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PrProfile: A Study to Assess the Safety, Tolerability, Pharmacokinetics and Pharmacodynamics of ION717

Phase 1
Active, not recruiting
Conditions
Prion Disease
Interventions
Drug: Placebo
Registration Number
NCT06153966
Lead Sponsor
Ionis Pharmaceuticals, Inc.
Brief Summary

The purpose of this study is to evaluate the safety, tolerability, pharmacokinetics and pharmacodynamics of intrathecal (IT) delivery of ION717.

Detailed Description

This is a first-in-human, randomized, multi-center study in participants with prion disease. Eligible participants will receive ION717 and placebo. The order of doses will be randomized and blinded to participants, study sites and the Sponsor. The study will consist of a screening period of up to 6 weeks, a 24-week double-blind treatment period and a 36-week post-treatment period. Multiple dose levels will be tested.

Recruitment & Eligibility

Status
ACTIVE_NOT_RECRUITING
Sex
All
Target Recruitment
56
Inclusion Criteria

Not provided

Exclusion Criteria

Not provided

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
ION717 + Placebo, Regimen 1ION717Participants will receive multiple doses of study drug (ION717 and placebo) during the 30-week double-blind treatment period; the order of doses is blinded. Participants will then receive multiple doses of ION717 during the 70-week open-label extension period.
ION717 + Placebo, Regimen 1PlaceboParticipants will receive multiple doses of study drug (ION717 and placebo) during the 30-week double-blind treatment period; the order of doses is blinded. Participants will then receive multiple doses of ION717 during the 70-week open-label extension period.
ION717 + Placebo, Regimen 2ION717Participants will receive multiple doses of study drug (ION717 and placebo) during the 30-week double-blind treatment period; the order of doses is blinded. Participants will then receive multiple doses of ION717 during the 70-week open-label extension period.
ION717 + Placebo, Regimen 2PlaceboParticipants will receive multiple doses of study drug (ION717 and placebo) during the 30-week double-blind treatment period; the order of doses is blinded. Participants will then receive multiple doses of ION717 during the 70-week open-label extension period.
Primary Outcome Measures
NameTimeMethod
Incidence of treatment-emergent adverse events.Baseline up to Week 33
Secondary Outcome Measures
NameTimeMethod
Maximum Observed Plasma Concentration (Cmax) of ION717on Day 1 and Week 9
Area Under the Plasma Concentration-time Curve (AUC) of ION717on Day 1 and Week 9
Half-life (t1/2λz) of ION717 in Plasmaon Day 1 and Week 9
Cerebrospinal fluid (CSF) Concentration of ION717Pre-dose and at multiple points post-dose up to Week 33
Amount of ION717 Excreted in UrinePost-dose on Day 1
Percent Change from Baseline in Prion Protein (PrP) Concentration in CSFPre-dose and at multiple points post-dose up to Week 33

Trial Locations

Locations (16)

UCLA Neurology Clinic

🇺🇸

Los Angeles, California, United States

University of Colorado Hospital

🇺🇸

Denver, Colorado, United States

Massachusetts General Hospital

🇺🇸

Boston, Massachusetts, United States

NYU Langone Health

🇺🇸

New York, New York, United States

University Hospitals Cleveland Medical Center

🇺🇸

Cleveland, Ohio, United States

Royal Melbourne Hospital

🇦🇺

Parkville, Australia

University of Alberta

🇨🇦

Edmonton, Alberta, Canada

Tel Aviv Sourasky Medical Center

🇮🇱

Tel Aviv, Israel

Fondazione I.R.C.C.S. Istituto Neurologico Carlo Besta

🇮🇹

Milan, Italy

Mihara Memorial Hospital

🇯🇵

Gunma, Isesaki-shi, Japan

National Center of Neurology and Psychiatry

🇯🇵

Tokyo, Kodaira-shi, Japan

Neuromuscular Center Yoshimizu Hospital

🇯🇵

Yamaguchi, Shimonoseki-shi, Japan

Hospital Clinic De Barcelona

🇪🇸

Barcelona, Spain

McGill University Health Centre

🇨🇦

Montréal, Quebec, Canada

Hôpital Universitaire Pitié Salpêtrière

🇫🇷

Paris, France

University Medical Center Göttingen

🇩🇪

Göttingen, Germany

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