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Study to Evaluate the Efficacy and Safety of Pemigatinib in Participants With Previously Treated Glioblastoma or Other Primary Central Nervous System Tumors Harboring Activating FGFR1-3 Alterations

Phase 2
Completed
Conditions
Glioblastoma
Adult-type Diffuse Gliomas
Interventions
Registration Number
NCT05267106
Lead Sponsor
Incyte Corporation
Brief Summary

This is an open-label, monotherapy study of pemigatinib in participants with recurrent glioblastoma (GBM) or other recurrent gliomas, circumscribed astrocytic gliomas, and glioneuronal and neuronal tumors with an activating FGFR1-3 mutation or fusion/rearrangement. This study consists of 2 cohorts, Cohorts A, and B, and will enroll approximately 82 participants into each cohort. Participants will receive pemigatinib 13.5 mg QD on a 2-week on-therapy and 1-week off-therapy schedule as long as they are receiving benefit and have not met any criteria for study withdrawal.

Detailed Description

Not available

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
83
Inclusion Criteria
  • Histological, cytological, or molecular confirmation of recurrent GBM or other glioma, circumscribed astrocytic glioma, or glioneuronalor neuronal tumors that has recurred.

  • Radiographically measurable disease.

    . -Karnofsky performance status ≥ 60.

  • Life expectancy ≥ 12 weeks.

  • Documentation of an actionable FGFR1-3 gene mutation or fusion/rearrangement from tissue : FGFR1-3 fusions or other rearrangements (FGFR1-3 in-frame fusions, any FGFR2 rearrangement, or FGFR1/3 rearrangement with known partner) or a defined FGFR1-3 activating mutation or in-frame deletion. Only participants with FGFR fusions or rearrangements with an intact kinase domain are eligible.

  • MRI-documented objective progression after prior therapy and must have no therapy available that is likely to provide clinical benefit.

  • Most recent archival tumor specimen must be a tumor block or a minimum of 15 unstained slides from biopsy or resection of primary tumor or metastasis.

  • Willingness to avoid pregnancy or fathering children.

Exclusion Criteria
  • Prior receipt of an FGFR inhibitor.
  • Receipt of anticancer medications or investigational drugs for any indication or reason within 28 days before first dose of study drug.
  • Participants may have had treatment for an unlimited number of prior relapses but must not have had prior bevacizumab or other VEGF/VEGFR inhibitors (exception: prior bevacizumab is allowed if it was administered for the treatment of radiation necrosis rather than progressive tumor and was stopped at least 12 weeks prior to MRI showing tumor progression).
  • Concurrent anticancer therapy
  • Candidate for potentially curative surgery.
  • Dexamethasone (or equivalent) > 4 mg daily at the time of study registration
  • Current evidence of clinically significant corneal or retinal disorder as confirmed by ophthalmologic examination.
  • Diffuse leptomeningeal disease.
  • Radiation therapy administered within 12 weeks before enrollment/first dose of study drug.
  • Known additional malignancy that is progressing or requires active systemic treatment.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Cohort A: IDH-wild-type GBMPemigatinibParticipants with histopathologically proven, WHO Grade 4, IDH-wild-type GBM OR molecular diagnosis of IDH-wild-type, diffuse astrocytic glioma with molecular features of Grade 4 GBM that are recurrent, harboring FGFR1-3 fusions/or other rearrangements, or with a defined FGFR1-3 mutation or in-frame deletion.
Cohort B: Other gliomas other than GBMPemigatinibParticipants with other histopathologically proven gliomas other than GBM, circumscribed astrocytic gliomas, and glioneuronal and neuronal tumors that are recurrent, harboring FGFR1-3 fusions/or other rearrangements or with a defined FGFR1-3 activating mutation or in-frame deletion
Primary Outcome Measures
NameTimeMethod
Cohort A: Overall Response Rate (ORR)Up to 3 months

Defined as the proportion of participants in Cohort A who achieve a best overall response (BOR) of complete response (CR) or partial response (PR) based on Response Assessment in Neuro-Oncology (RANO) as determined by an Independent Central Radiology (ICR).

Secondary Outcome Measures
NameTimeMethod
Cohorts A and B combined: ORRUp to 3 months

Defined as the proportion of participants in Cohorts A and B who achieve a BOR of CR or PR based on RANO as determined by an ICR.

Cohorts A and B: Disease Control Rate (DCR)Up to 3 months

Defined as the proportion of participants who achieve a CR, PR, or SD as assessed by ICR in cohorts A and B respectively

Cohorts A and B: Progression-Free Survival (PFS)Up to 3 months

Defined as the time from first dose until progressive disease (according to RANO and assessed by an ICR) or death (whichever occurs first) in cohorts A and B, respectively

Cohorts A and B: Overall Survival (OS)Up to 3 months

Defined as the time from first dose of study drug to death due to any cause in cohorts A and B respectively

Safety and tolerabilityUp to 3 months

Safety and tolerability in each cohort, assessed by monitoring the frequency and severity of AEs according to NCICTCAE v5.0.

Cohort B : ORRup to 3 months

Defined as the proportion of participants who achieve a CR or PR based on RANO. Response will be determined by an ICR review.

Cohorts A and B : Duration Of Response (DOR)up to 3 months

Defined as the time from first assessment of Complete Response (CR) or Partial Response (PR) until progressive disease (according to RANO and assessed by an ICR), or death (whichever occurs first) in cohorts A and B, respectively

Trial Locations

Locations (78)

Valkyrie Clinical Trials

🇺🇸

Beverly Hills, California, United States

City of Hope National Medical Center

🇺🇸

Duarte, California, United States

Providence Medical Foundation

🇺🇸

Fullerton, California, United States

Usc Norris Comprehensive Cancer Center

🇺🇸

Los Angeles, California, United States

Stanford Neuroscience Health Center

🇺🇸

Sacramento, California, United States

Sharp Memorial Hospital

🇺🇸

San Diego, California, United States

University of California San Francisco

🇺🇸

San Francisco, California, United States

Providence St Joseph Hospital Orange Center For Cancer Prevention and Treatment

🇺🇸

Santa Monica, California, United States

Yale Cancer Center

🇺🇸

New Haven, Connecticut, United States

Baptist Md Anderson Cancer Center

🇺🇸

Jacksonville, Florida, United States

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Valkyrie Clinical Trials
🇺🇸Beverly Hills, California, United States

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