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Clinical Trials/EUCTR2012-000856-33-FR
EUCTR2012-000856-33-FR
Active, not recruiting
Phase 1

A phase I/II, open-label, study of intracerebral administration of adeno-associated viral vector containing the human alpha-N-acetylglucosaminidase cDNA in children with Sanfilippo type B syndrome

Institut Pasteur0 sitesMay 15, 2014

Overview

Phase
Phase 1
Intervention
Not specified
Conditions
Mucopolysaccharidosis III B
Sponsor
Institut Pasteur
Status
Active, not recruiting
Last Updated
8 years ago

Overview

Brief Summary

No summary available.

Registry
who.int
Start Date
May 15, 2014
End Date
TBD
Last Updated
8 years ago
Study Type
Interventional clinical trial of medicinal product
Sex
All

Investigators

Eligibility Criteria

Inclusion Criteria

  • Age: 18 months up to the 5th birthday;
  • Onset of clinical manifestations related to MPSIIIB;
  • NaGlu activity in peripheral blood cell and/or cultured fibroblast extracts of less than 10% of controls;
  • Patient affiliated to, or covered by a French social security regimen or European patients with European Health Insurance Card
  • Family understanding the procedure and the informed consent;
  • Signed informed consent by both parents or legal representative
  • Vital laboratory parameters within normal range
  • Are the trial subjects under 18? yes
  • Number of subjects for this age range: 4
  • F.1\.2 Adults (18\-64 years) no

Exclusion Criteria

  • Presence of brain atrophy on pre\-inclusion MRI judged on a cortico\-dural distance of more than 0\.6 cm
  • Any condition that would contraindicate general anaesthesia;
  • Any other permanent medical condition not related to MPSIIIB that could contraindicate the study participation;
  • No independent walking (Ability to walk without help);
  • Any medication aiming at modifying the natural course of MPSIIIB given during the 6 months before vector injection (sleep and mood regulators are accepted)
  • Any condition that would contraindicate treatment with Tacrolimus, Cellcept® and Solupred®/Solumedrol®.

Outcomes

Primary Outcomes

Not specified

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