Indication and outcome of hematopoietic stem cell transplantation in primary immunodeficiency with predominant hypogammaglobulinemia – a retrospective study
- Conditions
- D80.9D83.9Z94.81Z94.80Immunodeficiency with predominantly antibody defects, unspecifiedCommon variable immunodeficiency, unspecified
- Registration Number
- DRKS00004296
- Lead Sponsor
- Centrum für Chronische Immundefizienz (CCI), Universitätsklinikum Freiburg
- Brief Summary
Not available
- Detailed Description
Not available
Recruitment & Eligibility
- Status
- Complete
- Sex
- All
- Target Recruitment
- 31
Inclusion Criteria
adult patients with primary immunodeficiency with predominant antibody deficiency having undergone allogeneic hematopoietic stem cell transplantation before 1st january 2013
Exclusion Criteria
age under 2 at transplantation, no informed consent to data collection
Study & Design
- Study Type
- observational
- Study Design
- Not specified
- Primary Outcome Measures
Name Time Method umber of adult PAD patients undergoing HSCT for any reason in cooperating centers worldwide.
- Secondary Outcome Measures
Name Time Method immune reconstitution, mortality, morbidity after HSCT