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Ecopipam Tablets to Study Tourette Syndrome in Children and Adolescents - Open Label Extension

Phase 2
Completed
Conditions
Tourette Syndrome in Children
Tourette Syndrome in Adolescence
Interventions
Registration Number
NCT04114539
Lead Sponsor
Emalex Biosciences Inc.
Brief Summary

This study was an international, multicenter, open-label, long term extension study evaluating the safety of ecopipam tablets for the treatment of children and adolescent subjects with Tourette Syndrome.

Detailed Description

This was an international, multicenter, open-label, long term extension study to evaluate the safety of ecopipam tablets for the treatment of pediatric subjects (aged ≥6 to ≤18 years at Baseline) with Tourette Syndrome. Participants who completed the Phase 2b, randomized, double-blind, efficacy and safety study (EBS-101-CL-001) without major reportable protocol deviations, and who met all the inclusion/exclusion criteria for this study were eligible to participate in this study. All participants were titrated to a target dose of 2 mg/kg/day as participants rolled over from the Phase 2b double-blind efficacy and safety study were tapered off study drug to maintain the blind from that study. Participants were to complete study visits every month for 1 year. Follow-up visits were conducted 7 and 14 days after the last dose of the study drug and a follow-up phone call was conducted 30 days after the last dose of study drug

Recruitment & Eligibility

Status
COMPLETED
Sex
All
Target Recruitment
124
Inclusion Criteria
  • Subjects must have completed the EBS-101-CL-001 study through the Day 14 Follow Up Visit within the last 30 days (or longer with permission of the medical monitor) without a major reportable protocol deviation and must be someone the Investigator feels would benefit from continued participation.
Exclusion Criteria
  • Certain mood or psychiatric disorders (i.e., dementia, bipolar disorder, schizophrenia, major depressive disorder).
  • Unstable medical illness or clinically significant lab abnormalities.
  • Risk of suicide.
  • Pregnant or lactating women.
  • Moderate to severe renal insufficiency.
  • Positive urine drug screen.
  • Certain medications that would lead to drug interactions.

Study & Design

Study Type
INTERVENTIONAL
Study Design
SINGLE_GROUP
Arm && Interventions
GroupInterventionDescription
EcopipamEcopipam-
Primary Outcome Measures
NameTimeMethod
Change From Baseline in Hematology Parameters: HemoglobinBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in hematology parameter hemoglobin was reported.

Change From Baseline in Serum Chemistry Parameters: Bicarbonate, Calcium, Chloride, Cholesterol, Glucose, Phosphate, Potassium, Sodium, Triglyceride and Urea NitrogenBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in Serum chemistry parameters (bicarbonate, calcium, chloride, cholesterol, glucose, phosphate, potassium, sodium, triglyceride, urea nitrogen) expressed in millimoles per liter (mmol/L) were reported.

Change From Baseline in Hematology Parameters: Basophils to Leukocytes Ratio Reported in Percentage of CellsBaseline up to Month 12

Basophils/Leukocytes was measured in percentages (%). Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in basophils to leukocytes ratio is reported in terms of percentage of cells.

Change From Baseline in Hematology Parameters: Eosinophils to Leukocytes Ratio Reported in Percentage of CellsBaseline up to Month 12

Eosinophils/Leukocytes was measured in percentages (%). Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in eosinophils to leukocytes ratio is reported in terms of percentage of cells.

Change From Baseline in Hematology Parameters: ErythrocytesBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in hematology parameter erythrocytes was reported.

Change From Baseline in Serum Chemistry Parameters: Albumin, Globulin and ProteinBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in Serum chemistry parameters (albumin, globulin and protein) were reported.

Change From Baseline in Vital Signs Parameter: Pulse RateBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in vital sign parameter pulse rate and according to assessment position (supine and standing) was reported.

Number of Participants With Adverse Events (AEs) and Serious Adverse Events (SAEs) and Their Relationship (Unrelated, Possibly Related, or Probably Related)From start of study drug administration until 30 days after last dose (Up to Month 13)

An AE was any untoward medical condition that occurs in a participant while participating in this clinical study. It can be any unfavorable and unintended sign (including an abnormal laboratory finding), symptom, or disease temporally associated with the use of a study drug, whether or not related to the study. An SAE was any untoward medical occurrence that at any dose met one, more of the following criteria: results in death, life-threatening, requires inpatient hospitalization or prolongation of existing hospitalization, results in persistent, significant disability/incapacity, a congenital abnormality/birth defect, an important medical event. The relationship of the study drug in causing or contributing to the AE whether unrelated, possibly related, or probably related was decided by investigator medical judgment.

Change From Baseline in Hematology Parameters: HematocritBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in hematology parameter hematocrit was reported.

Change From Baseline in Hematology Parameters: Leukocytes and PlateletsBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in hematology parameters (Leukocytes and Platelets) expressed in 10\^9 cells per liter were reported.

Change From Baseline in Hematology Parameters: Monocytes to Leukocytes Ratio Reported in Percentage of CellsBaseline up to Month 12

Monocytes/leukocytes was measured in percentages (%). Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in monocytes to leukocytes ratio is reported in terms of percentage of cells.

Change From Baseline in Serum Chemistry Parameters: Alanine Aminotransferase, Alkaline Phosphatase, Aspartate Aminotransferase, Lactase DehydrogenaseBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in Serum chemistry parameters (alanine aminotransferase, alkaline phosphatase, aspartate aminotransferase, and lactate dehydrogenase) were reported.

Change From Baseline in Hematology Parameters: Neutrophils to Leukocytes Ratio Reported in Percentage of CellsBaseline up to Month 12

Neutrophils/leukocytes was measured in percentages (%). Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in neutrophils to leukocytes ratio is reported in terms of percentage of cells.

Change From Baseline in Serum Chemistry Parameters: Bilirubin, Creatinine and Direct BilirubinBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in Serum chemistry parameters (bilirubin, creatinine and direct bilirubin) expressed in micromole per liter (mcmol/L) were reported.

Change From Baseline in Vital Signs Parameter: Diastolic Blood Pressure and Systolic Blood PressureBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in vital signs parameters diastolic blood pressure and systolic blood pressure and according to the assessment position (supine and standing) expressed in millimeter(s) of mercury (mmHg) was reported.

Change From Baseline in Electrocardiogram (ECG) Values Parameters: Aggregate PR Interval, Aggregate QRS Duration, Aggregate QT Interval, and Aggregate QTc IntervalBaseline to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change From Baseline in ECG parameters aggregate PR interval, aggregate QRS duration, aggregate QT interval, and aggregate QTc interval expressed in millisecond (msec) was reported.

Change From Baseline in Hematology Parameters: Lymphocytes to Leukocytes Ratio Reported in Percentage of CellsBaseline up to Month 12

Lymphocytes/leukocytes was measured in percentages (%). Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in lymphocytes to leukocytes ratio is reported in terms of percentage of cells.

Change From Baseline in Vital Signs Parameter: Body Mass Index [BMI]Baseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in vital signs parameter BMI was reported.

Change From Baseline in Hemoglobin A1c (HbA1c)Baseline up to Month 12

HbA1c is the glycosylated fraction of hemoglobin A. It is measured to identify average blood glucose concentration over prolonged periods of time. Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in HbA1c was reported.

Change From Baseline in Vital Signs Parameter: HeightBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in vital signs height was reported.

Change From Baseline in Vital Signs Parameter: WeightBaseline up to Month 12

Baseline was defined as the last measurement taken before the first dose of open-label treatment on Day 1 of current study. Change from baseline in vital signs parameter weight was reported.

Number of Participants With Clinically Significant Abnormal Physical Examination FindingsBaseline up to Month 12

Physical examination included examination of the following body areas and systems: Head, Eyes, Ears, Nose, Mouth, Throat, Neck (including Thyroid), Thorax, Abdomen, Urogenital, Extremities, Neurological, Skin and Mucosae and Others. Any clinically significant abnormalities in physical examination were judged by the investigator. Only non-zero values are reported.

Secondary Outcome Measures
NameTimeMethod
Change From Baseline in Clinical Global Impression of Tourette Syndrome of Severity (CGI-TS-S) at Months 1, 3, 6, 9, 12Baseline up to Months 1, 3, 6, 9, 12

The CGI consists of 2 reliable and valid 7-item Likert scales used to assess severity and change in clinical symptoms. The CGI severity scale (CGI-TS-S) ranges from 1 = "not ill at all" to 7 = "among the most extremely ill." Higher scores represent more severe symptoms. A negative change from baseline indicates improvement.

Change From Baseline in the Yale Global Tic Severity Scale - Global Score (YGTSS-GS) at Months 1, 3, 6, 9 and 12Baseline up to Months 1, 3, 6, 9 and 12

The YGTSS was a clinician-completed rating scale used to quantify overall tic severity as well as specific subdomains of tic number, frequency, duration, intensity, and complexity. Each of these subdomains was scored, on a 0 to 5 scale, separately for motor and vocal tics and then summed across both motor and vocal tics to yield a tic severity score ranging from 0 to 50. The YGTSS also provides for an overall impairment rating (0 = ''none'' to 50 = ''severe''). YGTSS-GS is the total of YGTSS-TTS and YGTSS-I. The maximum YGTSS Global score is 100, while the maximum motor score is 25, the maximum vocal score is 25, and the maximum impairment score is 50. Higher scores indicate more severe tics. A negative change from baseline indicates improvement.

Clinical Global Impression Tourette Syndrome of Improvement (CGI-TS-I) Scores at Months 1, 3, 6, 9 and 12Months 1, 3, 6, 9 and 12

The CGI consists of 2 reliable and valid 7-item Likert scales used to assess severity and change in clinical symptoms. The scale ranges from 1 = "very much improved" to 7 = very much worse" for the CGI-TS-I. Higher score represent more severe symptoms.

Change From Baseline in the Yale Global Tic Severity Scale -Total Tic Score (YGTSS-TTS) at Months 1, 3, 6, 9 and 12Baseline up to Months 1, 3, 6, 9 and 12

The YGTSS was a clinician-completed rating scale used to quantify overall tic severity as well as specific subdomains of tic number, frequency, intensity, complexity and interference. Each of these subdomains was scored, on a 0 to 5 scale, separately for motor and vocal tics and then summed across both motor and vocal tics to yield a total tic score ranging from 0 to 50. Higher scores represent more severe symptoms. A negative change from baseline indicates improvement.

Change From Baseline in the Yale Global Tic Severity Scale - Impairment (YGTSS-I) at Months 1, 3, 6, 9 and 12Baseline up to Months 1, 3, 6, 9 and 12

The YGTSS was a clinician-completed rating scale used to quantify overall tic severity as well as specific subdomains of tic number, frequency, duration, intensity, and complexity. Each of these subdomains was scored, on 0 to 5 scale, separately for an overall impairment rating from (0 = ''none'' to 50 = ''severe''). Higher score represent more severe symptoms. A negative change from baseline indicates improvement.

Change From Baseline in Gilles de la Tourette Syndrome-Quality of Life Scale for Children and Adolescents (C&A-GTS-QOL) Total Score at Months 1, 3, 6, 9 and 12Baseline up to Months 1, 3, 6, 9 and 12

The C\&A-GTS-QOL was a 27-item questionnaire specific to TS patients that asks the patient to assess the extent to which their quality of life is impacted by their symptoms. The C\&A-GTS-QOL consists of 6 subscales (cognitive \[score range 0-32\], coprophenomena \[range 0-12\], psychological \[range 0-24\], physical \[range 0-12\], obsessive-compulsive \[range 0-16\], and activities of daily living (ADL) \[range 0-12\] and uses a 5 point Likert scale ranging from no problem to extreme problem. Scores for six subscales were generated by summing items and, for ease of interpretation, transformation to a range of 0 to 100 (100\* \[(observed score-min possible score)/(max possible score-min possible score)\]). Total score, resulted from sum of the subscale scores, was also normalized to a 0 to 100 range. Higher score indicated worst quality of life. A negative change from baseline indicates better quality of life.

Trial Locations

Locations (65)

Rush University Medical Center

🇺🇸

Chicago, Illinois, United States

The University of Chicago Hospitals

🇺🇸

Chicago, Illinois, United States

Massachusetts General Hospital

🇺🇸

Boston, Massachusetts, United States

Center for Psychiatry and Behavioral Medicine Inc.

🇺🇸

Las Vegas, Nevada, United States

Cincinnati Childrens Hospital Medical Center

🇺🇸

Cincinnati, Ohio, United States

Road Runner Research Ltd.

🇺🇸

San Antonio, Texas, United States

Uniwersyteckie Centrum Kliniczne

🇵🇱

Gdansk, Poland

NZOZ Wielospecjalistyczna Poradnia Lekarska Synapsis

🇵🇱

Katowice, Poland

Yale School of Medicine

🇺🇸

New Haven, Connecticut, United States

CHU Sainte-Justine

🇨🇦

Montreal, Quebec, Canada

Gdanskie Centrum Zdrowia Sp z o.o.

🇵🇱

Gdańsk, Poland

Alivation Research, LLC

🇺🇸

Lincoln, Nebraska, United States

Centrum Medyczne Plejady

🇵🇱

Krakow, Poland

The NeuroCognitive Institute

🇺🇸

Mount Arlington, New Jersey, United States

University of Miami

🇺🇸

Miami, Florida, United States

Centrum Bada Klinicznych PI-House Sp. z o.o.

🇵🇱

Gdansk, Poland

Wojewdzki Specjalistyczny Szpital Dziecicy im. sw. Ludwika w Krakowie

🇵🇱

Krakow, Poland

University Hospitals Cleveland Medical Center

🇺🇸

Cleveland, Ohio, United States

Med-Polonia Sp. z o. o.

🇵🇱

Poznań, Poland

Coastal Pediatric Research

🇺🇸

Charleston, South Carolina, United States

APG Research LLC

🇺🇸

Orlando, Florida, United States

PCSD-Feighner Research

🇺🇸

San Diego, California, United States

University of South Florida

🇺🇸

Saint Petersburg, Florida, United States

Syrentis Clinical Research

🇺🇸

Santa Ana, California, United States

Michigan Clinical Research Institute PC

🇺🇸

Ann Arbor, Michigan, United States

Helen DeVos Children's Hospital / Spectrum Health Medical Group

🇺🇸

Wyoming, Michigan, United States

Quest Therapeutics of Avon Lake

🇺🇸

Avon Lake, Ohio, United States

North Texas Clinical Trials

🇺🇸

Fort Worth, Texas, United States

Baylor College of Medicine

🇺🇸

Houston, Texas, United States

University of Virginia

🇺🇸

Charlottesville, Virginia, United States

Phoenix Children's Hospital

🇺🇸

Phoenix, Arizona, United States

Access Clinical Trials, Inc.

🇺🇸

Nashville, Tennessee, United States

Vanderbilt University Medical Center

🇺🇸

Nashville, Tennessee, United States

Sarkis Clinical Trials

🇺🇸

Gainesville, Florida, United States

MedBio Trials

🇺🇸

North Miami, Florida, United States

Research in Miami Inc.

🇺🇸

Hialeah, Florida, United States

Northwest Florida Clinical Research Group, LLC

🇺🇸

Gulf Breeze, Florida, United States

Pediatric Epilepsy and Neurology Specialists

🇺🇸

Tampa, Florida, United States

Pediatric Neurology, PA

🇺🇸

Winter Park, Florida, United States

Rare Disease Research, LLC

🇺🇸

Atlanta, Georgia, United States

Meridian Clinical Research

🇺🇸

Savannah, Georgia, United States

AMR - Baber Research Inc.

🇺🇸

Naperville, Illinois, United States

Psychiatric Associates

🇺🇸

Overland Park, Kansas, United States

Neurobehavioral Medicine Group

🇺🇸

Bloomfield Hills, Michigan, United States

New York Neurology Associates P.C

🇺🇸

New York, New York, United States

Movement Disorders Center

🇺🇸

Saint Louis, Missouri, United States

St. Charles Psychiatric Associates dba Midwest Research Group

🇺🇸

Saint Charles, Missouri, United States

Hapworth Research Inc.

🇺🇸

New York, New York, United States

Mount Sinai School of Medicine

🇺🇸

New York, New York, United States

Suburban Research Associates

🇺🇸

Media, Pennsylvania, United States

North Star Medical Research LLC

🇺🇸

Middleburg Heights, Ohio, United States

Houston Clinical Trials LLC

🇺🇸

Bellaire, Texas, United States

Relaro Medical Trials

🇺🇸

Dallas, Texas, United States

Center for Pediatric Excellence

🇨🇦

Ottawa, Ontario, Canada

The Kids Clinic Inc

🇨🇦

Ajax, Ontario, Canada

CHU Poitiers

🇫🇷

Poitiers, France

Pharmakologisches Studienzentrum Chemnitz GmbH

🇩🇪

Mittweida, Germany

Harmonex Neuroscience Research

🇺🇸

Dothan, Alabama, United States

Advanced Research Center Inc.

🇺🇸

Anaheim, California, United States

UCLA

🇺🇸

Los Angeles, California, United States

Mood Disorders Consulting Medicine PLLC

🇺🇸

New York, New York, United States

Finger Lakes Clinical Research

🇺🇸

Rochester, New York, United States

Clinical Research Center of NJ

🇺🇸

Voorhees, New Jersey, United States

Noetic Psychiatry

🇺🇸

Springville, Utah, United States

Eastside Therapeutic Resource Inc dba Core Clinical Research

🇺🇸

Everett, Washington, United States

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