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Indication and outcome of hematopoietic stem cell transplantation in primary immunodeficiency with predominant hypogammaglobulinemia – a retrospective study

Conditions
D80.9
D83.9
Z94.81
Z94.80
Immunodeficiency with predominantly antibody defects, unspecified
Common variable immunodeficiency, unspecified
Registration Number
DRKS00004296
Lead Sponsor
Centrum für Chronische Immundefizienz (CCI), Universitätsklinikum Freiburg
Brief Summary

Not available

Detailed Description

Not available

Recruitment & Eligibility

Status
Complete
Sex
All
Target Recruitment
31
Inclusion Criteria

adult patients with primary immunodeficiency with predominant antibody deficiency having undergone allogeneic hematopoietic stem cell transplantation before 1st january 2013

Exclusion Criteria

age under 2 at transplantation, no informed consent to data collection

Study & Design

Study Type
observational
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
umber of adult PAD patients undergoing HSCT for any reason in cooperating centers worldwide.
Secondary Outcome Measures
NameTimeMethod
immune reconstitution, mortality, morbidity after HSCT
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