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A Real-World Study of Β-Thalassemia Major Treatment with Luspatercept in Taiwan

Recruiting
Conditions
β-Thalassemia Major
Interventions
Registration Number
NCT06596642
Lead Sponsor
Bristol-Myers Squibb
Brief Summary

This real-world study will assess the efficacy and safety of luspatercept treatment for β-thalassemia major in Taiwan as well as the impact on quality of life.

Detailed Description

Not available

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
90
Inclusion Criteria
  • Participants ≥18 years of age.
  • Participants with the diagnosis of transfusion-dependent β-thalassemia major who are eligible to the treatment of luspatercept.
  • Before luspatercept treatment, participant's transfusion burden ≥ 24 Red Blood Cell units in 24 weeks, without ≥35-day transfusion free.
Exclusion Criteria
  • Hypersensitivity to the active substance or to any of the excipients.
  • Pregnancy.
  • Participants requiring treatment to control the growth of extramedullary hematopoiesis (EMH) masses.

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Arm && Interventions
GroupInterventionDescription
Adults participants diagnosed with β-thalassemia majorLuspatercept-
Primary Outcome Measures
NameTimeMethod
Number of Red Blood Cell (RBC) transfusion units received by participantsBaseline, every 3 weeks thereafter until week 96
Participant hemoglobin (Hb) level resultsBaseline, every 3 weeks thereafter until week 96
Participant serum ferritin resultsBaseline, week 12, 24, 36, 48, 60, 72, 84 and 96
Secondary Outcome Measures
NameTimeMethod
Participant platelet level resultsBaseline, and every 3 weeks thereafter up to week 96
Participant white blood cell count resultsBaseline, and every 3 weeks thereafter up to week 96
Participant reticulocytes/normoblast count resultsBaseline, and weeks 12, 24, 36, 48, 60, 72, 84 and 96
Participant Hemoglobin F (HbF) levelsBaseline and weeks 6 and 12
Participant uric acid level resultsBaseline, and weeks 12, 24, 36, 48, 60, 72, 84 and 96
Participant lactate dehydrogenase (LDH) level resultsBaseline, and weeks 12, 24, 36, 48, 60, 72, 84 and 96
Participant aspartate aminotransferase (AST)/alanine aminotransferase (ALT) ratioBaseline, and weeks 12, 24, 36, 48, 60, 72, 84 and 96
Participant creatinine level resultsBaseline, and weeks 12, 24, 36, 48, 60, 72, 84 and 96
Participant bilirubin (total and direct) laboratory valuesBaseline, and weeks 12, 24, 36, 48, 60, 72, 84 and 96
Type of iron chelating therapy prescribed to participantsBaseline, every 3 weeks thereafter until week 96
Iron chelating therapy treatment dosage prescribed to participantsBaseline, every 3 weeks thereafter until week 96
Participant Adverse Events (AEs)Baseline and every 3 weeks until week 12, then weeks 24, 36, 48, 60, 72, 84 and 96
Participant health-related quality of life as assessed by Transfusion-dependent Quality of Life (TranQoL) questionnaireBaseline, week 12, 24, 48, 72 and 96
Participant health-related quality of life as assessed by EQ-5D-5L questionnaireBaseline, week 12, 24, 48, 72 and 96
Luspatercept treatment dosage prescribed to participantsBaseline, every 3 weeks thereafter until week 96
Duration of luspatercept treatmentBaseline, every 3 weeks thereafter until week 96
Participant reason(s) for luspatercept treatment discontinuation as assessed by the treating clinicianBaseline, every 3 weeks thereafter until week 96
Participant demographicsBaseline
Participant weightBaseline
Participant β0/β0 genotype statusBaseline
Participant disease statusBaseline
Participant comorbiditiesBaseline
Participant concomitant medicationBaseline
Participant β-thalassemia treatment historyBaseline
Participant surgical history (splenectomy and/or cholecystectomy)Baseline

Trial Locations

Locations (5)

Kaohsiung Medical University Chung-Ho Memorial Hospital

🇨🇳

Kaohsiung, Taiwan

National Cheng Kung University Hospital

🇨🇳

Tainan, Taiwan

MacKay Memorial Hospital

🇨🇳

Taipei, Taiwan

Chang Gung Memorial Hospital, Linkou

🇨🇳

Taoyuan, Taiwan

National Taiwan University Hospital

🇨🇳

Taipei, Taiwan

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