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Clinical Trials/DRKS00000298
DRKS00000298
Completed
Not Applicable

Genetic and immunological variability in Autoimmune lymphoproliferative Syndrome. A Patient Register. - ALPS

Centrum für Chronische ImmmundefizienzUniversitätsklinikum Freiburg0 sites311 target enrollmentJanuary 15, 2010

Overview

Phase
Not Applicable
Intervention
Not specified
Conditions
Autoimmune lymphoproliferative syndrome (ALPS)
Sponsor
Centrum für Chronische ImmmundefizienzUniversitätsklinikum Freiburg
Enrollment
311
Status
Completed
Last Updated
last year

Overview

Brief Summary

No summary available.

Registry
who.int
Start Date
January 15, 2010
End Date
August 31, 2017
Last Updated
last year
Study Type
Observational
Sex
All

Investigators

Sponsor
Centrum für Chronische ImmmundefizienzUniversitätsklinikum Freiburg

Eligibility Criteria

Inclusion Criteria

  • The following inclusion criteria are applied for patient selection:
  • 1\. Chronic benign lymphoproliferation (i.e. splenomegaly \+/\- lymphadenopathy \> 3 months, \> 0\.5 cm, at 2 sites without infectious or malignant cause) and autoimmune cytopenia in \>\= 1 lineage or:
  • 2\. Patients without lymphoproliferation but with autoimmune cytopenia in \>\= 2 lineages (Evan' s Syndrome)

Exclusion Criteria

  • No written informed consent of patient or parents (in case of minors) has been obtained

Outcomes

Primary Outcomes

Not specified

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