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Study to Evaluate the Efficacy and Safety of Pemigatinib in Participants With Previously Treated Glioblastoma or Other Primary Central Nervous System Tumors Harboring Activating FGFR1-3 Alterations

Phase 2
Completed
Conditions
Glioblastoma
Adult-type Diffuse Gliomas
Interventions
Registration Number
NCT05267106
Lead Sponsor
Incyte Corporation
Brief Summary

This is an open-label, monotherapy study of pemigatinib in participants with recurrent glioblastoma (GBM) or other recurrent gliomas, circumscribed astrocytic gliomas, and glioneuronal and neuronal tumors with an activating FGFR1-3 mutation or fusion/rearrangement. This study consists of 2 cohorts, Cohorts A, and B, and will enroll approximately 82 participants into each cohort. Participants will receive pemigatinib 13.5 mg QD on a 2-week on-therapy and 1-week off-therapy schedule as long as they are receiving benefit and have not met any criteria for study withdrawal.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
83
Inclusion Criteria
  • Histological, cytological, or molecular confirmation of recurrent GBM or other glioma, circumscribed astrocytic glioma, or glioneuronalor neuronal tumors that has recurred.

  • Radiographically measurable disease.

    . -Karnofsky performance status ≥ 60.

  • Life expectancy ≥ 12 weeks.

  • Documentation of an actionable FGFR1-3 gene mutation or fusion/rearrangement from tissue : FGFR1-3 fusions or other rearrangements (FGFR1-3 in-frame fusions, any FGFR2 rearrangement, or FGFR1/3 rearrangement with known partner) or a defined FGFR1-3 activating mutation or in-frame deletion. Only participants with FGFR fusions or rearrangements with an intact kinase domain are eligible.

  • MRI-documented objective progression after prior therapy and must have no therapy available that is likely to provide clinical benefit.

  • Most recent archival tumor specimen must be a tumor block or a minimum of 15 unstained slides from biopsy or resection of primary tumor or metastasis.

  • Willingness to avoid pregnancy or fathering children.

Exclusion Criteria
  • Prior receipt of an FGFR inhibitor.
  • Receipt of anticancer medications or investigational drugs for any indication or reason within 28 days before first dose of study drug.
  • Participants may have had treatment for an unlimited number of prior relapses but must not have had prior bevacizumab or other VEGF/VEGFR inhibitors (exception: prior bevacizumab is allowed if it was administered for the treatment of radiation necrosis rather than progressive tumor and was stopped at least 12 weeks prior to MRI showing tumor progression).
  • Concurrent anticancer therapy
  • Candidate for potentially curative surgery.
  • Dexamethasone (or equivalent) > 4 mg daily at the time of study registration
  • Current evidence of clinically significant corneal or retinal disorder as confirmed by ophthalmologic examination.
  • Diffuse leptomeningeal disease.
  • Radiation therapy administered within 12 weeks before enrollment/first dose of study drug.
  • Known additional malignancy that is progressing or requires active systemic treatment.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Cohort A: IDH-wild-type GBMPemigatinibParticipants with histopathologically proven, WHO Grade 4, IDH-wild-type GBM OR molecular diagnosis of IDH-wild-type, diffuse astrocytic glioma with molecular features of Grade 4 GBM that are recurrent, harboring FGFR1-3 fusions/or other rearrangements, or with a defined FGFR1-3 mutation or in-frame deletion.
Cohort B: Other gliomas other than GBMPemigatinibParticipants with other histopathologically proven gliomas other than GBM, circumscribed astrocytic gliomas, and glioneuronal and neuronal tumors that are recurrent, harboring FGFR1-3 fusions/or other rearrangements or with a defined FGFR1-3 activating mutation or in-frame deletion
Primary Outcome Measures
NameTimeMethod
Cohort A: Overall Response Rate (ORR)Up to 3 months

Defined as the proportion of participants in Cohort A who achieve a best overall response (BOR) of complete response (CR) or partial response (PR) based on Response Assessment in Neuro-Oncology (RANO) as determined by an Independent Central Radiology (ICR).

Secondary Outcome Measures
NameTimeMethod
Cohorts A and B combined: ORRUp to 3 months

Defined as the proportion of participants in Cohorts A and B who achieve a BOR of CR or PR based on RANO as determined by an ICR.

Cohorts A and B: Disease Control Rate (DCR)Up to 3 months

Defined as the proportion of participants who achieve a CR, PR, or SD as assessed by ICR in cohorts A and B respectively

Cohorts A and B: Progression-Free Survival (PFS)Up to 3 months

Defined as the time from first dose until progressive disease (according to RANO and assessed by an ICR) or death (whichever occurs first) in cohorts A and B, respectively

Cohorts A and B: Overall Survival (OS)Up to 3 months

Defined as the time from first dose of study drug to death due to any cause in cohorts A and B respectively

Safety and tolerabilityUp to 3 months

Safety and tolerability in each cohort, assessed by monitoring the frequency and severity of AEs according to NCICTCAE v5.0.

Cohorts A and B : Duration Of Response (DOR)up to 3 months

Defined as the time from first assessment of Complete Response (CR) or Partial Response (PR) until progressive disease (according to RANO and assessed by an ICR), or death (whichever occurs first) in cohorts A and B, respectively

Cohort B : ORRup to 3 months

Defined as the proportion of participants who achieve a CR or PR based on RANO. Response will be determined by an ICR review.

Trial Locations

Locations (78)

Providence Medical Foundation

🇺🇸

Fullerton, California, United States

East Carolina University

🇺🇸

Greenville, North Carolina, United States

University of Illinois Hospital & Health Sciences System

🇺🇸

Chicago, Illinois, United States

University of Pittsburgh Medical Center Health System

🇺🇸

Pittsburgh, Pennsylvania, United States

Miami Cancer Institute

🇺🇸

Miami, Florida, United States

Fred Hutchinson Cancer Research Center

🇺🇸

Seattle, Washington, United States

Sharp Memorial Hospital

🇺🇸

San Diego, California, United States

UC Health At Cincinnati Va Medical Center

🇺🇸

Cincinnati, Ohio, United States

Huntsman Cancer Institute

🇺🇸

Salt Lake City, Utah, United States

Odense University Hospital

🇩🇰

Odense C, Denmark

Valkyrie Clinical Trials

🇺🇸

Beverly Hills, California, United States

Providence St Joseph Hospital Orange Center For Cancer Prevention and Treatment

🇺🇸

Santa Monica, California, United States

University of Iowa Hospital and Clinics

🇺🇸

Iowa City, Iowa, United States

Northwell Health

🇺🇸

Lake Success, New York, United States

Cleveland Clinic Foundation

🇺🇸

Cleveland, Ohio, United States

University of Pennsylvania Hospital

🇺🇸

Philadelphia, Pennsylvania, United States

Houston Methodist Hospital

🇺🇸

Houston, Texas, United States

Aalborg Universitets Hospital

🇩🇰

Aalborg, Denmark

Chru de Lille Hopital Claude Huriez

🇫🇷

Lille Cedex, France

Rigshospitalet Uni of Hospital of Copenhagen

🇩🇰

Copenhagen, Denmark

Hospital Universitaire Pitie-Salpetriere

🇫🇷

Paris, France

Chu Hopital de La Timone

🇫🇷

Marseille, France

Universitatsklinikum Bonn Aoer

🇩🇪

Bonn, Germany

Universitaire Du Cancer de Toulouse Institut Claudius Regaud Iuct-Oncopole

🇫🇷

Toulouse, France

Klinikum Der Johann Wolfgang Goethe University

🇩🇪

Frankfurt, Germany

University Hospital Tuebingen

🇩🇪

Tuebingen, Germany

Universitaetsklinikum Heidelberg

🇩🇪

Heidelberg, Germany

Ospedale Bellaria

🇮🇹

Bologna, Italy

Istituto Di Ricovero E Cura A Carattere Scientifico (Irccs) Ospedale San Raffaele

🇮🇹

Milano, Italy

A.S.L. Napoli 1 Centro Ospedale Del Mare

🇮🇹

Ponticelli, Italy

Irccs Istituto Clinico Humanitas

🇮🇹

Rozzano, Italy

Iov - Istituto Oncologico Veneto Irccs

🇮🇹

Padova, Italy

University of Tokyo Hospital

🇯🇵

Bunkyo-ku, Japan

Azienda Ospedaliero Universitaria Citta Della Salute E Della Scienza

🇮🇹

Torino, Italy

National Cancer Center Hospital

🇯🇵

Chuo-ku, Japan

Kyushu University Hospital

🇯🇵

Fukuoka-shi, Japan

Nagoya University Hospital

🇯🇵

Nagoya-shi, Japan

Hospital Del Mar

🇪🇸

Barcelona, Spain

Hospital General Universitario Vall D Hebron

🇪🇸

Barcelona, Spain

Hospital de La Santa Creu I Sant Pau

🇪🇸

Barcelona, Spain

Hospital Clinic Barcelona Main

🇪🇸

Barcelona, Spain

Ico Girona Hospital Universitari de Girona Dr Josep Trueta

🇪🇸

Girona, Spain

Ico Institut Catala D Oncologia

🇪🇸

L'hospitalet de Llobregat, Spain

Hospital Universitario Ramon Y Cajal

🇪🇸

Madrid, Spain

Hospital General Universitario Gregorio Maranon

🇪🇸

Madrid, Spain

Hospital Universitario 12 de Octubre

🇪🇸

Madrid, Spain

Hospital Universitario Hm Sanchinarro

🇪🇸

Madrid, Spain

Clinica Universidad de Navarra (Cun)

🇪🇸

Pamplona, Spain

Hospital General de Catalunya

🇪🇸

Sant Cugat Del Valles, Spain

Addenbrooke'S Hospital

🇬🇧

Cambridge, United Kingdom

Hospital General Universitario de Valencia

🇪🇸

Valencia, Spain

Velindre Cancer Centre

🇬🇧

Cardiff, United Kingdom

St James'S University Hospital

🇬🇧

Leeds, United Kingdom

Guys Hospital

🇬🇧

London, United Kingdom

The Royal Marsden Nhs Foundation Trust - Sutton

🇬🇧

London, United Kingdom

The Royal Marsden Nhs Foundation Trust - Chelsea

🇬🇧

London, United Kingdom

The Christie Nhs Foundation Trust Uk

🇬🇧

Manchester, United Kingdom

The Clatterbridge Cancer Centre

🇬🇧

Wirral, United Kingdom

Columbia University Irving Medical Center

🇺🇸

New York, New York, United States

Usc Norris Comprehensive Cancer Center

🇺🇸

Los Angeles, California, United States

University of California San Francisco

🇺🇸

San Francisco, California, United States

University Medical Center New Orleans

🇺🇸

New Orleans, Louisiana, United States

Tennessee Oncology

🇺🇸

Nashville, Tennessee, United States

Kyoto University Hospital

🇯🇵

Kyoto-shi, Japan

City of Hope National Medical Center

🇺🇸

Duarte, California, United States

University of Minnesota Health Clinics and Surgery Center

🇺🇸

Minneapolis, Minnesota, United States

Baptist Md Anderson Cancer Center

🇺🇸

Jacksonville, Florida, United States

Memorial Sloan Kettering Cancer Center

🇺🇸

New York, New York, United States

Netherlands Cancer Institute Antoni Van Leeuwenhoek Ziekenhuis

🇳🇱

Amsterdam, Netherlands

Tohoku University Hospital

🇯🇵

Sendai-shi, Japan

Erasmus Mc Cancer Institute

🇳🇱

Rotterdam, Netherlands

Hospital Universitario Virgen Del Rocio

🇪🇸

Sevilla, Spain

Stanford Neuroscience Health Center

🇺🇸

Sacramento, California, United States

Yale Cancer Center

🇺🇸

New Haven, Connecticut, United States

Orlando Health Cancer Institute Downtown Orlando

🇺🇸

Orlando, Florida, United States

H. Lee Moffitt Cancer Center and Research Institute Hospital

🇺🇸

Tampa, Florida, United States

Wake Forest Baptist Health

🇺🇸

Winston-Salem, North Carolina, United States

Baylor University Medical Center

🇺🇸

Dallas, Texas, United States

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