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Cardiac Rehabilitation of Children and Adolescent With Long QT Syndrome

Active, not recruiting
Conditions
Congenital Long Qt Syndrome
Pediatric ALL
Long QT Syndrome
Inherited Cardiac Conduction Disorder
Registration Number
NCT05964322
Lead Sponsor
University Hospital, Montpellier
Brief Summary

Children and adolescents with inherited cardiac arrhythmia su ch Long QT Syndrome (LQTS) have lower physical and quality of life than their healthy peers. A multi-component cardiac rehabilitation, including an exercise training program and education program, might counteract those effects.

The goal of this pilot study is to evaluate the security, feasibility, and benefits of a cardiac rehabilitation program in children with LQTS aged between 6 to 18 years old.

The main question\[s\] it aims to answer are:

* Is center-based cardiac rehabilitation safe and feasible for children with LQTS?

* Does a 12-week cardiac rehabilitation program improve physical fitness and quality of life?

Detailed Description

Physical fitness is an independent predictor of all-cause mortality and global health in the general population. Assessments of cardiorespiratory and muscle fitness in children with chronic illness are growing in interest, even in less prevalent chronic diseases. For instance, children and adolescents with Long QT Syndrome (LQTS) have lower cardiorespiratory fitness, muscle strength, and quality of life than their healthy peers.

A multi-component cardiac rehabilitation including an exercise training program and education program might counteract this lowered physical fitness.

The RYTHMO'FIT pilot study seeks to test the security, and feasibility, and to evaluate the benefits of an innovative center-based program to improve physical and mental health in children and adolescents with LQTS.

In this retrospective study, eight children had undergone a 12-week program, within each session composed by:

* A 1-hour exercise training session with a trained exercise physiologist: resistance training, aerobic training, stretching, and different activity (e.g., basketball, handball, football, hockey)

* A 30-min educational workshop with a specialist nurse (e.g., beta-blockade, sports participation, healthy behaviors).

* A 10-min medical interview with a cardiologist to have feedback from parents and patients on each session and the past 7 seven days.

We hypothesized the RYTHMO'FIT study is safe, feasible, and provides benefits for mental and physical health in children and adolescents with LQTS. If the results of this pilot study are positive, they will lead to a larger randomized multicentric controlled trial to evaluate the effectiveness of a hybrid cardiac rehabilitation program in children, adolescents, and young adults with LQTS.

Recruitment & Eligibility

Status
ACTIVE_NOT_RECRUITING
Sex
All
Target Recruitment
8
Inclusion Criteria

Not provided

Exclusion Criteria

Not provided

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Recruitment ratesAt week 12

Number of participants who completed baseline assessment compared to the number who were eligible (expressed in %).

AdherenceAt week 12

Percentage exercise sessions attained by participants compared to number of sessions proposed.

SecurityAt week 12

Count and specify any cardiac events on the ECG scope during each session. Reporting of related and non-related event during the past 7 days through short questionnaire each week.

Retention ratesAt week 12

Participants who participated in the 12-week intervention and completed the follow-up assessments at the end of the program (expressed in %).

Secondary Outcome Measures
NameTimeMethod
Change on cardiorespiratory fitnessbetween week 0 and week 12

Assessing the following variables by cardiopulmonary exercise testing: peak oxygen uptake (VO2peak), ventilatory anaerobic threshold (VAT), ventilatory efficiency (VE/VCO2 slope), maximum heart rate (HR), oxygen pulse (VO2/HR), maximal power, respiratory exchange ratio.

Change on Proxy-reported total score of the Pediatric Quality of Life Inventory (PedsQL)between week 0 and week 12
Pediatric Quality of Life Inventory (PedsQL) 4.0 Health-related quality (HRQoL ) of life questionnaire score per dimension (self and proxy reports)between week 0 and week 12
Change on cardiological outcomesbetween week 0 and week 12

Electrocardiographic at rest (QTc, heart rate, PR, QRS interval time) and echocardiography (LVEF, IVSd, IVSs, LVEDV, E/A ratio)

Change on muscle architecturebetween week 0 and week 12

Assessing the following variables by ultrasounding: Anatomical cross sectional area, pennation angle, fascicle length and muscle thickness

Change on muscle strengthbetween week 0 and week 12

Lower and upper limb maximal isometric strength by knee extension and handgrip test, respectively. Lower body explosive muscular strength was assessed by standing long broad jump.

Change on Self reported total score of the Pediatric Quality of Life Inventory (PedsQL) 4.0 questionnairebetween week 0 and week 12
Change on physical activity levelbetween week 0 and week 12

Time spent in vigorous, moderate-to-vigorous, light physical activity assessed by waist-worn tri axial accelerometer during 7 days.

Trial Locations

Locations (2)

University Hospital of Montpellier - Arnaud de Villeneuve Hospita

🇫🇷

Montpellier, France

Saint-Pierre Institute

🇫🇷

Palavas-les-Flots, France

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