The influence of the order of spirometry and multiple breath washout on the outcome in patients with cystic fibrosis an primary ciliary dyskinesia

Not Applicable

• Conditions: Q34; E84; Cystic fibrosis; Other congenital malformations of respiratory system

• Registration Number: DRKS00027473
• Lead Sponsor: Klinik für Kinder- und Jugendmedizin, Universitätsklinikum der Ruhr-Universität Bochum

Brief Summary

Not available

Detailed Description

Not available

Study Timeline

• Study Start: 2022-06-20
• Study Completion: 2022-10-13
• Last Update Posted: 19 August 2024

Recruitment & Eligibility

• Status: Complete
• Sex: All
• Target Recruitment: 53

Inclusion Criteria

Age >6 years
- genetically approved cystic fibrosis or approved PCD after ERS-criteria (min. PCD highly likely)
- regularly participation in the ambulance appointments in the CF- or PCD-consulting hours in the last 12 month with appointments every 3 month

Exclusion Criteria

- missing consent of the patients respectively their custody if underaged
- the custody does not speak German
- missing cooperation in the measurement procedure of the lung function diagnosis
- acute exacerbation/decrease two weeks before study inclusion
- regularly participation in the ambulance appointments every 3 month is not guarenteed

Study & Design

• Study Type: interventional
• Study Design: Not specified

Primary Outcome Measures

Name	Time	Method
Test results of the bodyplethysmography including the test results of spirometry including FEV1 in liter and z-score

Secondary Outcome Measures

Name	Time	Method
Test results of the multiple breath washout (LCI2,5%, satin, scond)