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Efficacy and Safety of SOM3355 in Huntington's Disease Chorea

Phase 2
Completed
Conditions
Huntington's Chorea
Interventions
Drug: SOM3355 100mg BID
Drug: SOM3355 200mg BID
Drug: Placebo BID
Registration Number
NCT03575676
Lead Sponsor
SOM Innovation Biotech SA
Brief Summary

Phase IIa study to evaluate the efficacy and safety of SOM3355 in chorea movements associated with Huntington's disease

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
32
Inclusion Criteria
  • Subject is at least 18 years of age at time of consent.
  • Diagnosis of HD definite by a movement disorders expert and confirmed by a number of HTT gene CAG repeats equal or greater than 36.
  • Female of child bearing potential (FCBP) and non-vasectomized male agree to practice appropriate methods of birth control.
  • Ability to walk independently or with minimal assistance.
  • UHDRS TMC score equal or greater than 8.
  • UHDRS TFC equal or greater than 4.
  • Subject has provided written informed consent or through his/her legally authorized representative.
Exclusion Criteria
  • Onset of HD symptoms prior to age 18 (Juvenile forms of HD).
  • Non-ambulatory patients.
  • A past medical history of clinically significant ECG abnormalities or a family history (grandparents, parents and siblings) of a prolonged QT-interval syndrome.
  • Pregnant or breastfeeding female patients, including those planning to conceive during the period of the trial.
  • Patients with psychiatric symptoms, or other impairments, that would interfere with their full compliance with the Investigator instructions and testing, unless there is an identified caregiver to support the patient.
  • Any surgical or medical condition which might significantly alter the absorption, distribution, metabolism, or excretion of drugs, or which may jeopardize the subject in case of participation in the study. The Investigator should make this determination in consideration of the subject's medical history and/or clinical laboratory test results at screening and baseline.
  • Known allergy/sensitivity/intolerance to the study drugs or their excipients.
  • Any significant laboratory results which, in the Investigator's opinion, would not be compatible with study participation or represent a risk for the subject while in the study.
  • Prescribed anti-hypertensive medication, tetrabenazine, deutetrabenazine or valbenazine within 15 days prior starting the investigational treatment.
  • Excluded concomitant medications: any anti-hypertensive medication, tetrabenazine, deutetrabenazine or valbenazine, all typical neuroleptics and all MAO inhibitors
  • Subject has a history of alcohol or substance abuse in the previous 12 months.
  • Patients with diabetic ketoacidosis or metabolic acidosis.
  • Patients with cardiogenic shock, congestive heart failure, pulmonary hypertension due to right-sided heart failure, severe sinus bradycardia, atrioventricular block (grades II and III) or sinoatrial block.
  • Subject has participated in an investigational drug or device trial within 30 days prior starting the investigational treatment.

Study & Design

Study Type
INTERVENTIONAL
Study Design
CROSSOVER
Arm && Interventions
GroupInterventionDescription
Group BPlacebo BIDAdministration of placebo BID for 6 weeks, SOM3355 100mg BID for 6 weeks, SOM3355 200mg BID for 6 weeks and SOM3355 100mg BID for 6 weeks.
Group APlacebo BIDAdministration of SOM3355 100mg BID for 6 weeks, SOM3355 200mg BID for 6 weeks, SOM3355 100mg BID for 6 weeks and placebo BID for 6 weeks.
Group BSOM3355 100mg BIDAdministration of placebo BID for 6 weeks, SOM3355 100mg BID for 6 weeks, SOM3355 200mg BID for 6 weeks and SOM3355 100mg BID for 6 weeks.
Group ASOM3355 100mg BIDAdministration of SOM3355 100mg BID for 6 weeks, SOM3355 200mg BID for 6 weeks, SOM3355 100mg BID for 6 weeks and placebo BID for 6 weeks.
Group ASOM3355 200mg BIDAdministration of SOM3355 100mg BID for 6 weeks, SOM3355 200mg BID for 6 weeks, SOM3355 100mg BID for 6 weeks and placebo BID for 6 weeks.
Group BSOM3355 200mg BIDAdministration of placebo BID for 6 weeks, SOM3355 100mg BID for 6 weeks, SOM3355 200mg BID for 6 weeks and SOM3355 100mg BID for 6 weeks.
Primary Outcome Measures
NameTimeMethod
UHDRS (Unified Huntington's Disease Rating Scale) Total Maximal Chorea (TMC) score6 months

UHDRS subscore used to measure the effectiveness of SOM3355 on HD chorea.

Secondary Outcome Measures
NameTimeMethod
Columbia Suicide Severity Rating Scale (C-SSRS)6 months

International validated questionnaire used for suicide assessment.

UHDRS Total Functional Capacity (TFC)6 months

A standardized rating scale used to assess capacity to work, handle finances, perform domestic chores and self-care tasks.

Clinical Global Impression of Change (CGIC) scale6 months

PGIC reflects clinician's belief about the efficacy of treatment.

Patient Global Impression of Change (PGIC) scale6 months

PGIC reflects a patient's belief about the efficacy of treatment.

UHDRS Functional Assessment6 months

Functional Assessment should be judged according to the investigator's opinion of capacity to perform the activity rather than the actual performance of this activity.

UHDRS Total Motor Score (TMS)6 months

Categoric clinical rating scale assessing multiple domains of motor disability in HD.

UHDRS Gait score6 months

UHDRS subscore used to assess patient's gait.

Safety (number of participants with adverse events)6 months

The maximum grade for each type of AE will be recorded for each subject, and frequency tables will be presented and reviewed to determine patterns. The relationship of the AE to the study treatment will be taken into consideration. Hypotension and cardiovascular events will be specifically analyzed.

Trial Locations

Locations (4)

Hospital Universitari Vall d'Hebron

🇪🇸

Barcelona, Spain

Hospital Universitari de Bellvitge

🇪🇸

L'Hospitalet de Llobregat, Spain

Hospital Clínic de Barcelona

🇪🇸

Barcelona, Spain

Hospital de la Santa Creu i Sant Pau

🇪🇸

Barcelona, Spain

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