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Clinical Trials/DRKS00010150
DRKS00010150
Recruiting
未知

Investigation of the underlying pathomechanisms found in defects of the neurotransmitter, Pterine -, phenyl alanine, and 5-Methyltetrahydrofolate metabolism in induced pluripotent stem cells (iPSC) and derivatives - PaNeM

niversitätsklinikum Heidelberg0 sites50 target enrollmentMarch 10, 2016

Overview

Phase
未知
Intervention
Not specified
Conditions
Not specified
Sponsor
niversitätsklinikum Heidelberg
Enrollment
50
Status
Recruiting
Last Updated
last year

Overview

Brief Summary

No summary available.

Registry
who.int
Start Date
March 10, 2016
End Date
TBD
Last Updated
last year
Study Type
Interventional
Sex
All

Investigators

Sponsor
niversitätsklinikum Heidelberg

Eligibility Criteria

Inclusion Criteria

  • Children and adults with confirmed diagnosis of Neurotransmitter disorders
  • o Aromatic amino acid decarboxylase (AADC) deficiency
  • o Tyrosine hydroxylase (TH) deficiency
  • o Dopamine beta\-hydroxylase (DßH) deficiency
  • o Monoamine oxidase A (MAOA) deficiency
  • o Dopamine transporter (DAT) deficiency
  • o Vesicular monoamine transporter 2 (VMAT) deficiency
  • Children and adults with confirmed diagnosis of BH4 Deficiencies
  • o Autosomal rezessive GTP cyclohydrolase deficiency
  • o Autosomal dominant GTP cyclohydrolase deficiency (Segawa disease)

Exclusion Criteria

  • Not provided

Outcomes

Primary Outcomes

Not specified

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