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A Study to Evaluate the Efficacy and Safety of Rituximab Versus Mycophenolate Mofetil (MMF) in Participants With Pemphigus Vulgaris (PV)

Registration Number
NCT02383589
Lead Sponsor
Hoffmann-La Roche
Brief Summary

This is a Phase III, randomized, double-blind, double-dummy, active-comparator, parallel-arm, multicenter study to evaluate the efficacy and safety of rituximab compared with MMF in participants with moderate-to-severely active PV requiring 60-120 milligrams per day (mg/day) oral prednisone or equivalent. Participants must have a confirmed diagnosis of PV within the previous 24 months (by skin or mucosal biopsy and immunohistochemistry) and evidence of active disease at screening.

Approximately 135 participants will be enrolled at up to 60 centers worldwide. Participants will be randomized in a 1:1 ratio to receive either rituximab plus MMF placebo or rituximab placebo plus MMF. Randomization will be stratified by duration of illness.

The study will consist of three periods: a screening period of up to 28 days, a 52-week double-blind treatment period, and a 48-week safety follow up period that begins at the time of study treatment completion or discontinuation.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
135
Inclusion Criteria
  • Confirmed diagnosis of PV within the previous 24 months, based on the presence of histological features of acantholysis via skin or mucosal biopsy and one of the following: tissue bound immunoglobulin G (IgG) antibodies by direct immunofluorescence on the surface of affected epithelium or serological detection of serum desmoglein-3 (DSg3) autoantibodies against epithelial cell surface either by indirect immunofluorescence microscopy or by enzyme-linked immunosorbent assay
  • Presence of moderate-to-severely active disease, defined as overall PDAI activity score of greater than or equal to (>/=)15
  • Receiving standard-of-care corticosteroids consisting of 60-120 mg/day oral prednisone or equivalent and, in the judgment of the investigator, expected to benefit from the addition of immunosuppressive therapy
  • For women who are not postmenopausal (>/=12 months of non-therapy-induced amenorrhea) or surgically sterile (absence of ovaries and/or uterus): agreement to remain abstinent or use two effective methods of contraception, including at least one method with a failure rate of less than (<) 1 percent (%) per year, during the treatment period and for at least 12 months after the last dose of study treatment

Abstinence is acceptable only if it is in line with the preferred and usual lifestyle of the participant. Periodic abstinence (e.g., calendar, ovulation, symptothermal, or postovulation methods) and withdrawal are not acceptable methods of contraception

Barrier methods must always be supplemented with the use of a spermicide

Examples of contraceptive methods with a failure rate of < 1% per year (highly effective contraceptive methods) include tubal ligation, male sterilization, hormonal implants, established, proper use of combined oral or injected hormonal contraceptives, and certain intrauterine devices

  • For men (including those who have undergone a vasectomy): agreement to remain abstinent or use a condom during the treatment period and for at least 12 months after the last dose of study treatment and agreement to refrain from donating sperm during this same period

Abstinence is only acceptable if it is in line with the preferred and usual lifestyle of the participant

Periodic abstinence (e.g., calendar, ovulation, symptothermal, or postovulation methods) and withdrawal are not acceptable methods of contraception. In addition to male contraception, agreement to advise female partners of childbearing potential to use highly effective contraception during the study and for at least 12 months after the last dose of study treatment

  • Agreement to avoid excessive exposure to sunlight during study participation
  • Able to comply with the study protocol, in the investigator's judgment
Exclusion Criteria
  • Diagnosis of pemphigus foliaceus or evidence of paraneoplastic pemphigus or other non-PV autoimmune blistering disease
  • History of a severe allergic or anaphylactic reaction to humanized or murine monoclonal antibodies, or known hypersensitivity to any component of rituximab
  • Known hypersensitivity or contraindication to MMF, mycophenolic acid, polysorbate, or oral corticosteroids
  • Lack of peripheral venous access
  • Pregnant or lactating, or intending to become pregnant during the study

Women who are not postmenopausal (>/=12 months of non-therapy-induced amenorrhea) or surgically sterile must have two negative results with a sensitivity of >/=25 milli-international units per milliliter (mIU/mL): one from a serum pregnancy test at Day -8 to Day -10 of screening and another from a urine pregnancy test at Day 1 prior to randomization

  • Participated in another interventional clinical trial within 28 days prior to randomization
  • Use of any investigational agent within 28 days or 5 elimination half-lives prior to randomization (whichever is the longer)
  • Significant cardiovascular or pulmonary disease (including obstructive pulmonary disease)
  • Evidence of any new or uncontrolled concomitant disease that, in the investigator's judgment, would preclude participant participation, including but not limited to nervous system, renal, hepatic, endocrine, malignant, or gastrointestinal disorders
  • Any concomitant condition that required treatment with oral or systemic corticosteroids within 12 weeks prior to randomization
  • Treatment with intravenous (IV) immunoglobulin (Ig), plasmapheresis, or other similar procedure within 8 weeks prior to randomization
  • Treatment with immunosuppressive medications (e.g., azathioprine, MMF) within 1 week prior to randomization
  • Treatment with cyclophosphamide within 12 weeks prior to randomization
  • History of or currently active primary or secondary immunodeficiency, including known history of HIV infection and other severe immunodeficiency blood disorders
  • Known active infection of any kind (excluding fungal infections of nail beds) or any major episode of infection requiring hospitalization or treatment with IV anti-infectives within 4 weeks prior to screening, or completion of oral anti-infectives within 2 weeks prior to randomization; entry into this study may be reconsidered once the infection has fully resolved
  • History of or current cancer, including solid tumors, hematologic malignancies, and carcinoma in situ (except complete excision of basal cell of the skin and squamous cell carcinoma of the skin that have been treated or excised and cured)
  • Currently active alcohol or drug abuse, or history of alcohol or drug abuse within 24 weeks prior to screening
  • Major surgery within 4 weeks prior to randomization, excluding diagnostic surgery
  • Treatment with rituximab or a B cell-targeted therapy (e.g., anti-cluster of differentiation [CD] 20 [CD20], anti CD22, or anti-B-lymphocyte stimulator [BLyS]) within 12 months prior to randomization
  • Treatment with a live or attenuated vaccine within 28 days prior to randomization; it is recommended that a participant's vaccination record and the need for immunization prior to study entry be carefully investigated
  • Evidence of abnormal liver enzymes or hematology laboratory values
  • Positive test results for hepatitis B surface antigen (HBsAg), hepatitis B core antibody (HBcAb), or hepatitis C virus (HCV) serology at screening

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Mycophenolate Mofetil (MMF)Rituximab PlaceboParticipants will receive MMF orally twice daily (every 12 hours, Q12H) from Day 1 to Week 52. Participants will also receive rituximab matching placebo by intravenous (IV) infusion on Days 1 and 15 with repeat administration on Days 168 and 182 provided specific safety criteria have been met.
Rituximab (RTX)Mycophenolate Mofetil PlaceboParticipants will receive rituximab by IV infusion on Days 1 and 15 with repeat administration on Days 168 and 182 provided specific safety criteria have been met. Participants will also receive MMF matching placebo orally twice daily Q12H from Day 1 to Week 52.
Mycophenolate Mofetil (MMF)Mycophenolate MofetilParticipants will receive MMF orally twice daily (every 12 hours, Q12H) from Day 1 to Week 52. Participants will also receive rituximab matching placebo by intravenous (IV) infusion on Days 1 and 15 with repeat administration on Days 168 and 182 provided specific safety criteria have been met.
Rituximab (RTX)RituximabParticipants will receive rituximab by IV infusion on Days 1 and 15 with repeat administration on Days 168 and 182 provided specific safety criteria have been met. Participants will also receive MMF matching placebo orally twice daily Q12H from Day 1 to Week 52.
Primary Outcome Measures
NameTimeMethod
Percentage of Participants (Excluding Telemedicine [TM] Participants) Who Achieved Sustained Complete Remission, Evaluated by the Pemphigus Disease Area Index (PDAI) Activity ScoreFrom Baseline up to 52 Weeks (up to clinical cut-off date (CCOD) of 28 November 2018)
Secondary Outcome Measures
NameTimeMethod
Time to Protocol Defined Disease FlareFrom Baseline up to 52 Weeks (up to CCOD of 28 November 2018)

Disease flare is defined as the appearance of three or more new lesions a month that do not heal spontaneously within 1 week or by the extension of established lesions in a participant who has achieved disease control.

Change in Health-Related Quality of Life (HRQoL), as Measured by the Dermatology Life Quality Index (DLQI) ScoreFrom Baseline up to 52 Weeks (up to CCOD of 28 November 2018)

Total DLQI scores range from 0 to 30 with higher DLQI scores reflecting greater impairment in a participant's health-related quality of life. The DLQI score is calculated by summing the score of each question resulting in a maximum of 30 and a minimum of 0. The higher the score, the more quality of life is impaired. The measure type mean is the estimated mean from adjusted MMRM.

Percentage of Participants With Immunoglobulin (Ig) Levels Below Lower Limit of Normal (LLN)Baseline; Weeks 16, 24, 40 and 52; (end of treatment: up to Week 52) (up to CCOD of 28 November 2018)
Percentage of Participants With Adverse Events, Serious Adverse Events, and Corticosteroid-Related Adverse EventsBaseline up to 52 Weeks (up to CCOD of 28 November 2018)

An adverse event is any untoward medical occurrence in a participant to whom a medicinal product is administered and which does not necessarily have a causal relationship with this treatment. A serious adverse event is an adverse event that results in death or is life-threatening or requires/prolongs hospitalization or results in persistent/significant disability/incapacity or congenital abnormality/birth defect. Adverse events of Grade 3 of higher are severe and life-threatening adverse events CS-related adverse events - causality as determined by the investigator.

Time to Initial Sustained Complete RemissionFrom Baseline up to 52 Weeks (up to CCOD of 28 November 2018)
Percentage of Participants With Anti-Drug Antibodies (ADA)Baseline up to 52 Weeks (up to CCOD of 28 November 2018)

Participants with treatment-induced and treatment-enhanced anti-drug antibodies. The clinical relevance of anti-rituximab antibody formation in RITUXAN treated pemphigus vulgaris (PV) participants is unclear.

Cumulative Oral Corticosteroid DoseFrom Baseline up to 52 Weeks (up to CCOD of 28 November 2018)
Total Number of Protocol Defined Disease FlaresFrom Baseline up to 52 Weeks (up to CCOD of 28 November 2018)

Disease flare is defined as appearance of three or more new lesions a month that do not heal spontaneously within 1 week, or by the extension of established lesions, in a participant who has achieved disease control.

Trial Locations

Locations (68)

Gülhane Military Medical Academy in Ankara

🇹🇷

Ankara, Turkey

Hospital de la Victoria

🇪🇸

Malaga, Spain

Dnipropetrovsk State Medical Academy

🇺🇦

Dnipropterovsk, Ukraine

Gaziantep University Medical Faculty Sahinbey Hospital

🇹🇷

Gaziantep, Turkey

Celal Bayar University Medical Faculty Hafsa Sultan Hospital

🇹🇷

Manisa, Turkey

Bezm-i Alem University Medical Faculty

🇹🇷

Istanbul, Turkey

Akdeniz University Medical Faculty

🇹🇷

Antalya, Turkey

Haydarpasa Numune Training and Research Hospital

🇹🇷

Istanbul, Turkey

Marmara Uni

🇹🇷

Istanbul, Turkey

Territorial Medical Association "Dermatovenerologia"

🇺🇦

Kyiv, Ukraine

Hosp. G. U Gregorio Marañón

🇪🇸

Madrid, Spain

Istanbul Uni Istanbul Medical Faculty

🇹🇷

Istanbul, Turkey

Hospital Clínic. Barcelona

🇪🇸

Barcelona, Spain

Karadeniz Teknik Üniversitesi Tıp Fakültesi Farabi Hastanesi

🇹🇷

Trabzon, Turkey

University of Alabama Birmingham

🇺🇸

Birmingham, Alabama, United States

University of Arizona Medical Research Office

🇺🇸

Tucson, Arizona, United States

UC Davis Department of Dermatology

🇺🇸

Sacramento, California, United States

Massachusetts General Hospital Dermatology

🇺🇸

Boston, Massachusetts, United States

Univ of Calif-San Francisco

🇺🇸

San Francisco, California, United States

Los Angeles Biomedical Research Institute

🇺🇸

Torrance, California, United States

Northwestern University

🇺🇸

Chicago, Illinois, United States

Uni of NY and Roswell Cancer

🇺🇸

Buffalo, New York, United States

Cleveland Clinic

🇺🇸

Cleveland, Ohio, United States

St Louis University Hospital

🇺🇸

Saint Louis, Missouri, United States

Wake Forest Baptist Hospital Center for Dermatology Research

🇺🇸

Winston-Salem, North Carolina, United States

Oregon Health Sciences Uni

🇺🇸

Portland, Oregon, United States

Hospital Italiano

🇦🇷

Buenos Aires, Argentina

Centro de Investigaciones Médicas - CIM

🇦🇷

Florencio Varela, Argentina

Hospital Luis Lagomaggiore

🇦🇷

Mendoza, Argentina

Hospital Austral

🇦🇷

Pilar, Pcia De Buenos Aires, Argentina

St George Hospital

🇦🇺

Kogarah, New South Wales, New South Wales, Australia

Veracity Clinical Research

🇦🇺

Woolloongabba, Queensland, Australia

Faculdade de Medicina de Botucatu - Hospital das Clínicas

🇧🇷

Botucatu, SP, Brazil

Hospital das Clinicas - FMUSP

🇧🇷

Sao Paulo, SP, Brazil

Santa Casa de São Paulo Hospital Central X

🇧🇷

São Paulo, SP, Brazil

University of Alberta

🇨🇦

Edmonton, Alberta, Canada

Guildford Dermatology

🇨🇦

Surrey, British Columbia, Canada

Lynde Institute for Dermatology

🇨🇦

Markham, Ontario, Canada

Department of Dermatology Avicenne Hospital & University

🇫🇷

Bobigny, France

CHU Hopitaux de Bordeaux

🇫🇷

CHU Hopitaux De Bordeaux, France

Centre Hospitalier Régional Universitaire de Lille (CHRU) - Hôpital Claude Huriez

🇫🇷

Lille, France

CHU de Reims

🇫🇷

Reims, France

CHU de Rennes - Hopital de Pontchaillo

🇫🇷

Rennes, France

CHU Saint Etienne - Hôpital Nord

🇫🇷

Saint Etienne, France

Les Hospices Civils de Lyon Dermatologie inflammatoire et médecine interne

🇫🇷

Lyon / Pierre Bénite, France

CHU de Rouen - Hôpital Charles Nicolle

🇫🇷

Rouen, France

Kompetenzzentrum Fragile Haut Klinik fur Dermatologie und Venerologie

🇩🇪

Freiburg, Germany

Universitätsklinikum Heidelberg

🇩🇪

Heidelberg, Germany

Klinik und Poliklinik für Dermatologie und Venerologie Universitätsklinikum Köln

🇩🇪

Koeln, Germany

University Hospital Schleswig-Holstein

🇩🇪

Lübeck, Germany

Universitaetsmedizin der Johannes Gutenberg-Universitaet Mainz KöR, Hautklinik und Poliklinik

🇩🇪

Mainz, Germany

University of Munster

🇩🇪

Muenster, Germany

HaEmek MC

🇮🇱

Afula, Israel

Rambam Medical Centre; Dept. of Dermatology

🇮🇱

Haifa, Israel

Rabin Medical Centre; Dept. of Dermatology

🇮🇱

Petach Tikva, Israel

Sheba Medical Center

🇮🇱

Ramat Gan, Israel

Sourasky Medical Centre

🇮🇱

Tel-Aviv, Israel

Università di Parma Clinica Dermatologica

🇮🇹

Parma, Lazio, Italy

Ambulatorio di Malattie Rare e Immunopatologia Cutanea

🇮🇹

Florence, Lazio, Italy

U.O. Dermatologia Dipartimento Malattie Infettive Fondazione IRCCS Policlinico San Matteo

🇮🇹

Pavia, Lazio, Italy

Centro Clinico per le genodermatosi Dipartimento di Dermatologia dell'Immacolata - IRCCS

🇮🇹

Rome, Lazio, Italy

S.C. Dermatologia 2 - Ambulatorio Malattie Rare

🇮🇹

Turin, Lazio, Italy

ASST DEGLI SPEDALI CIVILI DI BRESCIA; Clinica Dermatologica

🇮🇹

Brescia, Lombardia, Italy

Clinica Universitaria de Navarra

🇪🇸

Pamplona, Navarra, Spain

University Hospital for Dermatology

🇩🇪

Dresden, Germany

Icahn School of Medicine at Mount Sinai

🇺🇸

New York, New York, United States

University of Minnesota

🇺🇸

Minneapolis, Minnesota, United States

Penn University

🇺🇸

Philadelphia, Pennsylvania, United States

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