MedPath

EMOTION & COGNITION in MYOCLONUS DYSTONIA (AGENT10-ECODYST)

Active, not recruiting
Conditions
DYT11
Myoclonus-Dystonia
Registration Number
NCT05671068
Lead Sponsor
Institut National de la Santé Et de la Recherche Médicale, France
Brief Summary

Background:

Myoclonus dystonia (DYT-SGCE) is characterized by myoclonus and dystonia. Such condition is associated with a high prevalence of psychiatric symptoms which are part of the phenotype. The mechanisms underlying these non-motor symptoms are still poorly understood.

Objective:

To investigate the neural correlates of cognition and emotion in DYT-SGCE.

Design:

Participants will have 1 - 2 visits at the clinical center. The total participation time is less than 24 hours.

Participants will have a medical interview and a neurological exam. They may give a urine sample before MRI.

Participants will have a short neuropsychologic and psychiatric interviews. Participants will have MRI scans. They will do small tasks or be asked to imagine things during the scanning.

Detailed Description

Eligibility:

DYT-SGCE patients and healthy volunteers (HV) between 15 and 60 years old.

Recruitment & Eligibility

Status
ACTIVE_NOT_RECRUITING
Sex
All
Target Recruitment
40
Inclusion Criteria

For all participants:

  • Age between 15-60 years
  • Able to give informed consent.

For patients:

  • An established diagnostic of DYT-SGCE
  • No change in medication (related to DYT-SGCE) for a month

For controls:

  • No neurological symptoms
  • No medication except oral contraception
Exclusion Criteria
  • No deprivation of liberty
  • Inability to give a consent
  • Established cognitive alteration
  • Contraindication to MRI (per MRI safety checklist)
  • Severe chronic psychiatric illness

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
BOLD signal derived from the functional magnetic resonance imaging46 month

Explore the differences in DYT-SGCE compared to HV

Secondary Outcome Measures
NameTimeMethod

Trial Locations

Locations (1)

Brain Institute

🇫🇷

Paris, France

© Copyright 2025. All Rights Reserved by MedPath