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Front Line Ibrutinib Without Corticosteroids for Newly Diagnosed Chronic Graft-versus-Host Disease

Phase 2
Active, not recruiting
Conditions
Chronic GVHD
Interventions
Diagnostic Test: ECG
Diagnostic Test: PFT's
Diagnostic Test: CT
Drug: Steroid pulse (prednisone)
Drug: Beclomethasone
Other: Filgrastim
Other: Pegfilgrastim
Other: Erythropoietin
Other: Transfusions
Procedure: Oral/Skin biopsy
Registration Number
NCT04294641
Lead Sponsor
National Cancer Institute (NCI)
Brief Summary

Background:

- Chronic Graft Versus Host Disease (cGVHD) can occur after a person has had a stem cell or bone marrow transplant. In cGVHD, the donor cells attack the recipient's body. Researchers want to see if a drug called ibrutinib can block one of the proteins that lead to the immune reaction that causes cGVHD.

Objective:

- To see if ibrutinib as a first-line treatment can help people with newly diagnosed cGVHD.

Eligibility:

- People age 18 and older with newly diagnosed moderate or severe cGVHD

Design:

* Participants will be screened with:

* Medical and medicine histories

* Physical exam and vital signs

* Electrocardiograms (to measure heart function)

* Assessment of their ability to perform daily activities

* Blood and urine tests

* Assessment of their general well-being.

* Participants will visit the Clinical Center every 2 weeks for the first 2 months. Then they will visit every 4 weeks.

* Participants will take ibrutinib by mouth once every day of every cycle. One cycle is 28 days. Treatment will last up to 2 years. Participants will keep a medicine diary.

* Participants will take tests to measure lung function. They may have computed tomography scans of their chest. They will complete questionnaires about their symptoms and how cGVHD is affecting their body and quality of life. They will repeat the screening tests.

* Participants may have optional blood tests and/or skin biopsies to better understand the drugs effect on the body.

* Participants will be contacted by phone 30 days after treatment ends. They will also be contacted once a year for 2 years to discuss how they are feeling and if they have taken any other medicines to treat cGVHD.

Detailed Description

Background:

* Chronic graft-versus-host disease (GvHD) is the leading cause of late morbidity and non-relapse mortality following allogeneic hematopoietic stem cell transplantation (alloHSCT), occurring in 40-60% long-term survivors.

* Chronic GvHD occurs due to the dysfunctional peripheral tolerance during post-transplant hematopoietic reconstitution that allows the development and persistence of alloreactive donor-derived T and B cells.

* Prednisone is the front-line therapy; however, about 50% of participants have steroid-refractory disease and there is no standard second-line therapy.

* The most attractive approach for controlling chronic GvHD would be early therapy intervention which could prevent the most severe and irreversible clinical manifestations.

* Anti-B-cell therapy delivered early in chronic GvHD could be effective and steroid-sparing.

* Ibrutinib, reversible small molecule inhibitor of Brutons tyrosine kinase, has been shown to be well-tolerated and effective in phase 1b/2 trial for steroid refractory chronic GvHD.

Objective:

-To evaluate efficacy of ibrutinib as a first-line treatment for persons with newly diagnosed chronic GvHD by measuring the overall response rate (complete response \[CR\] + partial response \[PR\]) at 6 months, according to the 2014 National Institutes of Health (NIH) Consensus Criteria

Eligibility:

* Newly diagnosed, moderate or severe chronic GvHD according to the 2014 NIH Consensus Criteria, requiring systemic immunosuppression

* Age greater than or equal to 18 years old

* Karnofsky performance status greater than or equal to 60%

* History of prior alloHSCT; any donors, conditioning regimens and graft sources are allowed

* Adequate cardiac, hepatic and other organ function

* Adequate laboratory parameters

Design:

* Multi-center, non-randomized, phase II study

* Two-stage design will be used to determine the overall response rate (CR + PR) at 6 months

* Continuous daily dose of ibrutinib 420 mg by mouth, with the potential for dose reductions to 280 mg and 140 mg

* The accrual ceiling will be set at 40 participants, allowing for a total of up to 28 evaluable subjects.

Recruitment & Eligibility

Status
ACTIVE_NOT_RECRUITING
Sex
All
Target Recruitment
10
Inclusion Criteria

Not provided

Exclusion Criteria

Not provided

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
Ibrutinib Without CorticosteroidsIbrutinibDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsECGDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsPFT'sDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsCTDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsSteroid pulse (prednisone)Determine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsVoriconazoleDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsPosaconazoleDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsAzithromycinDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsMontelukastDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsBudesonideDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsBeclomethasoneDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsFilgrastimDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsPegfilgrastimDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsErythropoietinDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsTransfusionsDetermine response rate via continuous daily dose by mouth to determine efficacy
Ibrutinib Without CorticosteroidsOral/Skin biopsyDetermine response rate via continuous daily dose by mouth to determine efficacy
Primary Outcome Measures
NameTimeMethod
Fraction of Participants With an Overall Response Rate (Complete Response [CR] + Partial Response [PR]) Reported With an 80% Confidence Interval at 6 MonthsAt 6 months

To evaluate the efficacy of Ibrutinib as a first-line treatment for persons with newly diagnosed chronic graft-versus-host disease (GvHD) overall response rate was measured using the 2014 National Institutes of Health (NIH) consensus criteria and reported with an 80% confidence interval. CR is defined as complete resolution in all of signs and symptoms at all affected organs or tissues. PR is defined as improvement in ≥1 organ or tissue with no progression in any other affected organ or tissue.

Fraction of Participants With an Overall Response Rate (Complete Response [CR] + Partial Response [PR]) Reported With an 95% Confidence Interval at 6 MonthsAt 6 months

To evaluate the efficacy of Ibrutinib as a first-line treatment for persons with newly diagnosed chronic graft-versus-host disease (GvHD) overall response rate was measured using the 2014 National Institutes of Health (NIH) consensus criteria and reported with a 95% confidence interval. CR is defined as complete resolution in all of signs and symptoms at all affected organs or tissues. PR is defined as improvement in ≥1 organ or tissue with no progression in any other affected organ or tissue.

Secondary Outcome Measures
NameTimeMethod
Fraction of Grade 3 and Grade 4 Serious and/or Non-serious Adverse Events in Participants With Newly Diagnosed Chronic Graft-versus-host Disease (GvHD)Adverse events are captured from the first study intervention, Study Day 1 of Cycle 1 through 30 days after the participant received the last study drug administration.

Safety of the agent will be determined by the fraction of grade of 3 and 4 serious and non-serious adverse events assessed by the Common Terminology Criteria for Adverse Events (CTCAE v5.0). A non-serious adverse event is any untoward medical occurrence. A serious adverse event is an adverse event or suspected adverse reaction that results in death, a life-threatening adverse drug experience, hospitalization, disruption of the ability to conduct normal life functions, congenital anomaly/birth defect or important medical events that jeopardize the patient or subject and may require medical or surgical intervention to prevent one of the previous outcomes mentioned. Grade 3 is severe, and Grade 4 is life-threatening.

Failure-free Survival (FFS)Participants were followed from enrollment without death, relapse or new GVHD treatment up to 14 months

Time to event endpoint failure free survival will be determined using a Kaplan-Meier curve and confidence intervals is calculated using the Brookmeyer-Crowley method. Failure-free survival (FFS) is defined as survival (from enrollment) without death, relapse of the underlying malignancy, or the addition of a new systemic chronic graft-versus-host-disease (GVHD) treatment.

Fraction of Participants Alive at 24 Months Follow-up Post-treatment24 months

Survival will be determined using a Kaplan-Meier curve at 24 months.

Trial Locations

Locations (2)

National Institutes of Health Clinical Center

🇺🇸

Bethesda, Maryland, United States

Washington University, School of Medicine

🇺🇸

Saint Louis, Missouri, United States

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