MedPath

Entospletinib Plus Intensive Induction/Consolidation Chemotherapy in Newly Diagnosed NPM1-mutated AML

Phase 3
Terminated
Conditions
Nucleophosmin 1-mutated Acute Myeloid Leukemia
Interventions
Drug: Placebo
Drug: Anthracycline
Registration Number
NCT05020665
Lead Sponsor
Kronos Bio
Brief Summary

The primary objective of this study is to evaluate the efficacy of entospletinib (ENTO) compared to placebo when added to chemotherapy in previously untreated nucleophosmin-1 mutated (NPM1-m) acute myeloid leukemia (AML), as defined by the rate of molecularly defined measurable residual disease (MRD).

Detailed Description

This is a multi-center, international, double-blind, placebo-controlled study in previously untreated participants with acute myeloid leukemia (AML) harboring nucleophosmin-1 (NPM1) mutations. Upon fulfillment of all eligibility criteria, participants were randomized 1:1 to receive intensive chemotherapy in combination with either the spleen tyrosine kinase (SYK) inhibitor entospletinib (ENTO), or placebo. The study consisted of Screening, Induction, Consolidation, End-of-Treatment, and Long-term Follow-up phases.

Recruitment & Eligibility

Status
TERMINATED
Sex
All
Target Recruitment
15
Inclusion Criteria
  1. Adults 18 to 74 years with previously untreated de novo acute myeloid leukemia (AML), AML with myelodysplastic syndromes (MDS) features, or therapy-related AML, who were candidates for intensive induction therapy.

  2. Nucleophosmin-1 (NPM1)-mutated disease documented in a local or the Sponsor's central testing facility.

    Note: Participants with local test results for nucleophosmin-1 mutated (NPM1-m) (and/or FMS-like tyrosine kinase 3 mutational status) may enroll, provided appropriate samples were sent to the Sponsor's central testing facility for NPM1-m companion diagnostic development.

  3. Eastern Cooperative Oncology Group Performance Status (ECOG PS) score of 0, 1, or 2.

  4. Adequate hepatic and renal function defined as:

    1. Serum aspartate aminotransferase (AST) and alanine aminotransferase (ALT) < 2.5 times the upper limit of normal (ULN), except those with hepatic involvement by AML, as documented by either computed tomography (CT) or ultrasound, in whom levels of AST and ALT < 5 times ULN are acceptable; total bilirubin < 1.5 times ULN unless elevated due to Gilbert's Disease or hemolysis.
    2. Calculated creatinine clearance > 40 mL/min or serum creatinine < 1.5 times ULN.
  5. Prothrombin time (PT), activated partial thromboplastin time (aPTT), and international normalized ratio (INR) ≤ 1.5 x ULN unless receiving therapeutic anticoagulation.

  6. Left ventricular ejection fraction ≥ 45% confirmed by echocardiogram (ECHO) or multi-gated acquisition (MUGA) scan.

Exclusion Criteria
  1. Isolated myeloid sarcoma (ie, participants must had peripheral blood and/or bone marrow involvement by AML) or acute promyelocytic leukemia.

  2. Concurrent FLT3 mutation (either tyrosine kinase domain or internal tandem duplication).

  3. Known central nervous system (CNS) involvement with leukemia.

  4. Was a candidate for more intensive treatment than specified in this protocol.

  5. Either not a candidate for any anthracycline therapy or a candidate for induction therapy with a higher dose of daunorubicin (eg. 90 mg/m^2).

  6. Was a candidate for daily doses of cytarabine > 100 mg/m^2 in Induction Cycle 1.

  7. Active infection with hepatitis B, C, or uncontrolled human immunodeficiency virus (HIV).

  8. Known active coronavirus disease 2019 (COVID-19) either symptomatic or asymptomatic, as determined by nasopharyngeal swab for severe acute respiratory syndrome (SARS) coronavirus 2 (SARS CoV-2) ribonucleic acid (RNA) or antigen.

    Note: Participants with a history of SARS-CoV-2 nasopharyngeal carriage (either with or without symptoms), who had subsequently tested negative on follow-up nasopharyngeal swab and were without signs or symptoms of COVID-19 might enroll. Participants who were fully vaccinated against SARS-CoV-2 might enroll.

  9. Disseminated intravascular coagulation with active bleeding or signs of thrombosis.

  10. History of prior allogeneic hematopoietic stem cell transplant or solid organ transplant.

  11. Treatment with proton pump inhibitors (PPIs) from 7 days prior to enrollment until 48 hours after completion of entospletinib (ENTO) or placebo.

    Note: PPIs were likely to interfere with ENTO absorption, thus requiring a 7-day washout period prior to the initiation of study medication. For management of acute gastrointestinal bleeding during the study treatment period (such as that related to chemotherapy), short term concurrent use of PPIs was permitted for up to 10 consecutive days. If longer durations of PPI exposure were required, participants should discontinue study medication. Histamine (H2) receptor antagonists and antacids were allowed throughout the study treatment period.

  12. Ongoing immunosuppressive therapy, including systemic chemotherapy for treatment of leukemia.

    Note: Participants may not receive AML-directed therapy prior to enrollment other than hydroxyurea or leukapheresis for acute management of hyperleukocytosis.

  13. Clinical signs/symptoms of leukostasis that had failed therapy including hydroxyurea and/or leukapheresis of at least 3 days duration.

  14. Clinically significant heart disease defined as:

    1. New York Heart Association Class 3 or 4 congestive heart failure,
    2. Acute myocardial infarction ≤ 6 months before enrollment,
    3. Symptomatic cardiac ischemia/unstable angina ≤ 3 months before enrollment,
    4. History of clinically significant arrhythmias (eg, ventricular tachycardia or fibrillation; Torsades de Pointe) including Mobitz type II 2nd degree or 3rd degree heart block without a permanent pacemaker in place.
  15. Participants with a corrected congenital long measure between Q wave and T wave in the electrocardiogram (QT) interval (using the Fredericia formula, Fridericia correction of the QT measure [QTcF]) > 480 msec or Long QT Syndrome.

  16. Evidence of ongoing, uncontrolled systemic bacterial, fungal, or viral infection at the time of study treatment initiation, including but not limited to persistent fever or positive cultures in the setting of appropriate antimicrobial therapy.

  17. Unable to swallow tablets or concurrent disease affecting gastrointestinal function such as, malabsorption syndrome, gastric or small bowel resection, bariatric surgery, inflammatory bowel disease, or bowel obstruction.

Study & Design

Study Type
INTERVENTIONAL
Study Design
PARALLEL
Arm && Interventions
GroupInterventionDescription
Intensive Chemotherapy + Entospletinib (ENTO)AnthracyclineParticipants received intensive chemotherapy (cytarabine and anthracycline \[daunorubicin or idarubicin\]) in combination with entospletinib (ENTO).
Intensive Chemotherapy + PlaceboPlaceboParticipants received intensive chemotherapy (cytarabine and anthracycline \[daunorubicin or idarubicin\]) in combination with the matching placebo.
Intensive Chemotherapy + PlaceboAnthracyclineParticipants received intensive chemotherapy (cytarabine and anthracycline \[daunorubicin or idarubicin\]) in combination with the matching placebo.
Intensive Chemotherapy + Entospletinib (ENTO)CytarabineParticipants received intensive chemotherapy (cytarabine and anthracycline \[daunorubicin or idarubicin\]) in combination with entospletinib (ENTO).
Intensive Chemotherapy + PlaceboCytarabineParticipants received intensive chemotherapy (cytarabine and anthracycline \[daunorubicin or idarubicin\]) in combination with the matching placebo.
Intensive Chemotherapy + Entospletinib (ENTO)EntospletinibParticipants received intensive chemotherapy (cytarabine and anthracycline \[daunorubicin or idarubicin\]) in combination with entospletinib (ENTO).
Primary Outcome Measures
NameTimeMethod
Number of Participants With Measurable Residual Disease (MRD) Negative Complete Response (CR) RateCycle 1 Day 1, up to Day 42 of chemotherapy cycle 2 (Cycle length = 42 days)

MRD negative CR requires CR as defined by the European Leukemia Network (ELN) 2017 criteria (with minor modification for neutrophil and platelet count thresholds as defined by International Working Group \[IWG\]) as assessed by study site investigators, and MRD negativity (\<0.01%) in bone marrow as measured by a molecular nucleophosmin-1 mutated (NPM1-m) assay (eg, next generation sequencing) in a central laboratory upon recovery of peripheral blood counts following completion of 2 cycles of chemotherapy, no later than Day 42 of Cycle 2.

Secondary Outcome Measures
NameTimeMethod
Event-free Survival (EFS)Cycle 1 Day 1, up to Day 42 of chemotherapy cycle 2 (Cycle length = 42 days)

EFS is defined as the time from randomization to the earliest occurrence of induction treatment failure, relapse from CR, or death from any cause. Induction treatment failure is failure to achieve morphological CR after completion of the last cycle of induction chemotherapy (no later than Day 42 of the last cycle of induction).

Relapse-free Survival (RFS)Cycle 1 Day 1, up to Day 42 of chemotherapy cycle 2 (Cycle length = 42 days)

RFS is defined as the time from CR until relapse or death from any cause as assessed by study site investigators.

Overall Survival (OS)Cycle 1 Day 1, up to Day 42 of chemotherapy cycle 2 (Cycle length = 42 days)

OS is defined as the time from randomization until death from any cause.

Number of Participant With Complete Response (CR) After 2 Cycles of ChemotherapyCycle 1 Day 1, up to Day 42 of chemotherapy cycle 2 (Cycle length = 42 days)

CR as defined by ELN 2017 criteria (with minor modification for neutrophil and platelet count thresholds as defined by IWG) as assessed by study site investigators.

Number of Participants Who Experienced Treatment-emergent Adverse Events (TEAEs)Cycle 1 Day 1 to 30 days following study treatment completion, (Cycle length = 42 days) maximum up to 198 days

A TEAE is any untoward medical occurrence in a clinical study participant, beginning or worsening from Cycle 1, Day 1 through 30 days following study treatment completion, temporarily associated with the use of treatment, whether or not considered related to the study treatment. TEAEs were recorded according to the most current version of the Medical Dictionary for Regulatory Activities (MedDRA).

Clinically significant changes in safety laboratory assessments, electrocardiograms, echocardiogram / multi-gated acquisition scans and Eastern Cooperative Oncology Group performance status findings, as assessed by the Investigator, were recorded as TEAEs.

Trial Locations

Locations (83)

Mount Sinai Health System

🇺🇸

New York, New York, United States

Hôpital Côte De Nacre

🇫🇷

Caen, Calvados, France

Hollings Cancer Center

🇺🇸

Charleston, South Carolina, United States

Fakultni Nemocnice Brno

🇨🇿

Brno, Czechia

City of Hope

🇺🇸

Duarte, California, United States

University of Michigan Medical School

🇺🇸

Ann Arbor, Michigan, United States

Bon Secours St. Francis Cancer Center

🇺🇸

Greenville, South Carolina, United States

Severance Hospital

🇰🇷

Seoul, Korea, Republic of

Uniwersyteckie Centrum Kliniczne WUM - Centralny Szpital Kliniczny

🇵🇱

Warsaw, Poland

Catholic University of Korea Seoul Saint Mary's Hospital

🇰🇷

Seoul, Korea, Republic of

UCLA - Jonsson Comprehensive Cancer Center

🇺🇸

Los Angeles, California, United States

Indiana Blood & Marrow Transplantation

🇺🇸

Indianapolis, Indiana, United States

Baylor University Medical Center

🇺🇸

Dallas, Texas, United States

Hospital Erasto Gaertner - Liga Paranaense de Combate ao Câncer

🇧🇷

Curitiba, Brazil

Hospital Universitário Walter Cantídio

🇧🇷

Fortaleza, Brazil

Henry Ford Health System

🇺🇸

Detroit, Michigan, United States

Duke Cancer Institute

🇺🇸

Durham, North Carolina, United States

Hospital Amaral Carvalho

🇧🇷

Jaú, Brazil

Hospital de Clínicas de Porto Alegre

🇧🇷

Porto Alegre, Brazil

Instituto Nacional de Câncer - Brazil

🇧🇷

Rio De Janeiro, Brazil

Hospital de Base - São José do Rio Preto

🇧🇷

Rio Preto, Brazil

A Beneficência Portuguesa de São Paulo - Unidade Mirante

🇧🇷

São Paulo, Brazil

Princess Margaret Cancer Centre

🇨🇦

Toronto, Canada

Debreceni Egyetem Klinikai Központ

🇭🇺

Debrecen, Hungary

Juravinski Hospital

🇨🇦

Hamilton, Canada

Fakultní Nemocnice Hradec Králové

🇨🇿

Hradec Králové, Czechia

Saskatchewan Cancer Agency

🇨🇦

Saskatoon, Canada

Centre Hosptitalier Universitaire d'Angers

🇫🇷

Angers, France

Fakultní Nemocnice Královské Vinohrady

🇨🇿

Praha, Czechia

Assuta Hospital - Ramat HaHayal

🇮🇱

Tel Aviv, Israel

Hôpital Claude Huriez

🇫🇷

Lille, France

Hôpital l'Archet

🇫🇷

Nice, France

Hôpital Saint-Antoine

🇫🇷

Paris, France

Hôpital Saint-Louis

🇫🇷

Paris, France

Hôpital Necker-Enfants Malades

🇫🇷

Paris, France

Centre Hospitalier Lyon-Sud

🇫🇷

Pierre-Bénite, France

Centre de Lutte Contre le Cancer - Centre Henri-Becquerel

🇫🇷

Rouen, France

Städtisches Klinikum Braunschweig

🇩🇪

Braunschweig, Germany

Helios St. Johannes Klinik

🇩🇪

Duisburg, Germany

Universitätsmedizin Mannheim

🇩🇪

Mannheim, Germany

Semmelweis Egyetem

🇭🇺

Budapest, Hungary

Marien Hospital Düsseldorf

🇩🇪

Düsseldorf, Germany

Universitätsklinikum Münster

🇩🇪

Münster, Germany

Medizinische Hochschule Hannover

🇩🇪

Hanover, Germany

Dél-pesti Centrumkórház - Országos Hematológiai és Infektológiai Intézet

🇭🇺

Budapest, Hungary

Jósa András Oktatókórház

🇭🇺

Nyíregyháza, Hungary

Szent-Györgyi Albert Klinikai Központ

🇭🇺

Szeged, Hungary

Rambam Health Care Campus

🇮🇱

Haifa, Israel

Shamir Medical Center (Assaf Harofeh)

🇮🇱

Be'er Ya'aqov, Israel

Samson Assuta Ashdod University Hospital

🇮🇱

Ashdod, Israel

Hadassah University Hospital Ein Kerem

🇮🇱

Jerusalem, Israel

Tel Aviv Sourasky Medical Center

🇮🇱

Tel Aviv, Israel

Azienda Ospedaliero Universitaria Policlinico Vittorio Emanuele

🇮🇹

Catania, Sicily, Italy

Azienda Ospedaliero-Universitaria di Bologna Policlinico Sant Orsola-Malpighi

🇮🇹

Bologna, Italy

Azienda Universitaria Ospedaliera Consorziale - Policlinico di Bari

🇮🇹

Bari, Italy

Azienda Socio Sanitaria Territoriale Grande Ospedale Metropolitano Niguarda

🇮🇹

Milan, Italy

Ospedale Santa Maria delle Croci di Ravenna

🇮🇹

Ravenna, Italy

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico

🇮🇹

Milano, Italy

Azienda Ospedaliero-Universitaria Maggiore della Carità di Novara

🇮🇹

Novara, Italy

Daegu Catholic University Medical Center

🇰🇷

Daegu, Korea, Republic of

Kyungpook National University Hospital

🇰🇷

Daegu, Korea, Republic of

Keimyung University Dongsan Hospital

🇰🇷

Daegu, Korea, Republic of

Chungnam National University Hospital

🇰🇷

Daejeon, Korea, Republic of

Samsung Medical Center

🇰🇷

Seoul, Korea, Republic of

Gachon University Gil Medical Center

🇰🇷

Incheon, Korea, Republic of

Korea University Guro Hospital

🇰🇷

Seoul, Korea, Republic of

Uniwersyteckie Centrum Kliniczne w Gdańsku

🇵🇱

Gdańsk, Poland

Samodzielny Publiczny Szpital Kliniczny Nr im. Prof. Tadeusza Sokołowskiego

🇵🇱

Szczecin, Poland

Instytut Hematologii I Transfuzjologii

🇵🇱

Warsaw, Poland

Institut D'Investigacions Biomédiques August Pi I Sunyer

🇪🇸

Barcelona, Spain

Uniwersytecki Szpital Kliniczny im. Jana Mikulicza-Radeckiego we Wrocławiu

🇵🇱

Wrocław, Poland

Hospital Germans Trias i Pujol

🇪🇸

Badalona, Catalonia, Spain

Hospital San Pedro de Alcantara

🇪🇸

Cáceres, Spain

Institut Català d'Oncologia - Hospital Duran i Reynals (ICO L'Hospitalet)

🇪🇸

Barcelona, Spain

Hospital General Universitario Gregorio Marañón

🇪🇸

Madrid, Spain

Hospital Son Llàtzer

🇪🇸

Palma De Mallorca, Spain

Hospital Universitario Fundación Jiménez Díaz

🇪🇸

Madrid, Spain

Hospital Clínico Universitario de Valencia

🇪🇸

Valencia, Spain

Hospital Universitario Central de Asturias

🇪🇸

Oviedo, Spain

Hospital Universitari I Politecnic La Fe

🇪🇸

Valencia, Spain

Irmandade da Santa Casa de Misericórdia Hospital - Porto Alegre

🇧🇷

Porto Alegre, Brazil

Instituto Brasileiro de Controle do Câncer - São Camilo Oncologia - Unidade Mooca

🇧🇷

São Paulo, Brazil

Seoul National University Hospital

🇰🇷

Incheon, Korea, Republic of

© Copyright 2025. All Rights Reserved by MedPath