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Effect of Enzyme Replacement Therapy on Cardiac Function in Children With Gaucher Disease Type 3

Conditions
Gaucher Disease Type 3
Interventions
Diagnostic Test: echo
Registration Number
NCT06627543
Lead Sponsor
Noha Osman
Brief Summary

all cases confirmed diagnosis of Gaucher disease type 3 recieving enzyme replacement therapy at Assiut university hospital

Detailed Description

evaluate cardiac involvement in a group of GD type 3 patients, evaluate pulmonary hypertension and valvular involvement, compare the findings of basic echo before the start of replacement therapy as well as with healthy controls, to assess the effects of enzyme replacement therpay on the cardiac function.

Recruitment & Eligibility

Status
ENROLLING_BY_INVITATION
Sex
All
Target Recruitment
44
Inclusion Criteria
  • Any sex
  • No age limit
  • Gaucher disease type 3
  • Receiving enzyme replacement therapy
Exclusion Criteria
  • Age18 years old
  • Cases of gaucher type 1 and 2
  • Other lipid storage disease

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Arm && Interventions
GroupInterventionDescription
Gaucher type patientsecho-
Primary Outcome Measures
NameTimeMethod
Evaluate Pulmonary Hypertension (PH) in Egyptian GD Type 3 Patients6 months

To assess the presence and severity of pulmonary hypertension using echocardiography. Unit of Measure: mmHg (for systolic pulmonary artery pressure)

Evaluate Valvular Involvement in Egyptian GD Type 3 Patients6 months

To assess the degree of valvular involvement, including stenosis or regurgitation, using echocardiography. Unit of Measure: Severity grading (mild, moderate, severe)

Secondary Outcome Measures
NameTimeMethod

Trial Locations

Locations (1)

Ahmed Mohammed Mohammed

🇪🇬

Assiut, Egypt

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