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REgiStry Of the NAtural History of recurreNt periCarditis in pEdiatric and Adult Patients

Active, not recruiting
Conditions
Recurrent Pericarditis
Registration Number
NCT04687358
Lead Sponsor
Kiniksa Pharmaceuticals International, plc
Brief Summary

The registry will focus on furthering the understanding of the natural history of recurrent pericarditis (RP), as well as document RP-related clinical, health-related quality of life (HRQoL), and economic burden and will assist the medical community to refine or develop data-driven recommendations for clinical management of RP patients to optimize clinical outcomes. It also aims to generate data in support of the impact of rilonacept on clinical outcomes in a real-world population.

Detailed Description

Not available

Recruitment & Eligibility

Status
ACTIVE_NOT_RECRUITING
Sex
All
Target Recruitment
500
Inclusion Criteria
  • Physician-confirmed (or confirmation in medical records) diagnosis of RP defined as an initial, acute, episode and at least one pericarditis recurrence after the initial acute episode
  • Experienced at least one pericarditis episode in the 3 years prior to inclusion
  • Under the care of a physician for the treatment and management of RP
  • Currently prescribed medication for RP

Select

Exclusion Criteria
  • Diagnosis of pericarditis secondary to tuberculosis (TB), cancer if not in full remission, post thoracic blunt trauma (e.g., motor-vehicle accidents), myocarditis, systemic autoimmune diseases, except SJIA and adult Still's disease, HIV
  • Appears to have an impairment (e.g., cognitive, hearing, visual) or insufficient English or Spanish proficiency that could interfere with ability to complete patient-completed assessments
  • Currently enrolled in a therapeutic investigational drug or device study

INACTIVE RP PATIENTS

Select Inclusion Criteria:

  • Physician-confirmed (or confirmation in medical records) diagnosis of RP defined as an initial, acute, episode and at least one pericarditis recurrence after the initial, acute episode
  • Patient had a last episode occurring at least 3 years and up to 5 years before registry inclusion
  • Resolution of RP symptoms confirmed with no further RP treatment for 3 years prior to registry enrollment

Select Exclusion Criteria:

  • Experienced a pericarditis episode within 3 years from enrolling in the registry
  • Currently receiving RP treatment prescribed by a treating physician (e.g., CS, colchicine)
  • Diagnosis of pericarditis secondary to tuberculosis (TB), cancer if not in full remission, post thoracic blunt trauma (e.g., motor-vehicle accidents), myocarditis, systemic autoimmune diseases except SJIA and adult Still's disease, HIV
  • Enrolled in a therapeutic investigational clinical trial during the observation period

Study & Design

Study Type
OBSERVATIONAL
Study Design
Not specified
Primary Outcome Measures
NameTimeMethod
Patients using 1 or more RP treatments5 years

Proportion of patients using 1, 2, 3, or more concomitant RP treatments

Secondary Outcome Measures
NameTimeMethod
Adverse event rate5 years

Rate of adverse events reported by PC treatment

Change in cardiac magnetic resonance imaging (cMRI)5 years

Change from baseline in cMRI

Change in echocardiogram5 years

Change from baseline in echocardiogram

Change in fever5 years

Change from baseline in fever

Change in Multidetector (cardiac) computed tomography (MDCT)5 years

Change from baseline in MDCT

Change in C-reactive protein (CRP)5 years

Change from baseline in CRP

Change in interleukin-1 (IL-1)5 years

Change from baseline in IL-1

Change in chest x-ray5 years

Change from baseline in chest x-ray

Changes in Patient Global Impression of Pericarditis Severity (PGIPS) patient-reported outcomes5 years

Change from baseline in PGIPS

Change in dyspnea5 years

Change from baseline in dyspnea

Change in interleukin-6 (IL-6)5 years

Change from baseline in IL-6

Change in cardiovascular magnetic resonance (CMR) imaging5 years

Change from baseline in CMR

Changes in PROMIS-29 patient-reported outcomes5 years

Change from baseline in PROMIS-29

Changes in PROMIS Pediatric/Parent 25 patient-reported outcomes5 years

Change from baseline in PROMIS Pediatric/Parent 25

Changes in insomnia severity index (ISI) patient-reported outcomes5 years

Change from baseline in ISI

Most frequently used RP treatments5 years

Number of subjects who used each treatment recorded during the study

Reduction in the use of corticosteroids5 years

Change from baseline through end of observation in corticosteroid use

Change in RP activity1 year

Change from baseline in RP disease recurrences within 1 year (from 1 year prior to baseline to 1 year after baseline

Change in pericardial rub5 years

Change from baseline in pericardial rub

Change in pericardial effusion5 years

Change from baseline in pericardial effusion

Change in erythrocyte sedimentation rate (ESR)5 years

Change from baseline in ESR

Change in white blood count (WBC)5 years

Change from baseline in WBC

Change in electrocardiogram (ECG)5 years

Change from baseline in ST-, PR-, QRS- and QT- intervals

Changes in persistent pericarditis numerical rating scale (PPNRS) patient-reported outcomes5 years

Change from baseline in PPNRS

Changes in D12 patient-reported outcomes5 years

Change from baseline in D12 outcome measures

Trial Locations

Locations (29)

Houston Methodist Hospital

🇺🇸

Houston, Texas, United States

Alaska Heart & Vascular Institute

🇺🇸

Anchorage, Alaska, United States

Pima Heart and Vascular

🇺🇸

Tucson, Arizona, United States

University of California San Diego Medical Center

🇺🇸

La Jolla, California, United States

Cedars-Sinai Medical Center

🇺🇸

Los Angeles, California, United States

Scripps Health

🇺🇸

San Diego, California, United States

Northwestern University

🇺🇸

Chicago, Illinois, United States

Midwest Cardiovascular Research Foundation

🇺🇸

Davenport, Iowa, United States

Johns Hopkins University

🇺🇸

Baltimore, Maryland, United States

Massachusetts General Hospital

🇺🇸

Boston, Massachusetts, United States

Brigham and Women's Hospital

🇺🇸

Boston, Massachusetts, United States

Detroit Medical Center

🇺🇸

Detroit, Michigan, United States

Minneapolis Heart Institute Foundation

🇺🇸

Minneapolis, Minnesota, United States

Mayo Clinic - PPDS

🇺🇸

Rochester, Minnesota, United States

Barnes-Jewish Hospital/Washington University

🇺🇸

Saint Louis, Missouri, United States

University of Nebraska

🇺🇸

Omaha, Nebraska, United States

TKL Research Inc.

🇺🇸

Fair Lawn, New Jersey, United States

NYU Langone Health

🇺🇸

New York, New York, United States

Northwell Health - Lenox Hill Hospital

🇺🇸

New York, New York, United States

The Linder Research Center at The Christ Hospital

🇺🇸

Cincinnati, Ohio, United States

Cleveland Clinic

🇺🇸

Cleveland, Ohio, United States

Legacy Medical Group, Cardiology

🇺🇸

Portland, Oregon, United States

Carnegie Mellon University, Allegheny Health Network, Allegheny General Hospital

🇺🇸

Pittsburgh, Pennsylvania, United States

University of Texas Southwestern Medical Center

🇺🇸

Dallas, Texas, United States

University of Utah

🇺🇸

Salt Lake City, Utah, United States

University of Vermont Medical Center

🇺🇸

Burlington, Vermont, United States

Virginia Commonwealth University

🇺🇸

Richmond, Virginia, United States

Seattle Children's Hospital

🇺🇸

Seattle, Washington, United States

Swedish Medical Center - Cherry Hill

🇺🇸

Seattle, Washington, United States

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