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Trial in Locally Advanced and Metastatic Adrenocortical Carcinoma Treatment (FIRM-ACT)

Phase 3
Completed
Conditions
Carcinoma, Adrenal Cortical
Interventions
Registration Number
NCT00094497
Lead Sponsor
Collaborative Group for Adrenocortical Carcinoma Treatment
Brief Summary

The purpose of this study is to determine whether treatment with etoposide, doxorubicin, cisplatin and mitotane (EDP/M) prolongs survival as compared to streptozotocin and mitotane (Sz/M) in patients with advanced adrenocortical carcinoma (ACC) whose disease is not amenable to complete surgical resection.

Detailed Description

The Firm-ACT trial is the first ever conducted randomized controlled phase III trial in adrenocortical carcinoma (ACC), a rare malignancy with poor prognosis. It will provide results leading to the establishment of an urgently needed gold standard chemotherapy regimen for patients with locally advanced or metastatic ACC. To this end the trial compares the two most promising drug combinations investigated in phase II trials, considered by the "International Consensus Conference on Adrenal Cancer" (Ann Arbor/USA, 2003) as valuable first line treatments for advanced ACC. The first regimen consists of etoposide, doxorubicin, cisplatin plus mitotane (EDP-M), the second regiment employs streptozotocin plus mitotane (Sz-M). Over a period of five years this international trial will include 300 patients with advanced ACC from different European countries. Blood mitotane concentrations will be monitored, aiming at drug levels between 14 - 20 mg/L. Patients not responding to the first line treatment will be switched to the alternative regimen. The primary objective of this trial is to investigate whether EDP-M given as first line treatment will prolong survival as compared to Sz-M. Secondary endpoints are quality of life, time to progression, best overall response rate and duration of response. In addition, the trial evaluates the role of reaching therapeutic mitotane serum concentrations for survival and tumour response and assesses the value of the two alternative treatment regimens as second line therapy in advanced ACC. Moreover, the FIRM-ACT trial will generate a lasting structural basis for successful future trials in ACC.

In a substudy of 40 patients a detailed analysis of the pharmacokinetics of oral mitotane will be analysed. Two different mitotane treatment regimens ("low dose" vs. "high dose") will be compared.

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
304
Inclusion Criteria
  • Histologically confirmed diagnosis of adrenocortical carcinoma
  • Locally advanced or metastatic disease not amenable to radical surgery resection (Stage III-IV)
  • Radiologically monitorable disease
  • ECOG performance status 0-2
  • Life expectancy > 3 months
  • Age ≥18 years
  • Adequate bone marrow reserve (neutrophils > 1500/mm3 and platelets > 100,000/mm3)
  • Effective contraception in pre-menopausal female and male patients
  • Patient's written informed consent
  • Ability to comply with the protocol procedures (including availability for follow-up visits)
  • Previous palliative surgery, radiotherapy or radiofrequency ablation is acceptable as long as radiologically monitorable disease is verifiable afterwards.
Exclusion Criteria
  • History of prior malignancy, except for cured non-melanoma skin cancer, curatively in situ cervical carcinoma, or other cancers treated with no evidence of disease for at least five years.
  • Previous cytotoxic chemotherapy for adrenocortical carcinoma
  • Renal insufficiency (serum creatinine ≥2 mg/dl or creatinine clearance ≤ 50 ml/min)
  • Hepatic insufficiency (serum bilirubin ≥2 x the institutional upper limit of normal range and/or serum transaminases ≥ 3 x the institutional upper limit of normal range; exception: in patients on mitotane, transaminase levels up to 5 x the institutional upper limit of normal range are acceptable)
  • Pregnancy or breast feeding
  • Known hypersensitivity to any drug included in the treatment protocol
  • Presence of active infection
  • Any other severe clinical condition that in the judgment of the local investigator would place the patient at undue risk or interfere with the study completion
  • Decompensated heart failure (ejection fraction <50%), myocardial infarction or revascularization procedure during the last 6 months, unstable angina pectoris, and uncontrolled cardiac arrhythmia
  • Current treatment with other experimental drugs and/or previous participation in clinical trials with other experimental agents for adrenocortical carcinoma
  • Prisoners

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Sz-MStreptozotocinstreptozotocin and mitotane
Sz-MMitotanestreptozotocin and mitotane
EDP-MEtoposideetopodide, doxorubicin, cisplatin and mitotane
EDP-MDoxorubicinetopodide, doxorubicin, cisplatin and mitotane
EDP-MCisplatinetopodide, doxorubicin, cisplatin and mitotane
EDP-MMitotaneetopodide, doxorubicin, cisplatin and mitotane
Primary Outcome Measures
NameTimeMethod
Overall Survivalevery 8 weeks until death up to 5 years

participants who died among those randomized to first-line therapy

Secondary Outcome Measures
NameTimeMethod
Best Overall Response Rateevery 8 weeks up to 5 years

RECIST 1.0 was used to evaluate response

Number of Disease-free Patientsevery 8 weeks until progression (up to 5 years)

complete response or disease-free by time of surgery

Change in Quality of Life as Measured by QLQ-C30baseline and 8 weeks

scale ranged from 0 to 100 with higher score meaning greater quality of life

Progression-free Survivalevery 8 weeks until progression or death up to 5 years

Trial Locations

Locations (32)

National Cancer Institute - Center for Cancer Research

🇺🇸

Bethesda, Maryland, United States

University of Michigan, Department of Internal Medicine

🇺🇸

Ann Arbor, Michigan, United States

Royal Adelaide Hospital

🇦🇺

Adelaide, Australia

University of Graz

🇦🇹

Graz, Austria

Institut Gustave Roussy

🇫🇷

Villejuif, France

Hospital Bordeaux haut leveque

🇫🇷

Pessac, France

Endokrinologie Medizinische Hochschule Hannover

🇩🇪

Hannover, Germany

Charité-Universitätsmedizin Berlin - Campus Mitte

🇩🇪

Berlin, Germany

Dept. of Medicine III

🇩🇪

Dresden, Germany

Dept of Medicine I

🇩🇪

Mainz, Germany

University of Duesseldorf, Dept. of Endocrrinology

🇩🇪

Duesseldorf, Germany

University of Wuerzburg - Dept. of Medicine

🇩🇪

Wuerzburg, Germany

Academisch Medisch Centrum; Dept. of Endocrinology

🇳🇱

Amsterdam, Netherlands

Maxima Medisch Centrum; Dept. of Internal Medicine

🇳🇱

Eindhoven, Netherlands

University of Turin, Dept of Internal Medicine

🇮🇹

Orbassano, Italy

Clinica Endocrinologica, Università di Padova, Azienda Ospedaliera di Padova

🇮🇹

Padova, Italy

Vrije Universiteit Medisch Centrum

🇳🇱

Amsterdam, Netherlands

Department of Oncology, Sahlgrenska University Hospital

🇸🇪

Gothenburg, Sweden

University Hospital Groningen; Dept. of Internal Medine

🇳🇱

Groningen, Netherlands

Leiden University Medical Center

🇳🇱

Leiden, Netherlands

Department of Oncology, Linköping University Hospital

🇸🇪

Linköping, Sweden

Department of Medicine, The Jubileum Institute, Lund University

🇸🇪

Lund, Sweden

Dept of Surgery, Karolinska Hospital, Stockholm

🇸🇪

Stockholm, Sweden

Uppsala University Hospital - Dept of Medical Sciences

🇸🇪

Uppsala, Sweden

Clinique Marc Linquette

🇫🇷

Lille, France

Centre Leon Berard

🇫🇷

Lyon, France

Cochin Hospital

🇫🇷

Paris, France

Hospital de Marseille la timone

🇫🇷

Marseille, France

Zentrum für Innere Medizin - Endokrinologie des Universitätsklinikum Essen

🇩🇪

Essen, Germany

University of Munich, Dept. of Internal Medicine (Innenstadt)

🇩🇪

Munich, Germany

Otto-von-Guericke University; Dept. of Endocrinology

🇩🇪

Magdeburg, Germany

Charité-University, Dept. of Endocrinology; Campus Benjamin Franklin

🇩🇪

Berlin, Germany

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