, United States

Hospital Universitario Fundación Favaloro

🇦🇷

Buenos Aires, Argentina

University Hospital Vienna

🇦🇹

Vienna, Austria

University Hospitals Leuven

🇧🇪

Leuven, Belgium

Santa Casa

🇧🇷

Porto Alegre, Brazil

Toronto General Hospital

🇨🇦

Toronto, Ontario, Canada

Kerckhoff Clinic, Department of Thoracic Surgery

🇩🇪

Bad Nauheim, Germany

National Cerebral and Cardiovascular Center

🇯🇵

Osaka, Japan

Department of Cardiac and Vascular Diseases, John Paul II Hospital

🇵🇱

Kraków, Poland

Department of Pulmonary Circulation, Thromboembolic Diseases and Cardiology, European Health Center Otwock

🇵🇱

Otwock, Poland

National Heart Centre of Singapore

🇸🇬

Singapore, Singapore

Royal Papworth Hospital

🇬🇧

Cambridge, United Kingdom

© Copyright 2025. All Rights Reserved by MedPath