MedPath

DAY101 vs. Standard of Care Chemotherapy in Pediatric Participants With Low-Grade Glioma Requiring First-Line Systemic Therapy (LOGGIC/FIREFLY-2)

Phase 3
Recruiting
Conditions
Low-grade Glioma
Pediatric Low-grade Glioma
Rapidly Accelerated Fibrosarcoma (RAF) Altered Glioma
Interventions
Drug: Chemotherapeutic Agent
Registration Number
NCT05566795
Lead Sponsor
Day One Biopharmaceuticals, Inc.
Brief Summary

This is a 2-arm, randomized, open-label, multicenter, global, Phase 3 trial to evaluate the efficacy, safety, and tolerability of tovorafenib monotherapy versus standard of care (SoC) chemotherapy in participants with pediatric low-grade glioma (LGG) harboring an activating rapidly accelerated fibrosarcoma (RAF) alteration requiring first-line systemic therapy.

Detailed Description

Approximately 400 treatment-naïve LGG participants will be randomized 1:1 to either tovorafenib (Arm 1) or an Investigator's choice of SoC chemotherapy (Arm 2).

Arm 1 (tovorafenib): Treatment cycles will repeat every 28 days in the absence of disease progression. Participants will continue tovorafenib until any of the following occurs: disease progression, unacceptable toxicity, withdrawal of consent to treatment, or end of study.

Arm 2 (Investigator's Choice of SoC Chemotherapy): Participants will receive one of 4 SoC chemotherapy options selected by the treating Investigator: Children's Oncology Group - Vincristine/Carboplatin (COG-V/C) regimen, International Society for Paediatric Oncology - Low-Grade Glioma Vincristine/Carboplatin (SIOPe-LGG-V/C) regimen, vinblastine (VBL) regimen, or monthly carboplatin. The choice of SoC chemotherapy regimen will be selected prior to participant randomization. Treatment will continue until completion of therapy or until any of the following occurs: disease progression, unacceptable toxicity, withdrawal of consent to treatment, or end of study.

Participants who discontinue treatment due to disease progression will have (1) radiographic evidence of disease progression, as determined by the Investigator, or (2) clinical progression, as determined by the Investigator. Investigators are encouraged to discuss cases of clinical progression and early radiographic progression without clinical symptoms with the Sponsor Medical Monitor prior to treatment discontinuation or initiation of a different form of treatment for the malignancy. Participants may continue therapy beyond progressive disease (PD).

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
400
Inclusion Criteria
  • Less than 25 years of age with LGG with known activating RAF alteration.
  • Histopathologic diagnosis of glioma or glioneuronal tumor.
  • At least one measurable lesion as defined by RANO criteria.
  • Meet indication for first-line systemic therapy.
Exclusion Criteria
  • Participant has any of the following tumor-histological findings:

    1. Schwannoma
    2. Subependymal giant cell astrocytoma (Tuberous Sclerosis)
    3. Diffuse intrinsic pontine glioma, even if histologically diagnosed as World Health Organization (WHO) Grade I-II
  • Participant's tumor has additional pathogenic molecular alterations, including but not limited to a) isocitrate dehydrogenase (IDH) 1/2 mutation, b) Histone H3 mutation, and c) neurofibromatosis Type 1 (NF-1) loss of function alteration.

  • Known or suspected diagnosis of NF-1/ neurofibromatosis Type 2 (NF-2).

  • Prior or ongoing nonsurgical anticancer therapy for this indication (eg, chemotherapy, oral/IV targeted therapy) including radiation.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
TovorafenibTovorafenib-
Investigator's choice of Standard of care therapyChemotherapeutic Agent-
Primary Outcome Measures
NameTimeMethod
Objective response rate (ORR) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

ORR assessed per Response Assessment in Pediatric Neuro Oncology (RAPNO) criteria by Independent Review Committee (IRC), and defined as the proportion of participants with overall confirmed response of complete response (CR), partial response (PR), or minor response (MR).

Secondary Outcome Measures
NameTimeMethod
Progression-free survival (PFS) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

PFS assessed per RAPNO criteria by IRC, and defined as time from randomization to PD or death from any cause, whichever comes first.

Change in best corrected visual acuity of tovorafenib monotherapy versus SoC chemotherapy in OPG participants aged ≥ 3 yearsBaseline and up to 5 years

Visual acuity assessments to be performed by an ophthalmologist or another qualified site clinical personnel.

Visual progression-free survival (v-PFS) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

Visual progression-free survival is defined as the time from start of treatment to visual event for OPG participants aged ≥ 3 years.

PFS of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

PFS per RANO-HGG or RANO-LGG criteria (as applicable), defined as time from randomization to PD or death from any cause, whichever occurs first.

Event-free survival (EFS) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

EFS assessed per RAPNO criteria by IRC, defined as time from randomization to PD, death from any cause, or initiation of any new anticancer therapy, whichever comes first.

Overall survival (OS) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

Overall survival is defined as time from randomization up to death from any cause.

Number of participants with any treatment-emergent adverse events, and Serious adverse eventsUp to 60 months

Type, frequency, and severity of adverse events of tovorafenib monotherapy versus SoC chemotherapy will be assessed.

. Number of participants with clinically significant vital signs and laboratory abnormalities findingsUp to 60 months

Type, frequency, and severity of vital signs and laboratory abnormalities of tovorafenib monotherapy versus SoC chemotherapy will be assessed.

Change from baseline in Adaptive Behavior Composite Score (ABS) of tovorafenib monotherapy versus SoC chemotherapyBaseline, Year 1, 2 and 5

Adaptive behavior Composite Score will be evaluated using domain scores collected from the comprehensive Vineland III Adaptive Behavior Scale (VABS).

Change from baseline in the Motor Skills Domain Score of tovorafenib monotherapy versus SoC chemotherapyBaseline, Year 1, 2 and 5

The motor skills (gross and fine) will be assessed using the Motor Skills Score domain of the VABS in pediatric participants.

Change from baseline in the Communication Domain Score of tovorafenib monotherapy versus SoC chemotherapyBaseline, Year 1, 2 and 5

The communication skills (receptive, expressive and written) will be assessed using Communication Domain Score of VABS.

Change from baseline in the Daily Living Domain Score of tovorafenib monotherapy versus SoC chemotherapyBaseline, Year 1, 2 and 5

The daily living (personal, domestic and community) will be assessed using Daily Living Domain Score of VABS.

Change from baseline in the Socialization Domain Score of tovorafenib monotherapy versus SoC chemotherapyBaseline, Year 1, 2 and 5

The socialization skills (Interpersonal relationships, play and leisure time and coping skills) will be assessed using Socialization Domain Score of VABS.

Change in age-adjusted visual acuity (VA) of tovorafenib monotherapy versus SoC chemotherapy in optic pathway glioma (OPG) participants aged < 3 yearsBaseline and up to 5 years

Visual acuity testing using current age-appropriate testing methodology will be performed for all participants at Screening. For participants with OPG or an underlying visual deficit related to the primary malignancy, visual acuity testing will be performed every time participants have a radiographic response assessment. Assessments will be performed in each eye separately at a recommended testing distance of 3 meters.

ORR of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

ORR, defined as the proportion of participants with overall confirmed response per Response Assessment in Neuro-Oncology for High-Grade Glioma (RANO-HGG) criteria (CR or PR) and RANO-LGG criteria (CR, PR, or MR), as applicable.

Change from Baseline in health-related quality of life (HRQoL) total score of tovorafenib monotherapy versus SoC chemotherapyBaseline, Year 1, 2 and 5

The Patient-Reported Outcomes Measurement Information System (PROMIS®) Pediatric/Parent Proxy Profile 49 v2.0 will be used to assess mental and social HRQoL.

Clinical benefit rate (CBR) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

CBR, defined as the proportion of participants with radiological tumor stabilization or regression per RANO-LGG (CR, PR, MR, or SD lasting 12 months or more), RANO-HGG (CR, PR, or SD lasting 12 months or more) or RAPNO criteria (CR, PR, MR or SD lasting 12 months or more), as applicable.

Time to response (TTR) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

TTR, measured by the time following randomization to first imaging of tumor response that was subsequently confirmed per RANO-HGG criteria (CR or PR), RANO-LGG criteria (CR, or PR, or MR), or RAPNO criteria (CR, PR, or MR), as applicable.

EFS of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

EFS per RANO-HGG or RANO-LGG criteria (as applicable), defined as time from randomization to PD, death from any cause, or initiation of any new anticancer therapy, whichever comes first.

Duration of response (DOR) of tovorafenib monotherapy versus SoC chemotherapyUp to 60 months

DOR, defined as time from first imaging of tumor response per RANO-LGG, RANO-HGG or RAPNO criteria, as applicable, that was subsequently confirmed to radiographic PD or death from any cause, whichever comes first.

Trial Locations

Locations (121)

Perth Children's Hospital

🇦🇺

Nedlands, Australia

Women's and Children's Health Network

🇦🇺

North Adelaide, Australia

The Royal Children's Hospital - Children's Cancer Centre

🇦🇺

Parkville, Australia

Children's of Alabama

🇺🇸

Birmingham, Alabama, United States

Phoenix Children's Hospital

🇺🇸

Phoenix, Arizona, United States

Children's Hospital Los Angeles

🇺🇸

Los Angeles, California, United States

Children's Hospital of Orange County Main Campus - Orange

🇺🇸

Orange, California, United States

UCSF Benioff Children's Hospital

🇺🇸

San Francisco, California, United States

Children's Hospital Colorado

🇺🇸

Aurora, Colorado, United States

Connecticut Children's Medical Center

🇺🇸

Hartford, Connecticut, United States

Children's National Medical Center

🇺🇸

Washington, District of Columbia, United States

University of Florida Health

🇺🇸

Gainesville, Florida, United States

Arnold Palmer Hospital for Children

🇺🇸

Orlando, Florida, United States

Children's Healthcare of Atlanta

🇺🇸

Atlanta, Georgia, United States

Ann & Robert H. Lurie Children's Hospital of Chicago

🇺🇸

Chicago, Illinois, United States

Riley Hospital for Children at Indiana University Health

🇺🇸

Indianapolis, Indiana, United States

Maine Children's Cancer Program

🇺🇸

Scarborough, Maine, United States

Dana-Farber Cancer Institute

🇺🇸

Boston, Massachusetts, United States

University of Michigan - - C.S. Mott Children's Hospital

🇺🇸

Ann Arbor, Michigan, United States

Children's Minnesota

🇺🇸

Minneapolis, Minnesota, United States

St. Louis Children's Hospital

🇺🇸

Saint Louis, Missouri, United States

University of Nebraska Medical Center

🇺🇸

Omaha, Nebraska, United States

New York University Langone Health

🇺🇸

New York, New York, United States

University of Rochester

🇺🇸

Rochester, New York, United States

Duke Cancer Institute

🇺🇸

Durham, North Carolina, United States

Cleveland Clinic Main Campus

🇺🇸

Cleveland, Ohio, United States

University of Texas Southwestern Medical Center

🇺🇸

Dallas, Texas, United States

Texas Children's Hospital

🇺🇸

Houston, Texas, United States

Seattle Children's Hospital

🇺🇸

Seattle, Washington, United States

University of Wisconsin - Madison

🇺🇸

Madison, Wisconsin, United States

Children's Health Queensland Hospital and Health Service

🇦🇺

South Brisbane, Queensland, Australia

Sydney Children's Hospital - Randwick

🇦🇺

Randwick, Australia

Children's Hospital at Westmead

🇦🇺

Westmead, Australia

Medizinische Universität Innsbruck

🇦🇹

Innsbruck, Tirol, Austria

Medizinische Universität Wien

🇦🇹

Wien, Austria

Cliniques Universitaires Saint-Luc

🇧🇪

Brussel, Belgium

Universitair Ziekenhuis Gent

🇧🇪

Ghent, Belgium

Universitair Ziekenhuis Leuven - Campus Gasthuisberg

🇧🇪

Leuven, Belgium

Grupo de Apoio ao Adolescente e à Criança com Câncer (GRAACC)

🇧🇷

São Paulo, Brazil

Alberta Children's Hospital

🇨🇦

Calgary, Alberta, Canada

Stollery Children's Hospital

🇨🇦

Edmonton, Alberta, Canada

British Columbia Children's Hospital

🇨🇦

Vancouver, British Columbia, Canada

McMaster Children's Hospital

🇨🇦

Hamilton, Ontario, Canada

Children's Hospital of Eastern Ontario

🇨🇦

Ottawa, Ontario, Canada

CHU Sainte-Justine

🇨🇦

Montréal, Quebec, Canada

The Montreal Children's Hospital

🇨🇦

Montréal, Quebec, Canada

Centre Hospitalier de l'Université Laval et Centre Mère-Enfant Soleil

🇨🇦

Québec, Canada

SickKids - The Hospital for Sick Children

🇨🇦

Toronto, Canada

Fakultní Nemocnice Brno - D?tská Nemocnice

🇨🇿

Brno, Czechia

Motol University Hospital

🇨🇿

Prague, Czechia

Aarhus Universitetshospital

🇩🇰

Aarhus, Midtjylland, Denmark

Rigshospitalet

🇩🇰

Copenhagen, Denmark

Helsingin yliopistollinen sairaala (HUS)

🇫🇮

Helsinki, Finland

Tampereen Yliopistollinen Sairaala

🇫🇮

Tampere, Finland

Centre de Lutte contre le Cancer - Centre Oscar Lambret

🇫🇷

Lille, France

Centre Léon Bérard

🇫🇷

Lyon, France

Hôpital de la Timone

🇫🇷

Marseille, France

Institut Curie

🇫🇷

Paris, France

Gustave Roussy

🇫🇷

Villejuif, France

Universitätsklinikum Freiburg

🇩🇪

Freiburg, Baden-Württemberg, Germany

Universitätsklinikum Augsburg

🇩🇪

Augsburg, Bayern, Germany

Universitätsklinikum Erlangen

🇩🇪

Erlangen, Bayern, Germany

Universitätsklinikum Würzburg

🇩🇪

Würzburg, Bayern, Germany

Universitätsklinikum Frankfurt

🇩🇪

Frankfurt, Hessen, Germany

Medizinische Hochschule Hannover

🇩🇪

Hannover, Niedersachsen, Germany

Universitaetsklinikum Essen

🇩🇪

Essen, Nordrhein-Westfalen, Germany

Universitätsklinikum Leipzig

🇩🇪

Leipzig, Sachsen, Germany

Charité Universitätsmedizin Berlin

🇩🇪

Berlin, Germany

Evangelische Klinikum Bethel (EvKB)

🇩🇪

Bielefeld, Germany

Universitätsklinikum Hamburg-Eppendorf

🇩🇪

Hamburg, Germany

Universitätsklinikum Heidelberg

🇩🇪

Heidelberg, Germany

Universitätsklinikum Tübingen

🇩🇪

Tübingen, Germany

Aghia Sofia General Children's Hospital

🇬🇷

Athens, Greece

Athens General Children's Hospital

🇬🇷

Athens, Greece

Semmelweis Egyetem Tűzoltó utcai II. Sz. Gyermekgyógyászati Kliniká

🇭🇺

Budapest, Hungary

Children's Health Ireland at Crumlin

🇮🇪

Crumlin, Dublin, Ireland

Schneider Children's Medical Center of Israel

🇮🇱

Petah tikva, Israel

The Edmond and Lily Safra Children's Hospital

🇮🇱

Ramat Gan, Israel

Fondazione IRCCS - Istituto Nazionale dei Tumori

🇮🇹

Milano, Milan, Italy

Ospedale Pediatrico Bambino Gesù

🇮🇹

Roma, Rome, Italy

Ospedale Infantile Regina Margherita

🇮🇹

Torino, Turin, Italy

Azienda Universitaria Ospedaliera Consorziale - Policlinico di Bari

🇮🇹

Bari, Italy

Istituto Giannina Gaslini

🇮🇹

Genova, Italy

Azienda Ospedaliera di Rilievo Nazional Santobono Pausilipon

🇮🇹

Napoli, Italy

Azienda Ospedale Università di Padova

🇮🇹

Padova, Italy

Azienda Sanitaria Universitaria Friuli Centrale - P.O. Santa Maria della Misericordia

🇮🇹

Udine, Italy

King Hussein Cancer Foundation - King Hussein Cancer Center

🇯🇴

Amman, Muhafazat al-Asima, Jordan

Seoul National University Hospital

🇰🇷

Seoul, Korea, Republic of

Severance Hospital

🇰🇷

Seoul, Korea, Republic of

Prinses Maxima Centrum Kinderoncologie

🇳🇱

Utrecht, Netherlands

Starship Paediatric Blood & Cancer Center

🇳🇿

Grafton, New Zealand

Universitetssykehuset Nord-Norge - Tromsø

🇳🇴

Tromsø, Troms, Norway

Oslo Universitetssykehus

🇳🇴

Oslo, Norway

SingHealth Group - KK Women's and Children's Hospital

🇸🇬

Singapore, Singapore

Univerzitetni Klinini Center Ljubljana

🇸🇮

Ljubljana, Slovenia

Hospital Universitario Cruces

🇪🇸

Barakaldo, Spain

Hospital Universitari Vall d'Hebrón

🇪🇸

Barcelona, Spain

Hospital Sant Joan de Déu Barcelona

🇪🇸

Barcelona, Spain

Hospital Infantil Universitario Niño Jesús

🇪🇸

Madrid, Spain

Hospital Universitario La Paz

🇪🇸

Madrid, Spain

Hospital Universitario Virgen del Rocío

🇪🇸

Sevilla, Spain

Hospital Universitari i Politècnic La Fe

🇪🇸

Valencia, Spain

Drottning Silvias barn- och ungdomssjukhus

🇸🇪

Göteborg, Sweden

Skånes Universitetssjukhus - Lund

🇸🇪

Lund, Sweden

Astrid Lindgrens Barnsjukhus Solna

🇸🇪

Stockholm, Sweden

Centre Hospitalier Universitaire Vaudois Lausanne

🇨🇭

Lausanne, Switzerland

Universitaets - Kinderspital Zürich

🇨🇭

Zurich, Switzerland

Taipei Medical University Hospital

🇨🇳

Taipei, Taiwan

Chang Gung Memorial Hospital - Linkou Branch

🇨🇳

Taoyuan, Taiwan

Birmingham Women's and Children's NHS Foundation Trust

🇬🇧

Birmingham, England, United Kingdom

Leeds Teaching Hospital NHS Trust

🇬🇧

Leeds, England, United Kingdom

Alder Hey Children's NHS Foundation Trust

🇬🇧

Liverpool, England, United Kingdom

Manchester University NHS Foundation Trust

🇬🇧

Manchester, England, United Kingdom

The Newcastle Upon Tyne Hospitals NHS Foundation Trust

🇬🇧

Newcastle Upon Tyne, England, United Kingdom

Great Ormond Street Hospital for Children

🇬🇧

Oxford, England, United Kingdom

Royal Belfast Hospital for Sick Children

🇬🇧

Belfast, Northern Ireland, United Kingdom

NHS Greater Glasgow and Clyde

🇬🇧

Glasgow, Scotland, United Kingdom

Sheffield Children's Hospital

🇬🇧

Sheffield, South Yorkshire, United Kingdom

The Royal Marsden NHS Foundation Trust

🇬🇧

Sutton, Surrey, United Kingdom

University Hospitals Bristol and Weston NHS Foundation Trust

🇬🇧

Bristol, United Kingdom

Cambridge University Hospitals NHS Foundation Trust

🇬🇧

Cambridge, United Kingdom

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