MedPath

A Study of Daratumumab-Based Therapies in Participants With Amyloid Light Chain (AL) Amyloidosis

Phase 2
Recruiting
Conditions
Amyloidosis
Interventions
Registration Number
NCT05250973
Lead Sponsor
Janssen Research & Development, LLC
Brief Summary

The purpose of this study is to characterize cardiac safety of Daratumumab, Cyclophosphamide, Bortezomib, and Dexamethasone (D-VCd) treatment regimens (Arm A: daratumumab + immediate VCd treatment and Arm B: daratumumab + deferred VCd) in newly diagnosed systemic amyloid light chain (AL) amyloidosis with cardiac involvement and to identify potential mitigation strategies for cardiac toxicity (cohort 1); to characterize the pharmacokinetics of subcutaneous (SC) daratumumab, among racial and ethnic minorities, including Black or African American, with newly diagnosed AL amyloidosis treated with D-VCd (cohort 2).

Detailed Description

Not available

Recruitment & Eligibility

Status
RECRUITING
Sex
All
Target Recruitment
150
Inclusion Criteria
  • Cohort 1: Cardiac involvement (amyloid light chain [AL] amyloidosis Mayo Cardiac Stage II and Stage IIIa) with or without other organ(s) involved; Cohort 2: One or more organs impacted by systemic AL amyloidosis according to consensus guidelines
  • Eastern Cooperative Oncology Group (ECOG) Performance Status score of 0, 1 or 2
  • A female participant of childbearing potential must have a negative serum or urine test at screening and within 72 hours of the first dose of study treatment and must agree to further serum or urine pregnancy tests during the study
  • A male participant must agree not to donate sperm for the purpose of reproduction during the study and for a minimum of 6 months after receiving the last dose of cyclophosphamide or 100 days after discontinuation of daratumumab, whichever is longer
  • Cohort 2 only: self-identified racial and ethnic minorities, including Black or African American
  • Measurable disease at screening defined by one of the following:

Difference between iFLC and uninvolved FLC (dFLC) >= 40mg/L per central laboratory Serum involved free light chain (iFLC) >= 40 mg/L with an abnormal kappa:lambda ratio Serum M-protein >= 0.5 g/dL

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Exclusion Criteria
  • Prior therapy for systemic AL amyloidosis or multiple myeloma including medications that target cluster of differentiation 38 (CD38), with the exception of 160 milligrams(mg) dexamethasone or equivalent corticosteroid maximum exposure prior to randomization/enrollment

  • Previous or current diagnosis of symptomatic multiple myeloma, including the presence of lytic bone disease, plasmacytomas, >=60% plasma cells in the bone marrow, or hypercalcemia related to myeloma.

  • Participant received any of the following therapies:

    1. treatment with an investigational drug or used an invasive investigational medical device within 14 days or at least 5 half-lives, whichever is less;
    2. vaccinated with an investigational vaccine (except for COVID-19) live, attenuated or replicating viral vector vaccines less than (<) 4 weeks prior to randomization/enrollment. Participants who are taking strong Cytochrome P450 3A4(CYP3A4) inducers must discontinue their use at least 5 half-lives prior to the first dose of bortezomib
  • Stem cell transplantation -Planned stem cell transplant during the first 9 cycles of protocol therapy are excluded. Stem cell collection during the first 9 cycles of protocol therapy is permitted

  • Grade 2 sensory or Grade 1 painful peripheral neuropathy

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Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Cohort1 (Arm A): Daratumumab + Immediate Cyclophosphamide, Bortezomib and Dexamethasone (VCd)DaratumumabParticipants with newly diagnosed systemic amyloid light chain (AL) amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive daratumumab 1800 milligrams (mg) subcutaneously (SC) starting on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Cohort1 (Arm A): Daratumumab + Immediate Cyclophosphamide, Bortezomib and Dexamethasone (VCd)CyclophosphamideParticipants with newly diagnosed systemic amyloid light chain (AL) amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive daratumumab 1800 milligrams (mg) subcutaneously (SC) starting on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Cohort1 (Arm A): Daratumumab + Immediate Cyclophosphamide, Bortezomib and Dexamethasone (VCd)BortezomibParticipants with newly diagnosed systemic amyloid light chain (AL) amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive daratumumab 1800 milligrams (mg) subcutaneously (SC) starting on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Cohort1 (Arm A): Daratumumab + Immediate Cyclophosphamide, Bortezomib and Dexamethasone (VCd)DexamethasoneParticipants with newly diagnosed systemic amyloid light chain (AL) amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive daratumumab 1800 milligrams (mg) subcutaneously (SC) starting on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Cohort1 (Arm B): Daratumumab + Deferred VCdDaratumumabParticipants with newly diagnosed systemic AL amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive SC daratumumab 1800mg on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (Cyclophosphamide 300 mg/m\^2 either orally or IV, Bortezomib 1.3 mg/m\^2 SC or IV, Dexamethasone 40 mg weekly either orally or IV) starting at Cycle 4 Day 1, weekly (Days 1, 8, 15, 22) in every 28-day cycle for a maximum of 6 cycles (Cycle 9 Day 22).
Cohort1 (Arm B): Daratumumab + Deferred VCdCyclophosphamideParticipants with newly diagnosed systemic AL amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive SC daratumumab 1800mg on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (Cyclophosphamide 300 mg/m\^2 either orally or IV, Bortezomib 1.3 mg/m\^2 SC or IV, Dexamethasone 40 mg weekly either orally or IV) starting at Cycle 4 Day 1, weekly (Days 1, 8, 15, 22) in every 28-day cycle for a maximum of 6 cycles (Cycle 9 Day 22).
Cohort1 (Arm B): Daratumumab + Deferred VCdBortezomibParticipants with newly diagnosed systemic AL amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive SC daratumumab 1800mg on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (Cyclophosphamide 300 mg/m\^2 either orally or IV, Bortezomib 1.3 mg/m\^2 SC or IV, Dexamethasone 40 mg weekly either orally or IV) starting at Cycle 4 Day 1, weekly (Days 1, 8, 15, 22) in every 28-day cycle for a maximum of 6 cycles (Cycle 9 Day 22).
Cohort1 (Arm B): Daratumumab + Deferred VCdDexamethasoneParticipants with newly diagnosed systemic AL amyloidosis with Mayo Cardiac Stage II and IIIa cardiac involvement will receive SC daratumumab 1800mg on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (Cyclophosphamide 300 mg/m\^2 either orally or IV, Bortezomib 1.3 mg/m\^2 SC or IV, Dexamethasone 40 mg weekly either orally or IV) starting at Cycle 4 Day 1, weekly (Days 1, 8, 15, 22) in every 28-day cycle for a maximum of 6 cycles (Cycle 9 Day 22).
Cohort 2: Daratumumab + VCdDaratumumabParticipants with racial and ethnic minorities, including Black or African American participants, with newly diagnosed AL amyloidosis will receive SC injection of daratumumab 1800 mg SC on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Cohort 2: Daratumumab + VCdCyclophosphamideParticipants with racial and ethnic minorities, including Black or African American participants, with newly diagnosed AL amyloidosis will receive SC injection of daratumumab 1800 mg SC on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Cohort 2: Daratumumab + VCdBortezomibParticipants with racial and ethnic minorities, including Black or African American participants, with newly diagnosed AL amyloidosis will receive SC injection of daratumumab 1800 mg SC on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Cohort 2: Daratumumab + VCdDexamethasoneParticipants with racial and ethnic minorities, including Black or African American participants, with newly diagnosed AL amyloidosis will receive SC injection of daratumumab 1800 mg SC on Day 1 once weekly (q1w) up to Day 22 for cycles 1-2, on Days 1 and 15 for cycles 3-6, and on Day 1 for cycles 7-24 of a 28-day cycle. Participants will also receive VCd (cyclophosphamide 300 milligrams per meter square \[mg/m\^2\] either orally or intravenously \[IV\], bortezomib 1.3 mg/m\^2 SC or IV, dexamethasone 40 mg weekly either orally or IV) weekly starting at Cycle 1 Day 1 up to Day 22 in every 28-day cycle for a maximum of 6 cycles (Cycle 6 Day 22).
Primary Outcome Measures
NameTimeMethod
Number of Participants with Cardiac Events of Any Toxicity GradeUp to 12 months

Number of participants with cardiac events of any toxicity grade will be reported.

Observed Concentration Immediately Prior to the Next Study Treatment Administration (Ctrough) of DaratumumabCycle 3 Day 1 predose (each cycle is of 28 days)

Ctrough is defined as the observed concentration immediately prior to the next study treatment administration.

Secondary Outcome Measures
NameTimeMethod
Overall Complete Hematologic Response (HemCR) RateUp to Cycle 12 or Month 12 (whichever occurs later)

Overall HemCR rate is defined as percentage of participants who achieve HemCR during or after the study treatment.

HemCR RateAt 6 months

HemCR rate at 6 month is defined as percentage of participants who achieve HemCR at 6 month during or after the study treatment.

Very Good Partial Response (VGPR) or Better RateUp to Cycle 12 or Month 12 (whichever occurs later)

Hematologic greater than or equal to (\>=) VGPR rate is defined as percentage of participants who achieve hematologic response of VGPR or better.

Time to HemCR or (VGPR or Better)Up to Cycle 12 or Month 12 (whichever occurs later)

For participants who achieve HemCR (or \>=VGPR), time to HemCR (or \>=VGPR) is defined as the time between the date of first study treatment and the first efficacy evaluation at which the participant has met all criteria for hematologic complete response (CR) (or \>=VGPR).

Duration of Response (HemCR and VGPR or Better)Up to Cycle 12 or Month 12 (whichever occurs later)

For participants who achieve HemCR (or \>=VGPR), duration of HemCR (or \>=VGPR) is defined as the time between the date of initial documentation of HemCR (or \>=VGPR) to the date of first documented evidence of hematologic progressive disease or death, whichever comes first.

Organ Response Rate (OrRR)Up to Cycle 12 or Month 12 (whichever occurs later)

Organ response rate is defined as the percentage of participants who achieve organ response in each corresponding organ (kidney, heart, liver).

Overall Survival (OS)Until Cycle 12 or Month 12 (whichever occurs later)

OS is measured from the date of first study treatment to the date of the participant's death.

Time to Subsequent TherapyUp to Cycle 12 or Month 12 (whichever occurs later)

Time to subsequent therapy for amyloid light chain (AL) amyloidosis is defined as the time from the date of first study treatment to the start date of subsequent AL amyloidosis (non-protocol) treatment.

Number of Participants with Adverse Events (AEs) by SeverityUp to Cycle 12 or Month 12 (whichever occurs later)

Number of participants with AEs by severity will be reported. An AE is any untoward medical occurrence in a participant participating in a clinical study that does not necessarily have a causal relationship with the pharmaceutical/ biological agent under study.

Serum Concentration of DaratumumabUp to 3 years

Serum samples will be analyzed to determine concentrations of daratumumab.

Number of Participants with Antibodies to DaratumumabUp to Cycle 12 or Month 12 (whichever occurs later)

Number of participants with antibodies to daratumumab will be reported.

Number of Participants with Antibodies to Recombinant Human Hyaluronidase PH20 Enzyme (rHuPH20)Up to Cycle 12 or Month 12 (whichever occurs later)

Number of participants with antibodies to rHuPH20 will be reported.

Change from Baseline in Clinical Signs and Symptoms Score of Cardiac AL AmyloidosisUp to Cycle 12 or Month 12 (whichever occurs later)

Change from baseline in clinical signs and symptoms score of cardiac AL amyloidosis will be reported.

Trial Locations

Locations (45)

West Penn Hospital

🇺🇸

Pittsburgh, Pennsylvania, United States

University of Washington

🇺🇸

Seattle, Washington, United States

University College Hospital

🇬🇧

London, United Kingdom

Hosp Clinico Univ de Salamanca

🇪🇸

Salamanca, Spain

Leicester Royal Infirmary - Haematology

🇬🇧

Leicester, United Kingdom

Clinica Univ. de Navarra

🇪🇸

Pamplona, Spain

West China Hospital Si Chuan University

🇨🇳

Chengdu, China

UMC Utrecht

🇳🇱

Utrecht, Netherlands

Hospital Maastricht University Medical Center

🇳🇱

Maastricht, Netherlands

Barbara Ann Karmanos Cancer Institute

🇺🇸

Detroit, Michigan, United States

Moffitt Cancer Center

🇺🇸

Tampa, Florida, United States

Winship Cancer Institute Emory University

🇺🇸

Atlanta, Georgia, United States

Tufts Medical Center

🇺🇸

Boston, Massachusetts, United States

Levine Cancer Institute

🇺🇸

Charlotte, North Carolina, United States

University Hospital of Cleveland

🇺🇸

Cleveland, Ohio, United States

UT Southwestern Medical Center

🇺🇸

Dallas, Texas, United States

Ohio Health Research Institute

🇺🇸

Columbus, Ohio, United States

VCU Medical Center

🇺🇸

Richmond, Virginia, United States

Cross Cancer Institute

🇨🇦

Edmonton, Alberta, Canada

University Health Network UHN Princess Margaret Cancer Centre

🇨🇦

Toronto, Ontario, Canada

Peking University First Hospital

🇨🇳

Beijing, China

Peking University People s Hospital

🇨🇳

Beijing, China

First affiliated Hospital of Zhejiang University

🇨🇳

Hangzhou, China

Ruijin Hospital Shanghai Jiao Tong University

🇨🇳

Shanghai, China

CHU de Limoges

🇫🇷

Limoges Cedex, France

Centre hospitalier Lyon-Sud

🇫🇷

Pierre Benite cedex, France

CHU De Poitiers

🇫🇷

Poitiers, France

CHU Rangueil

🇫🇷

Toulouse, France

Universitatsklinikum Essen

🇩🇪

Essen, Germany

Charite Campus Benjamin Franklin

🇩🇪

Berlin, Germany

Alexandra General Hospital of Athens

🇬🇷

Athens, Greece

Universitaetsklinikum Heidelberg Medizinische Klinik V

🇩🇪

Heidelberg, Germany

Università Degli Studi Di Napoli Federico Ii

🇮🇹

Napoli, Italy

Fondazione IRCCS Policlinico San Matteo

🇮🇹

Pavia, Italy

DIPARTIMENTO DI BIOTECNOLOGIE CELLULARI ED EMATOLOGIA - UNIVERSITà ''LA SAPIENZA''

🇮🇹

Roma, Italy

University Medical Center Groningen

🇳🇱

Groningen, Netherlands

Hosp Univ Vall D Hebron

🇪🇸

Barcelona, Spain

Hosp. Univ. Germans Trias I Pujol

🇪🇸

Badalona, Spain

Boston University Medical Center

🇺🇸

Boston, Massachusetts, United States

Hosp Clinic de Barcelona

🇪🇸

Barcelona, Spain

City of Hope

🇺🇸

Duarte, California, United States

Smilow Cancer Hospital/Yale Cancer Center

🇺🇸

New Haven, Connecticut, United States

Memorial Sloan Kettering

🇺🇸

New York, New York, United States

Tom Baker Cancer Center

🇨🇦

Calgary, Alberta, Canada

Wake Forest University - Baptist Medical Center

🇺🇸

Winston-Salem, North Carolina, United States

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